Granulomatosis con poliangeítis y compromiso en fosa posterior. Reporte de un caso

Granulomatosis with Poliangeitis or Wegner's granulomatosis has an incidence of5-10 cases per million of habitants and only 2-11% of cases present manifestationsin the central nervous system. There are no standardized diagnostic criteria, however,clinical suspicion, positive serology for ANCA’S...

ver descrição completa

Detalhes bibliográficos
Autores: Benavides Burbano, Camilo Armando, Vitola Dominguez, Alexander, Diaz Forero, Andres, Riveros Castillo, William Mauricio
Formato: tesis de maestría
Estado:Versión aceptada para publicación
Fecha de publicación:2020
País:Colombia
Recursos:Universidad del Rosario
Repositorio:Repositorio EdocUR - U. Rosario
Idioma:español
OAI Identifier:oai:repository.urosario.edu.co:10336/34592
Acesso em linha:https://doi.org/10.48713/10336_34592
https://repository.urosario.edu.co/handle/10336/34592
Access Level:acceso abierto
Palavra-chave:Granulomatosis with Polyangiitis
Wegener Granulomatosis
Antibodies Antineutrophil Cytoplasmic
Neurologic Manifestations
Neurosurgery
Ciencias médicas, Medicina
Descrição
Resumo:Granulomatosis with Poliangeitis or Wegner's granulomatosis has an incidence of5-10 cases per million of habitants and only 2-11% of cases present manifestationsin the central nervous system. There are no standardized diagnostic criteria, however,clinical suspicion, positive serology for ANCA’S, histological evidence of necrotizingvasculitis, necrotizing glomerulonephritis or granulomatous inflammation of organssuch as skin, lung or kidney, may suggest this pathology. Neurosurgery is a diagnosticand therapeutic option and could be a possibility in those cases in which the lesionsare in accessible areas and have low risk of generating comorbidities. We presentthe case of a 39-year-old female patient with granulomatosis and polyangiitis withinvolvement in the posterior fossa. After surgical management, it presents meningealinfection. Additionally, we conducted a review of the pathology.