Fulminant Hepatitis as the First Presentation of Wilson’s Disease
Wilson’s disease is rare, but it affects 6-12% of patients with an indication for urgent liver transplantation. The main manifestations, in addition to the liver, are neurological and psychiatric, with evolution with fulminant hepatitis without neuropsychiatric symptoms being rarer. Despite the urge...
| Autores: | , , , , , , , |
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| Tipo de recurso: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2023 |
| País: | Brasil |
| Institución: | Associação Brasileira de Transplante de Órgãos (ABTO) |
| Repositorio: | Brazilian Journal of Transplantation |
| Idioma: | inglés portugués |
| OAI Identifier: | oai:ojs3.emnuvens.com.br:article/497 |
| Acceso en línea: | https://bjt.emnuvens.com.br/revista/article/view/497 |
| Access Level: | acceso abierto |
| Palabra clave: | Insuficiência Hepática Fulminante Transplante de Fígado Pseudoaneurisma Fulminant Hepatic Insufficiency Liver Transplantation Pseudoaneurysm Enfermedad de Wilson Insuficiencia Hepática Fulminante Trasplante de Hígado Informes de Casos |
| Sumario: | Wilson’s disease is rare, but it affects 6-12% of patients with an indication for urgent liver transplantation. The main manifestations, in addition to the liver, are neurological and psychiatric, with evolution with fulminant hepatitis without neuropsychiatric symptoms being rarer. Despite the urgency, the prognosis for post-transplant patients averages 85% 5-year survival. In this report, we presentthe case of a female patient, 18 years old, with the onset of abdominal pain, jaundice and choluria that progressed to fulminanthepatitis and the need for urgent liver transplantation. The patient evolved postoperatively with septic shock due to herpetic encephalitis, duodenal ulcer with active bleeding and hepatic artery pseudoaneurysm. Despite measures for stabilization and the request for a transplant again, the patient died. |
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