Regulation of NUMB alternative splicing by RBM10 and control of cancer cell proliferation

Alternative pre-mRNA splicing of the Notch regulator NUMB exon 9 switches between isoforms that promote (exon inclusion) or prevent (exon skipping) cell proliferation. We have studied NUMB alternative splicing regulation by RBM10, an RNA binding protein frequently utated in lung adenocarcinomas. The...

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Detalles Bibliográficos
Autor: Hernández Ribera, Jordi
Tipo de recurso: tesis doctoral
Estado:Versión publicada
Fecha de publicación:2016
País:España
Institución:CBUC, CESCA
Repositorio:TDR. Tesis Doctorales en Red
OAI Identifier:oai:www.tdx.cat:10803/458766
Acceso en línea:http://hdl.handle.net/10803/458766
Access Level:acceso abierto
Palabra clave:RBM10
NUMB
Lung Cancer
Càncer de pulmó
Alternative splicing
Empalmament alternatiu
577
Descripción
Sumario:Alternative pre-mRNA splicing of the Notch regulator NUMB exon 9 switches between isoforms that promote (exon inclusion) or prevent (exon skipping) cell proliferation. We have studied NUMB alternative splicing regulation by RBM10, an RNA binding protein frequently utated in lung adenocarcinomas. The study of cancer-associated BM10 variants revealed domains and residues important for RBM10 function. Structure-function analysis identified residues in RRM2 that, without compromising RNA binding, fail to regulate NUMB exon 9. Immunoprecipitation and mass spectrometry analyses revealed interactors that include U2 snRNP and PRP19 spliceosomal components, allowing us to propose a mechanism for 3' splice site repression by RBM10.