Vulva Plexiform Fibrohistiocytic Tumor: Case Report

Introduction: Plexiform fibrohistiocytic tumor is a rare clinical condition, with about 150 cases described in the literature. Case report: 23-yearsold, female patient with nodular lesion in vulva without malignancy characteristics on ultrasound image. She underwent clinical follow-up and after an i...

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Detalles Bibliográficos
Autores: Baumgartner, Aluisio Juliano, Garcia, Fernanda Stefania Bastos, Ono, Lia Mizobe, Oliveira, Érica Condé Marques e, Fuzita, William Hiromi, Anjos, Caroline Souza dos
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2021
País:Brasil
Institución:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
Repositorio:Revista Brasileira de Cancerologia (Online)
Idioma:portugués
inglés
OAI Identifier:oai:rbc.inca.gov.br:article/1269
Acceso en línea:https://rbc.inca.gov.br/index.php/revista/article/view/1269
Access Level:acceso abierto
Palabra clave:Sarcoma Histiocítico
Neoplasias Vulvares
Relatos de Casos
Histiocytic Sarcoma
Vulvar Neoplasms
Case Reports
Neoplasias de la Vulva
Informes de Casos
Descripción
Sumario:Introduction: Plexiform fibrohistiocytic tumor is a rare clinical condition, with about 150 cases described in the literature. Case report: 23-yearsold, female patient with nodular lesion in vulva without malignancy characteristics on ultrasound image. She underwent clinical follow-up and after an increase in the size of the lesion, surgical resection was opted. Histopathological findings suggested plexiform fibrohistiocytic tumor, with free surgical margins. In follow up, she was referred to oncological evaluation for screening complementary exams and rule out morphologically similar diagnoses. After the complementary exams confirming the initial diagnosis of plexiform fibrohistiocytic tumor and without evidence of metastatic disease after complete surgical excision with free margins, the patient is in clinical follow-up. Conclusion: Reporting the case is extremely important to disseminate the clinical presentation, diagnostic steps, proposed treatment and share information about the clinical evolution presented.