Autoimmune kidney disease and impaired engulfment of apoptotic cells in mice with macrophage peroxisome proliferator-activated receptor gamma or retinoid X receptor alpha deficiency.

Autoimmune glomerulonephritis is a common manifestation of systemic lupus erythematosus (SLE). In this study, we show that mice lacking macrophage expression of the heterodimeric nuclear receptors PPARγ or RXRα develop glomerulonephritis and autoantibodies to nuclear Ags, resembling the nephritis se...

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Detalhes bibliográficos
Autores: Roszer, Tamás, Menéndez-Gutiérrez, María P, Lefterova, Martina I, Alameda, Daniel, Núñez, Vanessa, Lazar, Mitchell A, Fischer, Thierry, Ricote, Mercedes
Formato: artículo
Fecha de publicación:2011
País:España
Recursos:Instituto de Salud Carlos III (ISCIII)
Repositorio:Repisalud
Idioma:inglés
OAI Identifier:oai:repisalud.isciii.es:20.500.12105/15156
Acesso em linha:http://hdl.handle.net/20.500.12105/15156
Access Level:acceso abierto
Palavra-chave:Animals
Antibodies, Antinuclear
Apoptosis
Female
Lupus Nephritis
Macrophages
Mice
Mice, Inbred C57BL
Mice, Knockout
Mice, Transgenic
PPAR gamma
Phagocytosis
Retinoid X Receptor alpha
Self Tolerance
Descrição
Resumo:Autoimmune glomerulonephritis is a common manifestation of systemic lupus erythematosus (SLE). In this study, we show that mice lacking macrophage expression of the heterodimeric nuclear receptors PPARγ or RXRα develop glomerulonephritis and autoantibodies to nuclear Ags, resembling the nephritis seen in SLE. These mice show deficiencies in phagocytosis and clearance of apoptotic cells, and they are unable to acquire an anti-inflammatory phenotype upon feeding of apoptotic cells, which is critical for the maintenance of self-tolerance. These results demonstrate that stimulation of PPARγ and RXRα in macrophages facilitates apoptotic cell engulfment, and they provide a potential strategy to avoid autoimmunity against dying cells and to attenuate SLE.