Topical Imiquimod in Primary Cutaneous Extramammary Paget’s Disease: A Systematic Review

Extramammary Paget’s disease (EMPD) is subclinical in extent and multifocal in nature. There is no global consensus for treatment, so its management represents a challenge in clinical practice. Therefore, we conducted a systematic review through the main electronic databases to assess the effectiven...

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Detalles Bibliográficos
Autores: Mayo-Martínez, Fátima, Moro, Ruggero, Millán Esteban, David, Ríos-Viñuela, Elisa, Javier Bautista, Iker, Nagore Enguidanos, Eduardo, Sanmartín Jiménez, Onofre, Llombart Cussac, Beatriz
Tipo de recurso: artículo
Fecha de publicación:2023
País:España
Institución:Universidad Católica de Valencia San Vicente Mártir
Repositorio:RIUCV. Repositorio de la Universidad Católica de Valencia San Vicente Mártir
Idioma:inglés
OAI Identifier:oai:riucv.ucv.es:20.500.12466/4229
Acceso en línea:http://hdl.handle.net/20.500.12466/4229
Access Level:acceso abierto
Palabra clave:Imiquimod
Topical immunotherapy
Extramammary Paget’s disease
Vulvar Paget’s disease
Extramammary Paget disease
Scrotal Paget’s disease
Perianal Paget’s disease
Cutaneous Paget’s disease
Treatment
32 Ciencias Médicas
Descripción
Sumario:Extramammary Paget’s disease (EMPD) is subclinical in extent and multifocal in nature. There is no global consensus for treatment, so its management represents a challenge in clinical practice. Therefore, we conducted a systematic review through the main electronic databases to assess the effectiveness of topical imiquimod in cutaneous EMPD and to discuss its management. Finally, 24 studies involving a total of 233 EMPD patients treated with topical imiquimod were selected. The topical imiquimod response rate was 67%, and the complete response (CR) rate was 48%. Patients were treated with a three–four times a week regimen in most cases, ranging between 2 to 52 weeks. In addition, imiquimod was applied as an adjunctive treatment in 21 patients, achieving a CR rate of 71%. Consequently, imiquimod therapy could achieve a good response ratio as a first-line treatment, as adjuvant and neo-adjuvant therapy, and as a treatment for recurrent disease. The heterogeneity between studies and the lack of a control arm made it impossible to conduct a meta-analysis. To improve the quality of evidence on EMPD, multicenter studies are essential to collect a larger number of patients and, consequently, obtain high-quality evidence to standardize treatment. The Prospero registration number is CRD42023447443.