Fine-Tuning of Sirtuin 1 Expression Is Essential to Protect the Liver From Cholestatic Liver Disease

Cholestasis comprises aetiologically heterogeneous conditions characterized by accumulation of bile acids in the liver that actively contribute to liver damage. Sirtuin 1 (SIRT1) regulates liver regeneration and bile acid metabolism by modulating farnesoid X receptor (FXR); we here investigate its r...

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Autores: Blokker, Britt A., Maijo, Monica, Echeandia, Marta, Galduroz, Mikel, Patterson, Angela M., Ten, Anna, Philo, Mark, Schungel, Rebecca, Gutiérrez de Juan, Virginia, Halilbasic, Emina, Fuchs, Claudia, Le Gall, Gwenaelle, Milkiewicz, Malgorzata, Milkiewicz, Piotr, Bañales Asurmendi, Jesús María, Rushbrook, Simon M., Mato, José M., Trauner, Michael, Müller, Michael, Martínez Chantar, María Luz, Varela Rey, Marta, Beraza, Naiara
Tipo de recurso: artículo
Fecha de publicación:2019
País:España
Institución:Universidad del País Vasco
Repositorio:Addi. Archivo Digital para la Docencia y la Investigación
OAI Identifier:oai:addi.ehu.eus:10810/32113
Acceso en línea:http://hdl.handle.net/10810/32113
Access Level:acceso abierto
Palabra clave:farnesoid x receptor
bile-acid metabolism
norursodeoxycholic acid
sclerosing cholangitis
ursodeoxycholic acid
obeticholic acid
growth-factor
fxr
proliferation
pathogenesis
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oai_identifier_str oai:addi.ehu.eus:10810/32113
network_acronym_str ES
network_name_str España
repository_id_str
dc.title.none.fl_str_mv Fine-Tuning of Sirtuin 1 Expression Is Essential to Protect the Liver From Cholestatic Liver Disease
title Fine-Tuning of Sirtuin 1 Expression Is Essential to Protect the Liver From Cholestatic Liver Disease
spellingShingle Fine-Tuning of Sirtuin 1 Expression Is Essential to Protect the Liver From Cholestatic Liver Disease
Blokker, Britt A.
farnesoid x receptor
bile-acid metabolism
norursodeoxycholic acid
sclerosing cholangitis
ursodeoxycholic acid
obeticholic acid
growth-factor
fxr
proliferation
pathogenesis
title_short Fine-Tuning of Sirtuin 1 Expression Is Essential to Protect the Liver From Cholestatic Liver Disease
title_full Fine-Tuning of Sirtuin 1 Expression Is Essential to Protect the Liver From Cholestatic Liver Disease
title_fullStr Fine-Tuning of Sirtuin 1 Expression Is Essential to Protect the Liver From Cholestatic Liver Disease
title_full_unstemmed Fine-Tuning of Sirtuin 1 Expression Is Essential to Protect the Liver From Cholestatic Liver Disease
title_sort Fine-Tuning of Sirtuin 1 Expression Is Essential to Protect the Liver From Cholestatic Liver Disease
dc.creator.none.fl_str_mv Blokker, Britt A.
Maijo, Monica
Echeandia, Marta
Galduroz, Mikel
Patterson, Angela M.
Ten, Anna
Philo, Mark
Schungel, Rebecca
Gutiérrez de Juan, Virginia
Halilbasic, Emina
Fuchs, Claudia
Le Gall, Gwenaelle
Milkiewicz, Malgorzata
Milkiewicz, Piotr
Bañales Asurmendi, Jesús María
Rushbrook, Simon M.
Mato, José M.
Trauner, Michael
Müller, Michael
Martínez Chantar, María Luz
Varela Rey, Marta
Beraza, Naiara
author Blokker, Britt A.
author_facet Blokker, Britt A.
Maijo, Monica
Echeandia, Marta
Galduroz, Mikel
Patterson, Angela M.
Ten, Anna
Philo, Mark
Schungel, Rebecca
Gutiérrez de Juan, Virginia
Halilbasic, Emina
Fuchs, Claudia
Le Gall, Gwenaelle
Milkiewicz, Malgorzata
Milkiewicz, Piotr
Bañales Asurmendi, Jesús María
Rushbrook, Simon M.
Mato, José M.
Trauner, Michael
Müller, Michael
Martínez Chantar, María Luz
Varela Rey, Marta
Beraza, Naiara
author_role author
author2 Maijo, Monica
Echeandia, Marta
Galduroz, Mikel
Patterson, Angela M.
