Spontaneous Pneumothorax in Wegener's Granulomatosis: Case Report and Literature Review
Background: Pulmonary manifestations of Wegener's granulomatosis (WG) are present in 45% of cases at the onset of the disease, and they reach 85% of the patients during its evolution. Pulmonary affection usually starts with unspecific symptoms such as cough, dyspnea, hemoptysis, and pleuritis....
| Autores: | , , , , , , , |
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| Tipo de recurso: | artículo |
| Estado: | Versión borrador |
| Fecha de publicación: | 2011 |
| País: | España |
| Institución: | Universidad de Salamanca (USAL) |
| Repositorio: | GREDOS. Repositorio Institucional de la Universidad de Salamanca |
| OAI Identifier: | oai:gredos.usal.es:10366/163241 |
| Acceso en línea: | http://hdl.handle.net/10366/163241 |
| Access Level: | acceso abierto |
| Palabra clave: | spontaneous pneumothorax Wegener granulomatosis pyopneumotorax hydropneumothorax vasculitis 3205.08 Enfermedades Pulmonares |
| Sumario: | Background: Pulmonary manifestations of Wegener's granulomatosis (WG) are present in 45% of cases at the onset of the disease, and they reach 85% of the patients during its evolution. Pulmonary affection usually starts with unspecific symptoms such as cough, dyspnea, hemoptysis, and pleuritis. Pulmonary nodules are 1 of the most common manifestations. The prevalence of pleural affection is 10 to 20%. However, spontaneous pneumothorax is extremely rare. Although its real incidence is unknown, according to different classic series, it ranges between 3 and 5% of the cases. Objective: To present a new case of spontaneous pneumothorax in a patient suffering WG and a brief review on this subject. Methods: We report our experience in a case of spontaneous pneumothorax due to WG. We also review the literature through a PubMed search between 1960 and 2010, using a broad range of keywords related to WG and spontaneous pneumothorax. Publications were evaluated for the demographic features of patients, manifestations of the disease, and outcome. Results: Despite the large prevalence of the respiratory involvement, spontaneous pneumothorax is extremely rare, with only 21 cases reported in the literature. Conclusion: Pneumothorax is a rare complication in WG cases, without a clear pathogenic mechanism involved. |
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