Epidemiological patterns and in-hospital mortality in ANCA-associated vasculitis: Insights from Spain's National Health Data (2016-2022)

[EN]ANCA-associated vasculitis (AAV), including granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA), and eosinophilic granulomatosis with polyangiitis (EGPA), is a systemic autoimmune disease. This study represents the first large-scale analysis of AAV hospitalisation rates and in...

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Detalhes bibliográficos
Autores: Cordero Pérez, Francisco Josué, Martínez Rodríguez, Pablo, Arribas-Pérez, Luis, Puertas Miranda, David, Pires-Baltazar, Carlos-Rafael, Salcedo-Martín, Leticia, Sánchez-Villoria, Juan Antonio, Díaz-Ávila, Erik Gabriel, Ternavasio de la Vega, Hugo Guillermo, Marcos Martín, Miguel, Chamorro Fernández, Antonio Javier
Formato: artículo
Estado:Versión publicada
Fecha de publicación:2025
País:España
Recursos:Universidad de Salamanca (USAL)
Repositorio:GREDOS. Repositorio Institucional de la Universidad de Salamanca
OAI Identifier:oai:gredos.usal.es:10366/168217
Acesso em linha:http://hdl.handle.net/10366/168217
Access Level:acceso abierto
Palavra-chave:ANCA-associated vasculitis
Eosinophilic granulomatosis with polyangiitis
Epidemiology
Granulomatosis with polyangiitis
Microscopic polyangiitis
Mortality
Hospitalization
Aged
Adult
Hospital Mortality
Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis
Humans
Middle Aged
Retrospective Studies
Longitudinal Studies
hospitalización
adulto
mortalidad hospitalaria
vasculitis asociada a anticuerpos anticitoplasma de neutrófilos
humanos
anciano
estudios longitudinales
mediana edad
estudios retrospectivos
Descrição
Resumo:[EN]ANCA-associated vasculitis (AAV), including granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA), and eosinophilic granulomatosis with polyangiitis (EGPA), is a systemic autoimmune disease. This study represents the first large-scale analysis of AAV hospitalisation rates and in-hospital mortality trends in Spain. A retrospective longitudinal analysis of AAV-related hospital admissions between 2016 and 2022 was conducted using the ICD-10 codes from the Minimum Basic Dataset (MBDS) of the Spanish National Health System. Statistical analyses were performed, including odds ratios, Student's t-tests, and Mantel-Haenszel trend tests. Among 5753 AAV episodes, GPA was the most frequent subtype (53.9 %), followed by MPA (31.5 %) and EGPA (14.6 %). AAV episodes were more frequent in older patients (> 65 years) than in other hospital episodes (62.9 % vs. 38.9 %; OR: 2.66, 95 %CI: 2.51-2.80; P < 0.001). Larger hospitals accounted for more AAV episodes, longer hospital stays, and higher costs. MPA had the highest mortality rate (7.2 % vs. 4.9 %; OR: 1.52, 95 % CI: 1.27-1.79; P < 0.001), particularly in patients over 65 years (83.1 % vs. 61.8 %; OR: 3.04, 95 % CI: 2.47-3.75; P < 0.001) compared with the other AAV. In the GPA group, renal involvement significantly increased mortality compared to GPA cases without renal involvement (6.6 % vs. 4.6 %; OR: 1.46, 95 % CI: 1.16-1.83; P = 0.011). Notably, the relative risk of AAV-related deaths increased over the study period (Z = 2.77, P < 0.01). AAV, particularly MPA, is associated with increased hospital mortality, particularly among older adults and patients with renal involvement.