Extramammary Paget's Disease in Perineo-inguinoscrotal Region

Extramammary Paget’s Disease is a rare disease. There is a dose correlation with anorrectal carcinoma when the disease is perianal. It is also associated with internal malignancies and bad prognosis. The authors describe a case of extramammary Paget’s Disease in perineo-inguinoscrotal region of a 59...

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Detalhes bibliográficos
Autores: Junqueira Júnior, Gérson, Amaral, Renato Luiz, Vedovato, Julio Walter, Torres, Olavo Machado, Santos, Wellington Gemelli dos, Silva, Adriano de Lima e, Cartell, André
Tipo de documento: artigo
Estado:Versão publicada
Data de publicação:2022
País:Brasil
Recursos:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
Repositório:Revista Brasileira de Cancerologia (Online)
Idioma:português
OAI Identifier:oai:rbc.inca.gov.br:article/2784
Acesso em linha:https://rbc.inca.gov.br/index.php/revista/article/view/2784
Access Level:Acceso aberto
Palavra-chave:Doença de Paget
Extramamária
Pele
Neoplasias Malignas
Paget’s Disease
Extramammary
Skin
Malignant Neoplasms
Descrição
Resumo:Extramammary Paget’s Disease is a rare disease. There is a dose correlation with anorrectal carcinoma when the disease is perianal. It is also associated with internal malignancies and bad prognosis. The authors describe a case of extramammary Paget’s Disease in perineo-inguinoscrotal region of a 59-year-old-white man, who had a hyperpigmented and pruritic lesion of approximately 6 cm of diameter which has increased and was presenting minimum bleeding. Staging tests were normal, without evidence of metastasis. The anatomopathological test of the lesion revealed na aspect compatible with extramammary Paget’s Disease. The patient was submmited to an enlarged excision of the lesion and thin skin graft. The aspects related to epidemiology, pathology, staging, prognosis and treatment of this neoplasia are discussed in this article.