Nasal involvement of extranodal Rosai-Dorfman disease

A 60-year-old male patient with recurrent epistaxis, nasal obstruction, oral breathing, endonasal pain, intermittent frontal headache and progressive nasal deformity for four years. Histopathology revealed a chronic inflammatory infiltrate with abundant histiocytes that present the phenomenon of emp...

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Detalles Bibliográficos
Autores: Aliaga, Rolig, Salinas, José, Cabezas, Diego, Montes, Jaime, Ciudad, Pedro, Orrego, Carlos, Grados, Julio, Samamé, Juan Carlos, Pando, Fiorella, Custodio, Yinno, Aceituno, Lidia, Fernández, Gisell, Urbina, Dirce
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2020
País:Perú
Institución:Sociedad Peruana de Medicina Interna
Repositorio:Revista de la Sociedad Peruana de Medicina Interna
Idioma:español
OAI Identifier:oai:medicinainterna.net.pe:article/496
Acceso en línea:https://revistamedicinainterna.net/index.php/spmi/article/view/496
Access Level:acceso abierto
Palabra clave:Enfermedad de Rosai-Dorfman
histiocitosis sinusal
extranodal
afección nasal
emperipolesis
quimioterapia metronómica
terapia inmunomoduladora
Rosai-Dorfman disease
sinus histiocytosis
nasal involvement
metronomic chemotherapy
immunomodulatory therapy
Descripción
Sumario:A 60-year-old male patient with recurrent epistaxis, nasal obstruction, oral breathing, endonasal pain, intermittent frontal headache and progressive nasal deformity for four years. Histopathology revealed a chronic inflammatory infiltrate with abundant histiocytes that present the phenomenon of emperipolesis; and, immunohistochemistry confirmed the diagnosis of extranodal Rosai-Dorfman disease. The patient received metronomic chemotherapy and immunomodulatory therapy, a good clinical response was observed after three cycles of treatment.