Lactose and galactose content in spanish cheeses: usefulness in the dietary treatment of tatients with galactosaemia
In galactosaemia, a strict galactose-free diet is necessary to prevent or resolve acute symptoms in infants. However, because the body produces up to 10 times more galactose than is found in a galactose-restricted diet, excessively restrictive diets should be avoided in children and adults to preven...
| Autores: | , , , , , , |
|---|---|
| Tipo de recurso: | artículo |
| Fecha de publicación: | 2023 |
| País: | España |
| Institución: | Universidad de Cantabria (UC) |
| Repositorio: | UCrea Repositorio Abierto de la Universidad de Cantabria |
| Idioma: | inglés |
| OAI Identifier: | oai:repositorio.unican.es:10902/29883 |
| Acceso en línea: | https://hdl.handle.net/10902/29883 |
| Access Level: | acceso abierto |
| Palabra clave: | Inborn errors of metabolism Galactosaemia Galactose restriction Cheese Lactose Galactose |
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Lactose and galactose content in spanish cheeses: usefulness in the dietary treatment of tatients with galactosaemiaVitoria, IsidroMelendreras, FuensantaVázquez-Palazón, AntonioRausell, DoloresCorrecher, PatriciaGonzález-Lamuño Leguina, DomingoGarcía-Peris, MónicaInborn errors of metabolismGalactosaemiaGalactose restrictionCheeseLactoseGalactoseIn galactosaemia, a strict galactose-free diet is necessary to prevent or resolve acute symptoms in infants. However, because the body produces up to 10 times more galactose than is found in a galactose-restricted diet, excessively restrictive diets should be avoided in children and adults to prevent nutritional deficiencies. Since cheese is a nutritional source of the calcium necessary for bone health, the latest international guidelines on the management of classical galactosaemia (2017) allow the consumption of cured cheeses with less than 25 mg of galactose/100 g and recommend that each country verifies the adequacy of the cheeses, since most mature cheeses do not always have a lower galactose content. In total, 32 cheese samples were purchased (19 Spanish and 13 international cheeses), and their lactose and galactose contents were analysed using ion chromatography with pulsed amperometric detection (IC-PAD). Five Spanish cheeses contained less than 25 mg of galactose/100 g: García Baquero semi-cured cheese; Hacendado, Gran Reserva and Mahón cured cheeses; and García Baquero Reserva 12-month cured cheese. In addition, eight international cheeses were confirmed as suitable: Comté, Gouda, Gruyere, Maasdam, Parmigiano, Edam, Emmental, and some samples of Cheddar. In addition to the well-known low-galactose Swiss and Dutch cheeses, according to the current results, five Spanish cheeses can be safely consumed. The greater availability of types of cheese favours better bone health in patients with galactosaemiaMDPIUniversidad de Cantabria20232023-01-01journal articlehttp://purl.org/coar/resource_type/c_6501NAhttp://purl.org/coar/version/c_be7fb7dd8ff6fe43info:eu-repo/semantics/articlehttps://hdl.handle.net/10902/29883Nutrients, 2023, 15, 594reponame:UCrea Repositorio Abierto de la Universidad de Cantabriainstname:Universidad de Cantabria (UC)Inglésengopen accesshttp://purl.org/coar/access_right/c_abf2Attribution 4.0 Internationalhttp://creativecommons.org/licenses/by/4.0/info:eu-repo/semantics/openAccessoai:repositorio.unican.es:10902/298832026-06-02T12:39:31Z |
| dc.title.none.fl_str_mv |
Lactose and galactose content in spanish cheeses: usefulness in the dietary treatment of tatients with galactosaemia |
| title |
Lactose and galactose content in spanish cheeses: usefulness in the dietary treatment of tatients with galactosaemia |
| spellingShingle |
Lactose and galactose content in spanish cheeses: usefulness in the dietary treatment of tatients with galactosaemia Vitoria, Isidro Inborn errors of metabolism Galactosaemia Galactose restriction Cheese Lactose Galactose |
| title_short |
Lactose and galactose content in spanish cheeses: usefulness in the dietary treatment of tatients with galactosaemia |
| title_full |
Lactose and galactose content in spanish cheeses: usefulness in the dietary treatment of tatients with galactosaemia |
| title_fullStr |
Lactose and galactose content in spanish cheeses: usefulness in the dietary treatment of tatients with galactosaemia |
