National consensus on the cardiological treatment and follow-up of Kawasaki disease

Kawasaki disease is a self-limiting acute vasculitis that affects small and medium-sized vessels, and is the most common cause of acquired heart disease in children in our environment. Up to 25% of untreated patients develop coronary aneurysms. It is suspected that an infectious agent may be the tri...

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Detalhes bibliográficos
Autores: Sombrero, HR, Fernandez-Cooke, E, Sanchez-Manubens, J, Picarzo, JPL, de la Torre, LA, Alvarez-Fuente, M, Garcia, GG, Gutierrez-Larraya, F, Vazquez, BT, McMullan, PD, Perez, GA, Arboledas, FJA, Martin, CA, Echauri, JA, Garcia, PA, Arevalo, P, Rofes, AA, Sanchez, MA, Domingo, EJB, Rodrigo, AB, Abbona, MSB, Fernandez, IB, Tascon, AB, Torralva, CMB, Jover, EB, Rodriguez, CB, Trigo, SB, Sayago, MJB, Diaz, MJC, Tejedor, MTC, Moreno, JIC, Blesa, CC, Bellon, JMC, Cassanello, MP, Malfaz, FC, Spoturno, ACC, Hernandez, RC, Orvay, JAC, Marcos, DC, Manotas, HAC, Peiro, VC, de Caro, AP, Cancho, MD, Iglesias, LAD, Bronte, LD, Menendez, BD, Megias, LD, Tomas, JJD, Colina, PD, Garcia, OD, Garrido, MND, Manzano, PD, Bedoya, JD, Espinosa, JE, Nava, FEE, Pinela, HDE, Asenjo, ME, Ruiz, APF, Aracama, JF, Sarabia, JF, Soria, MTF, Suarez, NF, Belda, AF, Villar, SF, Garcia, JF, Moure, AF, de Vinuesa, APGG, Arzoz, MG, Angleu, FG, Cerro, EG, Rodriguez-Monte, MEGL, Villanueva, NG, Crespo, MG, Carrasco, MEG, Marin, MAG, Menchen, CG, Ipina, FG, Rodriguez, IG, Esteve, MTG, Gomez, MH, Blanco, AH, Sanchez, YH, del Rey, CH, Fernandez, AI, Martin, GI, Fos, II, Riezu, MAI, Casso, MSJ, Montanes, LJ, de Lera, CL, Navarro, LL, Abel, BL, Balseiro, ML, Gonzalez, JL, Julian, NM, Cazcarra, JAM, Toral, MJM, Linero, AM, Garcia, BM, Llagaria, MM, Alonso, SM, Blanch, CM, de Lara, IM, del Villar, MM, Lorente, MIM, Oloron, PM, Soto, MIM, Checa, LM, Morillo, MAM, Lopez, CM, Abad, PM, Ortiz, FM, Gutierrez, AM, Tirado, AM, Montes, AO, Matamala, AO, Garrido, AO, Erroz, IO, Argueta, JRP, Aguera, LP, Molina, EP, Salas, JEP, Carrillo, CJP, Campos, DP, Herrera, VP, Agapito, MAPM, Munuzuri, AP, Pardo, AMP, Roldan, JMP, Picarzo, FJPL, Moreno, MRPP, Perin, F, Fuentes, IP, Izquierdo, BP, Morales, MP, Dalmau, MAP, Ovalle, EP, Poveda, MTR, Rodriguez, SR, Garcia, SMR, Arcelus, ER, Mendez, BR, Armada, AR, Jimenez, NR, Gonzalez, MR, Mesa, MDR, Serrano, RR, Sombrero, MHR, Barba, VR, Ibarra, CR, Vivas, FR, Nunez, FR, Soriano, JR, Rotes, AS, Salguero, FJS, Capunay, JFS, Peracaula, CS, Andres, AS, Calderon, AS, Vaquerizo, CS, Pascual, ES, Robles, MIS, Sanchez-Manjavacas, AS, Baladron, AS, Garcia, RS, Belmonte, DS, Garcia, MS, Cabrera, PS, Moreno, ATM, Moreno, RTM, Hernandez, MAT, Rico, MT, Prat, SU, Carrasco, AIU, Padrino, EV, Adan, MTV, Albert, SV, Nogales, JV, Walter, CC, Martin, MY, Casajona, MDZ, SECPCC
Formato: artículo
Estado:Versión publicada
Fecha de publicación:2018
País:España
Recursos:Instituto de Investigación Biomédica y Sanitaria de Alicante (ISABIAL)
Repositorio:r-ISABIAL. Repositorio Institucional de Producción Científica del Instituto de Investigación Biomédica y Sanitaria de Alicante
