Alagille syndrome: from the cutaneous to the systemic

Here is reported the case of a girl with Alagille syndrome, in whom the keys to diagnosis were the dermatological manifestations characterized by chronic and persistent pruritus that led us to search for other systemic conditions, confirming the pathology.

Detalles Bibliográficos
Autores: Macías, M.A., Reina, A., Motta Beltrán, Adriana, Truffello, D., Sepúlveda, A.
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2019
País:Colombia
Institución:Universidad El Bosque
Repositorio:Repositorio U. El Bosque
Idioma:inglés
OAI Identifier:oai:repositorio.unbosque.edu.co:20.500.12495/2030
Acceso en línea:http://hdl.handle.net/20.500.12495/2030
https://doi.org/10.26326/2281-9649.29.1.1941
Access Level:acceso abierto
Palabra clave:Manifestaciones cutáneas
Enfermedades de los conductos biliares
Colestasis intrahepática
Pruritus
Cholestasis
Alagille syndrome
Descripción
Sumario:Here is reported the case of a girl with Alagille syndrome, in whom the keys to diagnosis were the dermatological manifestations characterized by chronic and persistent pruritus that led us to search for other systemic conditions, confirming the pathology.