| title_full_unstemmed |
Lactose and galactose content in spanish cheeses: usefulness in the dietary treatment of tatients with galactosaemia |
| title_sort |
Lactose and galactose content in spanish cheeses: usefulness in the dietary treatment of tatients with galactosaemia |
| dc.creator.none.fl_str_mv |
Vitoria, Isidro Melendreras, Fuensanta Vázquez-Palazón, Antonio Rausell, Dolores Correcher, Patricia González-Lamuño Leguina, Domingo García-Peris, Mónica |
| author |
Vitoria, Isidro |
| author_facet |
Vitoria, Isidro Melendreras, Fuensanta Vázquez-Palazón, Antonio Rausell, Dolores Correcher, Patricia González-Lamuño Leguina, Domingo García-Peris, Mónica |
| author_role |
author |
| author2 |
Melendreras, Fuensanta Vázquez-Palazón, Antonio Rausell, Dolores Correcher, Patricia González-Lamuño Leguina, Domingo García-Peris, Mónica |
| author2_role |
author author author author author author |
| dc.contributor.none.fl_str_mv |
Universidad de Cantabria |
| dc.subject.none.fl_str_mv |
Inborn errors of metabolism Galactosaemia Galactose restriction Cheese Lactose Galactose |
| topic |
Inborn errors of metabolism Galactosaemia Galactose restriction Cheese Lactose Galactose |
| description |
In galactosaemia, a strict galactose-free diet is necessary to prevent or resolve acute symptoms in infants. However, because the body produces up to 10 times more galactose than is found in a galactose-restricted diet, excessively restrictive diets should be avoided in children and adults to prevent nutritional deficiencies. Since cheese is a nutritional source of the calcium necessary for bone health, the latest international guidelines on the management of classical galactosaemia (2017) allow the consumption of cured cheeses with less than 25 mg of galactose/100 g and recommend that each country verifies the adequacy of the cheeses, since most mature cheeses do not always have a lower galactose content. In total, 32 cheese samples were purchased (19 Spanish and 13 international cheeses), and their lactose and galactose contents were analysed using ion chromatography with pulsed amperometric detection (IC-PAD). Five Spanish cheeses contained less than 25 mg of galactose/100 g: García Baquero semi-cured cheese; Hacendado, Gran Reserva and Mahón cured cheeses; and García Baquero Reserva 12-month cured cheese. In addition, eight international cheeses were confirmed as suitable: Comté, Gouda, Gruyere, Maasdam, Parmigiano, Edam, Emmental, and some samples of Cheddar. In addition to the well-known low-galactose Swiss and Dutch cheeses, according to the current results, five Spanish cheeses can be safely consumed. The greater availability of types of cheese favours better bone health in patients with galactosaemia |
| publishDate |
2023 |
| dc.date.none.fl_str_mv |
2023 2023-01-01 |
| dc.type.none.fl_str_mv |
journal article http://purl.org/coar/resource_type/c_6501 NA http://purl.org/coar/version/c_be7fb7dd8ff6fe43 |
| dc.type.openaire.fl_str_mv |
info:eu-repo/semantics/article |
| format |
article |
| dc.identifier.none.fl_str_mv |
https://hdl.handle.net/10902/29883 |
| url |
https://hdl.handle.net/10902/29883 |
| dc.language.none.fl_str_mv |
Inglés eng |
| language_invalid_str_mv |
Inglés |
| language |
eng |
| dc.rights.none.fl_str_mv |
open access http://purl.org/coar/access_right/c_abf2 Attribution 4.0 International http://creativecommons.org/licenses/by/4.0/ |
| dc.rights.openaire.fl_str_mv |
info:eu-repo/semantics/openAccess |
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open access http://purl.org/coar/access_right/c_abf2 Attribution 4.0 International http://creativecommons.org/licenses/by/4.0/ |
| eu_rights_str_mv |
openAccess |
| dc.publisher.none.fl_str_mv |
MDPI |
| publisher.none.fl_str_mv |
MDPI |
| dc.source.none.fl_str_mv |
Nutrients, 2023, 15, 594 reponame:UCrea Repositorio Abierto de la Universidad de Cantabria instname:Universidad de Cantabria (UC) |
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Universidad de Cantabria (UC) |
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UCrea Repositorio Abierto de la Universidad de Cantabria |
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UCrea Repositorio Abierto de la Universidad de Cantabria |
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1869406482288607232 |
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15.301603 |