Ten, Anna
Philo, Mark
Schungel, Rebecca
Gutiérrez de Juan, Virginia
Halilbasic, Emina
Fuchs, Claudia
Le Gall, Gwenaelle
Milkiewicz, Malgorzata
Milkiewicz, Piotr
Bañales Asurmendi, Jesús María
Rushbrook, Simon M.
Mato, José M.
Trauner, Michael
Müller, Michael
Martínez Chantar, María Luz
Varela Rey, Marta
Beraza, Naiara
author2_role author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
dc.subject.none.fl_str_mv farnesoid x receptor
bile-acid metabolism
norursodeoxycholic acid
sclerosing cholangitis
ursodeoxycholic acid
obeticholic acid
growth-factor
fxr
proliferation
pathogenesis
topic farnesoid x receptor
bile-acid metabolism
norursodeoxycholic acid
sclerosing cholangitis
ursodeoxycholic acid
obeticholic acid
growth-factor
fxr
proliferation
pathogenesis
description Cholestasis comprises aetiologically heterogeneous conditions characterized by accumulation of bile acids in the liver that actively contribute to liver damage. Sirtuin 1 (SIRT1) regulates liver regeneration and bile acid metabolism by modulating farnesoid X receptor (FXR); we here investigate its role in cholestatic liver disease. We determined SIRT1 expression in livers from patients with cholestatic disease, in two experimental models of cholestasis, as well as in human and murine liver cells in response to bile acid loading. SIRT1-overexpressing (SIRToe) and hepatocyte-specific SIRT1-KO (knockout) mice (SIRThep-/-) were subjected to bile duct ligation (BDL) and were fed with a 0.1% DDC (3,5-diethoxycarbonyl-1,4-dihydrocollidine) diet to determine the biological relevance of SIRT1 during cholestasis. The effect of NorUDCA (24-norursodeoxycholic acid) was tested in BDL/SIRToe mice. We found that SIRT1 was highly expressed in livers from cholestatic patients, mice after BDL, and Mdr2 knockout mice (Mdr2(-/-)) animals. The detrimental effects of SIRT1 during cholestasis were validated in vivo and in vitro. SIRToe mice showed exacerbated parenchymal injury whereas SIRThep-/- mice evidenced a moderate improvement after BDL and 0.1% DDC feeding. Likewise, hepatocytes isolated from SIRToe mice showed increased apoptosis in response to bile acids, whereas a significant reduction was observed in SIRThep-/- hepatocytes. Importantly, the decrease, but not complete inhibition, of SIRT1 exerted by norUDCA treatment correlated with pronounced improvement in liver parenchyma in BDL/SIRToe mice. Interestingly, both SIRT1 overexpression and hepatocyte-specific SIRT1 depletion correlated with inhibition of FXR, whereas modulation of SIRT1 by NorUDCA associated with restored FXR signaling. Conclusion: SIRT1 expression is increased during human and murine cholestasis. Fine-tuning expression of SIRT1 is essential to protect the liver from cholestatic liver damage.
publishDate 2019
dc.date.none.fl_str_mv 2019
2019
2019
dc.type.none.fl_str_mv info:eu-repo/semantics/article
format article
dc.identifier.none.fl_str_mv http://hdl.handle.net/10810/32113
url http://hdl.handle.net/10810/32113
dc.language.none.fl_str_mv Inglés
language_invalid_str_mv Inglés
dc.relation.none.fl_str_mv info:eu-repo/grantAgreement/MINECO/SAF2014-54658-R/
info:eu-repo/grantAgreement/MINECO/ BIO15/CA
https://aasldpubs.onlinelibrary.wiley.com/doi/full/10.1002/hep.30275
dc.rights.none.fl_str_mv info:eu-repo/semantics/openAccess
http://creativecommons.org/licenses/by/3.0/es/
Atribución 3.0 España
eu_rights_str_mv openAccess
rights_invalid_str_mv http://creativecommons.org/licenses/by/3.0/es/
Atribución 3.0 España
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Wiley
publisher.none.fl_str_mv Wiley
dc.source.none.fl_str_mv reponame:Addi. Archivo Digital para la Docencia y la Investigación
instname:Universidad del País Vasco
instname_str Universidad del País Vasco
reponame_str Addi. Archivo Digital para la Docencia y la Investigación
collection Addi. Archivo Digital para la Docencia y la Investigación
repository.name.fl_str_mv
repository.mail.fl_str_mv