OAI Identifier:oai:isabial.fundanetsuite.com:p8033
Acesso em linha:https://isabial.portalinvestigacion.com/publicaciones8033
Access Level:acceso abierto
Palavra-chave:Kawasaki disease
Mucocutaneous lymphnode syndrome
Vasculitis
Arteritis
Coronary aneurysm
Coronary vessels
Aneurysm
Immunoglobulins
intravenous
Steroids
Consensus
id ES_cd93e1580dc7babda39edf1517490f01
oai_identifier_str oai:isabial.fundanetsuite.com:p8033
network_acronym_str ES
network_name_str España
repository_id_str
dc.title.none.fl_str_mv National consensus on the cardiological treatment and follow-up of Kawasaki disease
title National consensus on the cardiological treatment and follow-up of Kawasaki disease
spellingShingle National consensus on the cardiological treatment and follow-up of Kawasaki disease
Sombrero, HR
Kawasaki disease
Mucocutaneous lymphnode syndrome
Vasculitis
Arteritis
Coronary aneurysm
Coronary vessels
Aneurysm
Immunoglobulins
intravenous
Steroids
Consensus
title_short National consensus on the cardiological treatment and follow-up of Kawasaki disease
title_full National consensus on the cardiological treatment and follow-up of Kawasaki disease
title_fullStr National consensus on the cardiological treatment and follow-up of Kawasaki disease
title_full_unstemmed National consensus on the cardiological treatment and follow-up of Kawasaki disease
title_sort National consensus on the cardiological treatment and follow-up of Kawasaki disease
dc.creator.none.fl_str_mv Sombrero, HR
Fernandez-Cooke, E
Sanchez-Manubens, J
Picarzo, JPL
de la Torre, LA
Alvarez-Fuente, M
Garcia, GG
Gutierrez-Larraya, F
Vazquez, BT
McMullan, PD
Perez, GA
Arboledas, FJA
Martin, CA
Echauri, JA
Garcia, PA
Arevalo, P
Rofes, AA
Sanchez, MA
Domingo, EJB
Rodrigo, AB
Abbona, MSB
Fernandez, IB
Tascon, AB
Torralva, CMB
Jover, EB
Rodriguez, CB
Trigo, SB
Sayago, MJB
Diaz, MJC
Tejedor, MTC
Moreno, JIC
Blesa, CC
Bellon, JMC
Cassanello, MP
Malfaz, FC
Spoturno, ACC
Hernandez, RC
Orvay, JAC
Marcos, DC
Manotas, HAC
Peiro, VC
de Caro, AP
Cancho, MD
Iglesias, LAD
Bronte, LD
Menendez, BD
Megias, LD
Tomas, JJD
Colina, PD
Garcia, OD
Garrido, MND
Manzano, PD
Bedoya, JD
Espinosa, JE
Nava, FEE
Pinela, HDE
Asenjo, ME
Ruiz, APF
Aracama, JF
Sarabia, JF
Soria, MTF
Suarez, NF
Belda, AF
Villar, SF
Garcia, JF
Moure, AF
de Vinuesa, APGG
Arzoz, MG
Angleu, FG
Cerro, EG
Rodriguez-Monte, MEGL
Villanueva, NG
Crespo, MG
Garcia, GG
Carrasco, MEG
Marin, MAG
Menchen, CG
Ipina, FG
Rodriguez, IG
Esteve, MTG
Gomez, MH
Blanco, AH
Sanchez, YH
del Rey, CH
Fernandez, AI
Martin, GI
Fos, II
Riezu, MAI
Casso, MSJ
Montanes, LJ
de Lera, CL
Navarro, LL
Abel, BL
Balseiro, ML
Gonzalez, JL
Julian, NM
Cazcarra, JAM
Toral, MJM
Linero, AM
Garcia, BM
Llagaria, MM
Alonso, SM
Blanch, CM
de Lara, IM
del Villar, MM
Lorente, MIM
Oloron, PM
Soto, MIM
Checa, LM
Morillo, MAM
Lopez, CM
Abad, PM
Ortiz, FM
Gutierrez, AM
Tirado, AM
Montes, AO
Matamala, AO
Garrido, AO
Erroz, IO
Argueta, JRP
Aguera, LP
Molina, EP
Salas, JEP
Carrillo, CJP
Campos, DP
Herrera, VP
Agapito, MAPM
Munuzuri, AP
Pardo, AMP
Roldan, JMP
Picarzo, FJPL
Moreno, MRPP
Perin, F
Fuentes, IP
Izquierdo, BP
Morales, MP
Dalmau, MAP
Ovalle, EP
Poveda, MTR
Rodriguez, SR
Garcia, SMR
