Effects of gene therapy on cardiovascular symptoms of lysosomal storage diseases

Lysosomal storage diseases (LSDs) are inherited conditions caused by impaired lysosomal function and consequent substrate storage, leading to a range of clinical manifestations, including cardiovascular disease. This may lead to significant symptoms and even cardiac failure, which is an important ca...

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Detalles Bibliográficos
Autores: Poletto, Édina, Pasqualim, Gabriela, Giugliani, Roberto, Matte, Ursula da Silveira, Baldo, Guilherme
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2019
País:Brasil
Institución:Universidade Federal do Rio Grande do Sul (UFRGS)
Repositorio:Repositório Institucional da UFRGS
Idioma:inglés
OAI Identifier:oai:www.lume.ufrgs.br:10183/201049
Acceso en línea:http://hdl.handle.net/10183/201049
Access Level:acceso abierto
Palabra clave:Terapia genética
Doenças cardiovasculares
Doenças por armazenamento dos lisossomos
Doença de depósito de glicogênio
Lysosomal storage disease
Gene therapy
Cardiovascular disease
Animal models
Heart.
Descripción
Sumario:Lysosomal storage diseases (LSDs) are inherited conditions caused by impaired lysosomal function and consequent substrate storage, leading to a range of clinical manifestations, including cardiovascular disease. This may lead to significant symptoms and even cardiac failure, which is an important cause of death among patients. Currently available treatments do not completely correct cardiac involvement in the LSDs. Gene therapy has been tested as a therapeutic alternative with promising results for the heart disease. In this review, we present the results of different approaches of gene therapy for LSDs, mainly in animal models, and its effects in the heart, focusing on protocols with cardiac functional analysis.