Proximal type epithelioid sarcoma of the vulva

Epithelioid sarcoma is a rare type of mesenchymal tumor. Proximal-type epithelioidsarcoma of the vulva is an extremely rare malignant tumor of the soft tissues withfrequent recurrences due to its aggressive behaviour. Because its characteristicsare similar to other benign lesions, this leads to diag...

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Detalles Bibliográficos
Autores: Torres-Cepeda, Duly, Rondon-Tapia, Martha, Reyna-Villasmil, Eduardo
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2022
País:Perú
Institución:Sociedad Peruana de Obstetricia y Ginecología
Repositorio:Revista Peruana de Ginecología y Obstetricia
Idioma:español
inglés
OAI Identifier:oai:ginecologiayobstetricia.pe:article/2420
Acceso en línea:https://ginecologiayobstetricia.pe/index.php/RPGO/article/view/2420
Access Level:acceso abierto
Palabra clave:Vulva
Sarcoma epitelioide
Neoplasia de la vulva
Descripción
Sumario:Epithelioid sarcoma is a rare type of mesenchymal tumor. Proximal-type epithelioidsarcoma of the vulva is an extremely rare malignant tumor of the soft tissues withfrequent recurrences due to its aggressive behaviour. Because its characteristicsare similar to other benign lesions, this leads to diagnostic and therapeutic delays.Histologic features of this tumor include prominent epithelioid cells and theappearance of rhabdoid features with marked nuclear atypia. Due to its low incidence,there are no evidence-based diagnostic algorithms or published recommendationsfor treatment. The prognosis is generally poor. A case of proximal type epithelioidsarcoma of the vulva is presented.