National consensus on the cardiological treatment and follow-up of Kawasaki disease

Kawasaki disease is a self-limiting acute vasculitis that affects small and medium-sized vessels, and is the most common cause of acquired heart disease in children in our environment. Up to 25% of untreated patients develop coronary aneurysms. It is suspected that an infectious agent may be the tri...

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Autores: Barrios Tascon, Ana, Centeno Malfaz, Fernando, Rojo Sombrero, Henar, Fernandez-Cooke, Elisa, Sanchez-Manubens, Judith, Perez-Lescure Picarzo, Javier, Albert de la Torre, Leticia, Alcalde Martin, Carlos, Alvarez-Fuente, Maria, Blanco Rodriguez, Carolina, Giralt Garcia, Gemma, Gutierrez-Larraya, Federico, Latorre Navarro, Libertad, Sanchez Andres, Antonio, Toral Vazquez, Belen, de Vera McMullan, Paula, Akel Perez, Georges, Alados Arboledas, Francisco Javier, Alegria Echauri, Josune, Aparicio Garcia, Patricia, Arevalo, Paola, Armengol Rofes, August, Arroyas Sanchez, Maria, Balbacid Domingo, Enrique Jose, Bano Rodrigo, Antonio, Barcudi Abbona, Maria Silvina, Barranco Fernandez, Isabel, Bernaldez Torralva, Clara Maria, Blanca Jover, Enrique, Blazquez Trigo, Sonia, Bravo Sayago, Maria Jose, Caldeiro Diaz, Maria Jesus, Cantero Tejedor, Maria Teresa, Carrasco Moreno, Jose Ignacio, Carreras Blesa, Carmen, Carretero Bellon, Juan Manuel, Pia Cassanello, Maria, Cis Spoturno, Adela Cristina, Collell Hernandez, Rosa, Costa Orvay, Juan Antonio, Crespo Marcos, David, Cuellar Manotas, Hector Augusto, Cuenca Peiro, Victorio, Patricia de Caro, Adalgisa, de la Parte Cancho, Maria, Degano Iglesias, Lucas Alberto, Deiros Bronte, Lucia, del Pozo Menendez, Beatriz, del Rey Megias, Laura, Diez Tomas, Juan Jose, Dolader Colina, Paola, Dominguez Garcia, Olga, Dominguez Garrido, Maria Nieves, Dominguez Manzano, Paula, Duque Bedoya, Jesus, Echeverria Espinosa, Javier, Echeverria Nava, Fidel Ernesto, Escobar Pinela, Hemir David, Esquivias Asenjo, Maria, Farina Ruiz, Ana Patricia, Fernandez Aracama, Javier, Fernandez Sarabia, Javier, Fernandez Soria, Maria Teresa, Fernandez Suarez, Natalia, Ferre Belda, Aina, Flores Villar, Sergio, Fontenla Garcia, Julio, Fuertes Moure, Angeles, Garcia de Vinuesa, Antonia Pastora Gailego, Gambra Arzoz, Marta, Garcia Angleu, Francisco, Garcia Cerro, Estefania, Garrido-Lestache Rodriguez-Monte, Maria Elvira, Gil Villanueva, Nuria, Giner Crespo, Maribel, Giralt Garcia, Gema, Gonzalez Carrasco, Maria Ersilia, Gonzalez Marin, Maria Aranzazu, Gonzalez Menchen, Cristina, Gran Ipina, Fernando, Guillen Rodriguez, Inmaculada, Guixeres Esteve, Maria Teresa, Haro Gomez, Manuel, Hernandez Blanco, Aida, Herranz Sanchez, Yolanda, Herrera del Rey, Carmen, Ibanez Fernandez, Aleida, Inigo Martin, Gema, Izquierdo Fos, Ignacio, Izquierdo Riezu, Maria Angeles, Jimenez Casso, Maria Soledad, Jimenez Montanes, Lorenzo, Labrandero de Lera, Carlos, Lopez Abel, Bernardo, Lozano Balseiro, Maria, Luaces Gonzalez, Jose, Macias Julian, Nazaret, Mairal Cazcarra, Jesus Antonio, Maldonado Toral, Maria Jose, Manchola Linero, Alejandra, Manso Garcia, Begona, Maravall Llagaria, Maria, Marcos Alonso, Sonia, Marimon Blanch, Cristina, Martin de Lara, Ismael, Martinez del Villar, Maria, Martinez Lorente, Maria Isabel, Martinez Oloron, Patricia, Martinez Soto, Maria Isabel, Marzo Checa, Laura, Matamala Morillo, Miguel Angel, Medrano Lopez, Constancio, Mendez Abad, Paula, Meza Ortiz, Francisco, Moriano Gutierrez, Ana, Moruno Tirado, Antonio, Ortega Montes, Angeles, Ortigado Matamala, Alfonso, Ortiz Garrido, Almudena, Oulego Erroz, Ignacio, Palacios Argueta, Jorge Roberto, Parra Aguera, Laura, Peiro Molina, Esteban, Peralta Salas, Julio Ernesto, Perera