Arcelus, ER
Mendez, BR
Armada, AR
Jimenez, NR
Gonzalez, MR
Mesa, MDR
Serrano, RR
Sombrero, MHR
Barba, VR
Ibarra, CR
Vivas, FR
Nunez, FR
Soriano, JR
Rotes, AS
Salguero, FJS
Capunay, JFS
Peracaula, CS
Andres, AS
Calderon, AS
Vaquerizo, CS
Pascual, ES
Robles, MIS
Sanchez-Manjavacas, AS
Baladron, AS
Garcia, RS
Belmonte, DS
Garcia, MS
Cabrera, PS
Moreno, ATM
Moreno, RTM
Hernandez, MAT
Rico, MT
Prat, SU
Carrasco, AIU
Padrino, EV
Adan, MTV
Albert, SV
Nogales, JV
Walter, CC
Martin, MY
Casajona, MDZ
SECPCC
author Sombrero, HR
author_facet Sombrero, HR
Fernandez-Cooke, E
Sanchez-Manubens, J
Picarzo, JPL
de la Torre, LA
Alvarez-Fuente, M
Garcia, GG
Gutierrez-Larraya, F
Vazquez, BT
McMullan, PD
Perez, GA
Arboledas, FJA
Martin, CA
Echauri, JA
Garcia, PA
Arevalo, P
Rofes, AA
Sanchez, MA
Domingo, EJB
Rodrigo, AB
Abbona, MSB
Fernandez, IB
Tascon, AB
Torralva, CMB
Jover, EB
Rodriguez, CB
Trigo, SB
Sayago, MJB
Diaz, MJC
Tejedor, MTC
Moreno, JIC
Blesa, CC
Bellon, JMC
Cassanello, MP
Malfaz, FC
Spoturno, ACC
Hernandez, RC
Orvay, JAC
Marcos, DC
Manotas, HAC
Peiro, VC
de Caro, AP
Cancho, MD
Iglesias, LAD
Bronte, LD
Menendez, BD
Megias, LD
Tomas, JJD
Colina, PD
Garcia, OD
Garrido, MND
Manzano, PD
Bedoya, JD
Espinosa, JE
Nava, FEE
Pinela, HDE
Asenjo, ME
Ruiz, APF
Aracama, JF
Sarabia, JF
Soria, MTF
Suarez, NF
Belda, AF
Villar, SF
Garcia, JF
Moure, AF
de Vinuesa, APGG
Arzoz, MG
Angleu, FG
Cerro, EG
Rodriguez-Monte, MEGL
Villanueva, NG
Crespo, MG
Carrasco, MEG
Marin, MAG
Menchen, CG
Ipina, FG
Rodriguez, IG
Esteve, MTG
Gomez, MH
Blanco, AH
Sanchez, YH
del Rey, CH
Fernandez, AI
Martin, GI
Fos, II
Riezu, MAI
Casso, MSJ
Montanes, LJ
de Lera, CL
Navarro, LL
Abel, BL
Balseiro, ML
Gonzalez, JL
Julian, NM
Cazcarra, JAM
Toral, MJM
Linero, AM
Garcia, BM
Llagaria, MM
Alonso, SM
Blanch, CM
de Lara, IM
del Villar, MM
Lorente, MIM
Oloron, PM
Soto, MIM
Checa, LM
Morillo, MAM
Lopez, CM
Abad, PM
Ortiz, FM
Gutierrez, AM
Tirado, AM
Montes, AO
Matamala, AO
Garrido, AO
Erroz, IO
Argueta, JRP
Aguera, LP
Molina, EP
Salas, JEP
Carrillo, CJP
Campos, DP
Herrera, VP
Agapito, MAPM
Munuzuri, AP
Pardo, AMP
Roldan, JMP
Picarzo, FJPL
Moreno, MRPP
Perin, F
Fuentes, IP
Izquierdo, BP
Morales, MP
Dalmau, MAP
Ovalle, EP
Poveda, MTR
Rodriguez, SR
Garcia, SMR
Arcelus, ER
Mendez, BR
Armada, AR
Jimenez, NR
Gonzalez, MR
Mesa, MDR
Serrano, RR
Sombrero, MHR
Barba, VR
Ibarra, CR
Vivas, FR
Nunez, FR
Soriano, JR
Rotes, AS
Salguero, FJS
Capunay, JFS
Peracaula, CS
Andres, AS
Calderon, AS
Vaquerizo, CS
Pascual, ES
Robles, MIS
Sanchez-Manjavacas, AS
Baladron, AS
Garcia, RS
Belmonte, DS
Garcia, MS
Cabrera, PS
Moreno, ATM
Moreno, RTM
Hernandez, MAT
Rico, MT
Prat, SU
Carrasco, AIU
Padrino, EV
Adan, MTV
Albert, SV
Nogales, JV
Walter, CC
Martin, MY
Casajona, MDZ
SECPCC
author_role author
author2 Fernandez-Cooke, E
Sanchez-Manubens, J
Picarzo, JPL
de la Torre, LA
Alvarez-Fuente, M
Garcia, GG
Gutierrez-Larraya, F
Vazquez, BT
McMullan, PD
Perez, GA
Arboledas, FJA
Martin, CA
Echauri, JA
Garcia, PA
Arevalo, P
Rofes, AA
Sanchez, MA
Domingo, EJB
Rodrigo, AB
Abbona, MSB
Fernandez, IB
Tascon, AB
Torralva, CMB
Jover, EB
Rodriguez, CB
Trigo, SB
Sayago, MJB
Diaz, MJC
Tejedor, MTC
Moreno, JIC
Blesa, CC
Bellon, JMC
