Retinal detachment with spontaneous dialysis of the ora serrata in a 13-year-old child with neurofibromatosis type 1: A case report

A 13-year-old child diagnosed with neurofibromatosis type 1 who on a routine control presented with rhegmatogenous retinal detachment associated to dialysis of the ora serrata in the left eye (OS). There were no clinical signs or history of contuse ocular trauma. Neurofibromatosis produces alteratio...

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Autores: Clemente-Tomas, R, Ruiz-Del Rio, N, Gargallo-Benedicto, A, Garcia-Ibor, F, Hervas-Hernandis, JM, Duch-Samper, AM
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2020
País:España
Institución:INCLIVA
Repositorio:r-INCLIVA. Repositorio Institucional de Producción Científica de INCLIVA
OAI Identifier:oai:incliva.fundanetsuite.com:p15361
Acceso en línea:https://incliva.portalinvestigacion.com/publicaciones/15361
Access Level:acceso abierto
Palabra clave:Dialysis of the ora serrata
fibroblasts
neurofibromatosis type 1
rhegmatogenous retinal detachment
vitreous base
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spelling Retinal detachment with spontaneous dialysis of the ora serrata in a 13-year-old child with neurofibromatosis type 1: A case reportClemente-Tomas, RRuiz-Del Rio, NGargallo-Benedicto, AGarcia-Ibor, FHervas-Hernandis, JMDuch-Samper, AMDialysis of the ora serratafibroblastsneurofibromatosis type 1rhegmatogenous retinal detachmentvitreous baseA 13-year-old child diagnosed with neurofibromatosis type 1 who on a routine control presented with rhegmatogenous retinal detachment associated to dialysis of the ora serrata in the left eye (OS). There were no clinical signs or history of contuse ocular trauma. Neurofibromatosis produces alterations in fibroblasts of the cortex of the vitreous base. This results in deficient production of the collagen fibers that anchor the vitreous base to the pars plana and the peripheral neurosensory retina. Thus, suboptimal function of the fibroblasts explains spontaneous avulsion of the vitreous base. Such avulsion in turn is related to dialysis of the ora serrata.WOLTERS KLUWER MEDKNOW PUBLICATIONS2020info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionhttps://incliva.portalinvestigacion.com/publicaciones/15361INDIAN JOURNAL OF OPHTHALMOLOGYISSN: 03014738ISSNe: 19983689reponame:r-INCLIVA. Repositorio Institucional de Producción Científica de INCLIVAinstname:INCLIVAInglésinfo:eu-repo/semantics/openAccessoai:incliva.fundanetsuite.com:p153612026-06-07T16:35:31Z
dc.title.none.fl_str_mv Retinal detachment with spontaneous dialysis of the ora serrata in a 13-year-old child with neurofibromatosis type 1: A case report
title Retinal detachment with spontaneous dialysis of the ora serrata in a 13-year-old child with neurofibromatosis type 1: A case report
spellingShingle Retinal detachment with spontaneous dialysis of the ora serrata in a 13-year-old child with neurofibromatosis type 1: A case report
Clemente-Tomas, R
Dialysis of the ora serrata
fibroblasts
neurofibromatosis type 1
rhegmatogenous retinal detachment
vitreous base
title_short Retinal detachment with spontaneous dialysis of the ora serrata in a 13-year-old child with neurofibromatosis type 1: A case report
title_full Retinal detachment with spontaneous dialysis of the ora serrata in a 13-year-old child with neurofibromatosis type 1: A case report
title_fullStr Retinal detachment with spontaneous dialysis of the ora serrata in a 13-year-old child with neurofibromatosis type 1: A case report
title_full_unstemmed Retinal detachment with spontaneous dialysis of the ora serrata in a 13-year-old child with neurofibromatosis type 1: A case report
title_sort Retinal detachment with spontaneous dialysis of the ora serrata in a 13-year-old child with neurofibromatosis type 1: A case report
dc.creator.none.fl_str_mv Clemente-Tomas, R
Ruiz-Del Rio, N
Gargallo-Benedicto, A
Garcia-Ibor, F
Hervas-Hernandis, JM
Duch-Samper, AM
author Clemente-Tomas, R
author_facet Clemente-Tomas, R
Ruiz-Del Rio, N
Gargallo-Benedicto, A
Garcia-Ibor, F
Hervas-Hernandis, JM
Duch-Samper, AM
author_role author
author2 Ruiz-Del Rio, N
Gargallo-Benedicto, A
Garcia-Ibor, F
Hervas-Hernandis, JM
Duch-Samper, AM
author2_role author
author
author
author
author
dc.subject.none.fl_str_mv Dialysis of the ora serrata
fibroblasts
neurofibromatosis type 1
rhegmatogenous retinal detachment
vitreous base
topic Dialysis of the ora serrata
fibroblasts
neurofibromatosis type 1
rhegmatogenous retinal detachment
vitreous base
description A 13-year-old child diagnosed with neurofibromatosis type 1 who on a routine control presented with rhegmatogenous retinal detachment associated to dialysis of the ora serrata in the left eye (OS). There were no clinical signs or history of contuse ocular trauma. Neurofibromatosis produces alterations in fibroblasts of the cortex of the vitreous base. This results in deficient production of the collagen fibers that anchor the vitreous base to the pars plana and the peripheral neurosensory retina. Thus, suboptimal function of the fibroblasts explains spontaneous avulsion of the vitreous base. Such avulsion in turn is related to dialysis of the ora serrata.
publishDate 2020
dc.date.none.fl_str_mv 2020
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://incliva.portalinvestigacion.com/publicaciones/15361
url https://incliva.portalinvestigacion.com/publicaciones/15361
dc.language.none.fl_str_mv Inglés
language_invalid_str_mv Inglés
dc.rights.none.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.publisher.none.fl_str_mv WOLTERS KLUWER MEDKNOW PUBLICATIONS
publisher.none.fl_str_mv WOLTERS KLUWER MEDKNOW PUBLICATIONS
dc.source.none.fl_str_mv INDIAN JOURNAL OF OPHTHALMOLOGY
ISSN: 03014738
ISSNe: 19983689
reponame:r-INCLIVA. Repositorio Institucional de Producción Científica de INCLIVA
instname:INCLIVA
instname_str INCLIVA
reponame_str r-INCLIVA. Repositorio Institucional de Producción Científica de INCLIVA
collection r-INCLIVA. Repositorio Institucional de Producción Científica de INCLIVA
repository.name.fl_str_mv
repository.mail.fl_str_mv
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