HHV8 and EBV-negative primary effusion-based lymphoma

HHV8- and EBV-negative primary effusion lymphoma is an extremely rare neoplasm involving body cavities without detectable tumor mass. It usually presents in elderly patients without known immunodeficiency. Compared to primary effusion lymphoma, it has a better prognosis. Primary effusion lymphoma (P...

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Detalles Bibliográficos
Autores: Canelo-Vilaseca, Marta|||0000-0003-4479-4925, Tapia, Gustavo|||0000-0003-1882-0368, Orna, Elisa|||0000-0002-6862-9636, Sorigue, Marc|||0000-0002-0587-591X, Granada, Isabel|||0000-0002-4275-0104, Palomar-Muñoz, Azahara|||0000-0002-4372-5242, Castillo, Ana, Grau Cat, Javier, Mesa Tudel, Alba|||0000-0002-8377-7573, Ribera, Jose-Maria|||0000-0003-1042-6024, Sancho, Juan-Manuel|||0000-0001-7168-6538, Navarro Ferrando, José Tomás|||0000-0001-9101-6013
Tipo de recurso: artículo
Fecha de publicación:2023
País:España
Institución:Universitat Autònoma de Barcelona
Repositorio:Dipòsit Digital de Documents de la UAB
Idioma:inglés
OAI Identifier:oai:ddd.uab.cat:279358
Acceso en línea:https://ddd.uab.cat/record/279358
https://dx.doi.org/urn:doi:10.1002/ccr3.7282
Access Level:acceso abierto
Palabra clave:HHV8 and EBV-negative primary effusion-based lymphoma
PEL
PEL-like
Descripción
Sumario:HHV8- and EBV-negative primary effusion lymphoma is an extremely rare neoplasm involving body cavities without detectable tumor mass. It usually presents in elderly patients without known immunodeficiency. Compared to primary effusion lymphoma, it has a better prognosis. Primary effusion lymphoma (PEL) is a rare non-Hodgkin lymphoma confined exclusively to body cavities without detectable tumor masses. The term PEL-like is an entity similar to PEL in clinical presentation but without relation to human herpesvirus 8 (HHV8). We report a case of HHV8- and EBV-negative primary effusion-based lymphoma.