Cassanello, MP
Malfaz, FC
Spoturno, ACC
Hernandez, RC
Orvay, JAC
Marcos, DC
Manotas, HAC
Peiro, VC
de Caro, AP
Cancho, MD
Iglesias, LAD
Bronte, LD
Menendez, BD
Megias, LD
Tomas, JJD
Colina, PD
Garcia, OD
Garrido, MND
Manzano, PD
Bedoya, JD
Espinosa, JE
Nava, FEE
Pinela, HDE
Asenjo, ME
Ruiz, APF
Aracama, JF
Sarabia, JF
Soria, MTF
Suarez, NF
Belda, AF
Villar, SF
Garcia, JF
Moure, AF
de Vinuesa, APGG
Arzoz, MG
Angleu, FG
Cerro, EG
Rodriguez-Monte, MEGL
Villanueva, NG
Crespo, MG
Carrasco, MEG
Marin, MAG
Menchen, CG
Ipina, FG
Rodriguez, IG
Esteve, MTG
Gomez, MH
Blanco, AH
Sanchez, YH
del Rey, CH
Fernandez, AI
Martin, GI
Fos, II
Riezu, MAI
Casso, MSJ
Montanes, LJ
de Lera, CL
Navarro, LL
Abel, BL
Balseiro, ML
Gonzalez, JL
Julian, NM
Cazcarra, JAM
Toral, MJM
Linero, AM
Garcia, BM
Llagaria, MM
Alonso, SM
Blanch, CM
de Lara, IM
del Villar, MM
Lorente, MIM
Oloron, PM
Soto, MIM
Checa, LM
Morillo, MAM
Lopez, CM
Abad, PM
Ortiz, FM
Gutierrez, AM
Tirado, AM
Montes, AO
Matamala, AO
Garrido, AO
Erroz, IO
Argueta, JRP
Aguera, LP
Molina, EP
Salas, JEP
Carrillo, CJP
Campos, DP
Herrera, VP
Agapito, MAPM
Munuzuri, AP
Pardo, AMP
Roldan, JMP
Picarzo, FJPL
Moreno, MRPP
Perin, F
Fuentes, IP
Izquierdo, BP
Morales, MP
Dalmau, MAP
Ovalle, EP
Poveda, MTR
Rodriguez, SR
Garcia, SMR
Arcelus, ER
Mendez, BR
Armada, AR
Jimenez, NR
Gonzalez, MR
Mesa, MDR
Serrano, RR
Sombrero, MHR
Barba, VR
Ibarra, CR
Vivas, FR
Nunez, FR
Soriano, JR
Rotes, AS
Salguero, FJS
Capunay, JFS
Peracaula, CS
Andres, AS
Calderon, AS
Vaquerizo, CS
Pascual, ES
Robles, MIS
Sanchez-Manjavacas, AS
Baladron, AS
Garcia, RS
Belmonte, DS
Garcia, MS
Cabrera, PS
Moreno, ATM
Moreno, RTM
Hernandez, MAT
Rico, MT
Prat, SU
Carrasco, AIU
Padrino, EV
Adan, MTV
Albert, SV
Nogales, JV
Walter, CC
Martin, MY
Casajona, MDZ
SECPCC
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dc.subject.none.fl_str_mv Kawasaki disease
Mucocutaneous lymphnode syndrome
Vasculitis
Arteritis
Coronary aneurysm
Coronary vessels
Aneurysm
Immunoglobulins
intravenous
Steroids
Consensus
topic Kawasaki disease
Mucocutaneous lymphnode syndrome
Vasculitis
Arteritis
Coronary aneurysm
Coronary vessels
Aneurysm
Immunoglobulins
intravenous
Steroids
Consensus
description Kawasaki disease is a self-limiting acute vasculitis that affects small and medium-sized vessels, and is the most common cause of acquired heart disease in children in our environment. Up to 25% of untreated patients develop coronary aneurysms. It is suspected that an infectious agent may be the trigger of the disease, but the causative agent is still unknown. Based on the previous evidence, recommendations are proposed for the diagnosis, treatment of acute disease, and the long-term management of these patients, in order to unify criteria. The diagnosis must be quick, based on easy-to-use algorithms and with the support of complementary tests. This document includes the indication of available imaging techniques, as well as the planning of cardiological examinations based on the initial involvement. Intravenous immunoglobulin is the basis of the initial treatment. The role of corticosteroids is still controversial, but there are studies that support its use as adjuvant