Steroid-resistant eosinophilic fasciitis successfully treated with addition of extracorporeal photopheresis

Eosinophilic fasciitis (EF) is an uncommon fibrosing disease of the fascia with characteristic cutaneous and hematologic manifestations. Although EF is most commonly treated with corticosteroids at the beginning, a considerable number of patients show an inadequate response and hence various therape...

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Detalles Bibliográficos
Autores: Partarrieu-Mejias, F, Giacaman-Von der Weth, MM, Perez-Ferriols, A, Goterris-Viciedo, R, Alegre-de Miquel, V
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2019
País:España
Institución:INCLIVA
Repositorio:r-INCLIVA. Repositorio Institucional de Producción Científica de INCLIVA
OAI Identifier:oai:incliva.fundanetsuite.com:p3829
Acceso en línea:https://incliva.portalinvestigacion.com/publicaciones/3829
Access Level:acceso abierto
Palabra clave:eosinophilic fasciitis
extracorporeal Photopheresis
treatment
Descripción
Sumario:Eosinophilic fasciitis (EF) is an uncommon fibrosing disease of the fascia with characteristic cutaneous and hematologic manifestations. Although EF is most commonly treated with corticosteroids at the beginning, a considerable number of patients show an inadequate response and hence various therapeutic strategies have been tried, including extracorporeal photopheresis (ECP). We describe the case of a 66-year-old woman with steroid-resistant EF that improved significantly after ECP was added to her treatment regimen. To date, only six cases of this therapeutic strategy have been reported in English literature.