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spelling Fine-Tuning of Sirtuin 1 Expression Is Essential to Protect the Liver From Cholestatic Liver DiseaseBlokker, Britt A.Maijo, MonicaEcheandia, MartaGalduroz, MikelPatterson, Angela M.Ten, AnnaPhilo, MarkSchungel, RebeccaGutiérrez de Juan, VirginiaHalilbasic, EminaFuchs, ClaudiaLe Gall, GwenaelleMilkiewicz, MalgorzataMilkiewicz, PiotrBañales Asurmendi, Jesús MaríaRushbrook, Simon M.Mato, José M.Trauner, MichaelMüller, MichaelMartínez Chantar, María LuzVarela Rey, MartaBeraza, Naiarafarnesoid x receptorbile-acid metabolismnorursodeoxycholic acidsclerosing cholangitisursodeoxycholic acidobeticholic acidgrowth-factorfxrproliferationpathogenesisCholestasis comprises aetiologically heterogeneous conditions characterized by accumulation of bile acids in the liver that actively contribute to liver damage. Sirtuin 1 (SIRT1) regulates liver regeneration and bile acid metabolism by modulating farnesoid X receptor (FXR); we here investigate its role in cholestatic liver disease. We determined SIRT1 expression in livers from patients with cholestatic disease, in two experimental models of cholestasis, as well as in human and murine liver cells in response to bile acid loading. SIRT1-overexpressing (SIRToe) and hepatocyte-specific SIRT1-KO (knockout) mice (SIRThep-/-) were subjected to bile duct ligation (BDL) and were fed with a 0.1% DDC (3,5-diethoxycarbonyl-1,4-dihydrocollidine) diet to determine the biological relevance of SIRT1 during cholestasis. The effect of NorUDCA (24-norursodeoxycholic acid) was tested in BDL/SIRToe mice. We found that SIRT1 was highly expressed in livers from cholestatic patients, mice after BDL, and Mdr2 knockout mice (Mdr2(-/-)) animals. The detrimental effects of SIRT1 during cholestasis were validated in vivo and in vitro. SIRToe mice showed exacerbated parenchymal injury whereas SIRThep-/- mice evidenced a moderate improvement after BDL and 0.1% DDC feeding. Likewise, hepatocytes isolated from SIRToe mice showed increased apoptosis in response to bile acids, whereas a significant reduction was observed in SIRThep-/- hepatocytes. Importantly, the decrease, but not complete inhibition, of SIRT1 exerted by norUDCA treatment correlated with pronounced improvement in liver parenchyma in BDL/SIRToe mice. Interestingly, both SIRT1 overexpression and hepatocyte-specific SIRT1 depletion correlated with inhibition of FXR, whereas modulation of SIRT1 by NorUDCA associated with restored FXR signaling. Conclusion: SIRT1 expression is increased during human and murine cholestasis. Fine-tuning expression of SIRT1 is essential to protect the liver from cholestatic liver damage.Supported by the Biotechnology and Biological Sciences Research Council (BBSRC) by the BBSRC Institute Strategic Programme Gut Health and Food Safety and Gut Microbes and Health BBS/E/F/00044509 (to N.B.), the NRP Science Links Seed Corn Fund grant (to N.B., S.R.), Biotechnology and Biological Sciences Research Council (BBSRC) Doctoral Training Partnership programme (to N.B., A.T.), and Instituto de Salud Carlos III; FIS, PS12/00402 (to N.B. and M.V.R.). N.B. was funded by the BBSRC Institute Strategic Programme Gut Health and Food Safety BB/J004529/1, the Program Ramon y Cajal (Ministry of Economy and Competitiveness, Spain) and Ikerbaske foundation (Basque government, Spain). FIS PI12/00380, FIS PI15/01132, and Miguel Servet Program CON14/00129 cofinanced by "Fondo Europeo de Desarrollo Regional" (FEDER; to J.M.B.). Gobierno Vasco-Departamento de Salud 2013111114 (to M.L.M.-C.), MINECO: SAF2014-54658-R, EITB Maratoia BIO15/CA/014 (to M.L.M.C.) Asociacion Espanola contra el Cancer. Ciberehd is funded by the Instituto de Salud Carlos III. Work produced with the support of a 2017 Leonardo Grant for Researchers and Cultural Creators, BBVA Foundation (to M.V.R.). M.E. and M.G. were supported by the Camara de Comercio de Navarra.Wiley201920192019info:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10810/32113reponame:Addi. Archivo Digital para la Docencia y la Investigacióninstname:Universidad del País VascoInglésinfo:eu-repo/grantAgreement/MINECO/SAF2014-54658-R/info:eu-repo/grantAgreement/MINECO/ BIO15/CAhttps://aasldpubs.onlinelibrary.wiley.com/doi/full/10.1002/hep.30275info:eu-repo/semantics/openAccesshttp://creativecommons.org/licenses/by/3.0/es/This is an open access article under the terms of the Creative Commons Attribution License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited.Atribución 3.0 Españaoai:addi.ehu.eus:10810/321132026-06-18T09:23:17Z
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