treatment. A multidisciplinary working group has developed a scheme with different treatment guidelines depending on the risk factors at diagnosis, the patient's clinical situation, and response to previous treatment, including indications for thromboprophylaxis in patients with coronary involvement. The stratification of risk for long-term treatment is essential, as well as the recommendations on the procedures based on the initial cardiological involvement and its progression. Patients with coronary aneurysms require continuous and uninterrupted cardiological monitoring for life. (C) 2018 Asociacion Espanola de Pediatria. Published by Elsevier Espana, S.L.U.
publishDate 2018
dc.date.none.fl_str_mv 2018
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://isabial.portalinvestigacion.com/publicaciones8033
url https://isabial.portalinvestigacion.com/publicaciones8033
dc.language.none.fl_str_mv Español
language_invalid_str_mv Español
dc.rights.none.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.publisher.none.fl_str_mv EDICIONES DOYMA S A
publisher.none.fl_str_mv EDICIONES DOYMA S A
dc.source.none.fl_str_mv ANALES DE PEDIATRIA
ISSN: 16954033
ISSNe: 16959531
reponame:r-ISABIAL. Repositorio Institucional de Producción Científica del Instituto de Investigación Biomédica y Sanitaria de Alicante
instname:Instituto de Investigación Biomédica y Sanitaria de Alicante (ISABIAL)
instname_str Instituto de Investigación Biomédica y Sanitaria de Alicante (ISABIAL)
reponame_str r-ISABIAL. Repositorio Institucional de Producción Científica del Instituto de Investigación Biomédica y Sanitaria de Alicante
collection r-ISABIAL. Repositorio Institucional de Producción Científica del Instituto de Investigación Biomédica y Sanitaria de Alicante
repository.name.fl_str_mv
repository.mail.fl_str_mv
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spelling National consensus on the cardiological treatment and follow-up of Kawasaki diseaseSombrero, HRFernandez-Cooke, ESanchez-Manubens, JPicarzo, JPLde la Torre, LAAlvarez-Fuente, MGarcia, GGGutierrez-Larraya, FVazquez, BTMcMullan, PDPerez, GAArboledas, FJAMartin, CAEchauri, JAGarcia, PAArevalo, PRofes, AASanchez, MADomingo, EJBRodrigo, ABAbbona, MSBFernandez, IBTascon, ABTorralva, CMBJover, EBRodriguez, CBTrigo, SBSayago, MJBDiaz, MJCTejedor, MTCMoreno, JICBlesa, CCBellon, JMCCassanello, MPMalfaz, FCSpoturno, ACCHernandez, RCOrvay, JACMarcos, DCManotas, HACPeiro, VCde Caro, APCancho, MDIglesias, LADBronte, LDMenendez, BDMegias, LDTomas, JJDColina, PDGarcia, ODGarrido, MNDManzano, PDBedoya, JDEspinosa, JENava, FEEPinela, HDEAsenjo, MERuiz, APFAracama, JFSarabia, JFSoria, MTFSuarez, NFBelda, AFVillar, SFGarcia, JFMoure, AFde Vinuesa, APGGArzoz, MGAngleu, FGCerro, EGRodriguez-Monte, MEGLVillanueva, NGCrespo, MGGarcia, GGCarrasco, MEGMarin, MAGMenchen, CGIpina, FGRodriguez, IGEsteve, MTGGomez, MHBlanco, AHSanchez, YHdel Rey, CHFernandez, AIMartin, GIFos, IIRiezu, MAICasso, MSJMontanes, LJde Lera, CLNavarro, LLAbel, BLBalseiro, MLGonzalez, JLJulian, NMCazcarra, JAMToral, MJMLinero, AMGarcia, BMLlagaria, MMAlonso, SMBlanch, CMde Lara, IMdel