Carrillo, Cesar Jorge, Perez Campos, Dolores, Perez Herrera, Veronica, Moneo Agapito, Maria Angeles Perez, Perez Munuzuri, Alejandro, Perez Pardo, Ana Maria, Perez Roldan, Jose Maria, Perez-Lescure Picarzo, Francisco Javier, Perez-Piaya Moreno, Maria Rosa, Perin, Francesca, Pinto Fuentes, Isabel, Plata Izquierdo, Beatriz, Portoles Morales, Maria, Puigdevall Dalmau, Maria Angeles, Pulido Ovalle, Erika, Raga Poveda, Maria Teresa, Rellan Rodriguez, Sara, Rey Garcia, Susana Maria, Rezola Arcelus, Erika, Riano Mendez, Bibiana, Rico Armada, Andres, Rivero Jimenez, Natalia, Rodriguez Gonzalez, Moises, Rodriguez Mesa, Maria Dolores, Rodriguez Serrano, Raul, Roman Barba, Violeta, Romero Ibarra, Carlos, Romero Vivas, Felix, Rueda Nunez, Fernando, Rueda Soriano, Joaquin, Sabate Rotes, Anna, Salas Salguero, Francisco Javier, Saldana Capunay, Julio Federico, Salido Peracaula, Carlos, Sanchez Calderon, Alberto, Sanchez Vaquerizo, Cristina, Sanz Pascual, Elena, Serrano Robles, Maria Isabel, Siles Sanchez-Manjavacas, Ana, Sobrino Baladron, Adolfo, Solana Garcia, Ruth, Soriano Belmonte, Dolors, Sorli Garcia, Moises, Suarez Cabrera, Pedro, Tamariz-Martes, Amalia, Tamariz-Martel Moreno, Rocio, Tejero Hernandez, Maria Angeles, Torres Rico, Maria, Uriel Prat, Susana, Usano Carrasco, Ana Isabel, Valdeolmillos Padrino, Estibaliz, Valero Adan, Maria Teresa, Villagra Albert, Sandra, Villalba Nogales, Javier, Walter, Carin Cristina, Yague Martin, Marta, Zambrano Casajona, Maria Dolores, SECPCC
Tipo de recurso: artículo
Fecha de publicación:2018
País:España
Institución:Conselleria de Salut i Consum del Govern de les Illes Balears
Repositorio:Docusalut
Idioma:español
OAI Identifier:oai:docusalut.com:20.500.13003/17448
Acceso en línea:https://hdl.handle.net/20.500.13003/17448
Access Level:acceso abierto
Palabra clave:Child
Heart Diseases
Follow-Up Studies
Humans
Mucocutaneous Lymph Node Syndrome
Estudios de Seguimiento
Humanos
Síndrome Mucocutáneo Linfonodular
Niño
Cardiopatías
Kawasaki disease
Mucocutaneous lymphnode syndrome
Vasculitis
Arteritis
Coronary aneurysm
Coronary vessels
Aneurysm
Immunoglobulins
intravenous
Steroids
Consensus
Descripción
Sumario:Kawasaki disease is a self-limiting acute vasculitis that affects small and medium-sized vessels, and is the most common cause of acquired heart disease in children in our environment. Up to 25% of untreated patients develop coronary aneurysms. It is suspected that an infectious agent may be the trigger of the disease, but the causative agent is still unknown. Based on the previous evidence, recommendations are proposed for the diagnosis, treatment of acute disease, and the long-term management of these patients, in order to unify criteria. The diagnosis must be quick, based on easy-to-use algorithms and with the support of complementary tests. This document includes the indication of available imaging techniques, as well as the planning of cardiological examinations based on the initial involvement. Intravenous immunoglobulin is the basis of the initial treatment. The role of corticosteroids is still controversial, but there are studies that support its use as adjuvant treatment. A multidisciplinary working group has developed a scheme with different treatment guidelines depending on the risk factors at diagnosis, the patient's clinical situation, and response to previous treatment, including indications for thromboprophylaxis in patients with coronary involvement. The stratification of risk for long-term treatment is essential, as well as the recommendations on the procedures based on the initial cardiological involvement and its progression. Patients with coronary aneurysms require continuous and uninterrupted cardiological monitoring for life.