Villar, MMLorente, MIMOloron, PMSoto, MIMCheca, LMMorillo, MAMLopez, CMAbad, PMOrtiz, FMGutierrez, AMTirado, AMMontes, AOMatamala, AOGarrido, AOErroz, IOArgueta, JRPAguera, LPMolina, EPSalas, JEPCarrillo, CJPCampos, DPHerrera, VPAgapito, MAPMMunuzuri, APPardo, AMPRoldan, JMPPicarzo, FJPLMoreno, MRPPPerin, FFuentes, IPIzquierdo, BPMorales, MPDalmau, MAPOvalle, EPPoveda, MTRRodriguez, SRGarcia, SMRArcelus, ERMendez, BRArmada, ARJimenez, NRGonzalez, MRMesa, MDRSerrano, RRSombrero, MHRBarba, VRIbarra, CRVivas, FRNunez, FRSoriano, JRRotes, ASSalguero, FJSCapunay, JFSPeracaula, CSAndres, ASCalderon, ASVaquerizo, CSPascual, ESRobles, MISSanchez-Manjavacas, ASBaladron, ASGarcia, RSBelmonte, DSGarcia, MSCabrera, PSMoreno, ATMMoreno, RTMHernandez, MATRico, MTPrat, SUCarrasco, AIUPadrino, EVAdan, MTVAlbert, SVNogales, JVWalter, CCMartin, MYCasajona, MDZSECPCCKawasaki diseaseMucocutaneous lymphnode syndromeVasculitisArteritisCoronary aneurysmCoronary vesselsAneurysmImmunoglobulinsintravenousSteroidsConsensusKawasaki disease is a self-limiting acute vasculitis that affects small and medium-sized vessels, and is the most common cause of acquired heart disease in children in our environment. Up to 25% of untreated patients develop coronary aneurysms. It is suspected that an infectious agent may be the trigger of the disease, but the causative agent is still unknown. Based on the previous evidence, recommendations are proposed for the diagnosis, treatment of acute disease, and the long-term management of these patients, in order to unify criteria. The diagnosis must be quick, based on easy-to-use algorithms and with the support of complementary tests. This document includes the indication of available imaging techniques, as well as the planning of cardiological examinations based on the initial involvement. Intravenous immunoglobulin is the basis of the initial treatment. The role of corticosteroids is still controversial, but there are studies that support its use as adjuvant treatment. A multidisciplinary working group has developed a scheme with different treatment guidelines depending on the risk factors at diagnosis, the patient's clinical situation, and response to previous treatment, including indications for thromboprophylaxis in patients with coronary involvement. The stratification of risk for long-term treatment is essential, as well as the recommendations on the procedures based on the initial cardiological involvement and its progression. Patients with coronary aneurysms require continuous and uninterrupted cardiological monitoring for life. (C) 2018 Asociacion Espanola de Pediatria. Published by Elsevier Espana, S.L.U.EDICIONES DOYMA S A2018info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionhttps://isabial.portalinvestigacion.com/publicaciones8033ANALES DE PEDIATRIAISSN: 16954033ISSNe: 16959531reponame:r-ISABIAL. Repositorio Institucional de Producción Científica del Instituto de Investigación Biomédica y Sanitaria de Alicanteinstname:Instituto de Investigación Biomédica y Sanitaria de Alicante (ISABIAL)Españolinfo:eu-repo/semantics/openAccessoai:isabial.fundanetsuite.com:p80332026-06-12T10:20:37Z
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