Solid pseudopapillary neoplasm of the pancreas. (Frantz´s tumor) Anatomo-clinical aspects.

Pseudo papillary tumor of the pancreas, also called Frantz´s tumor, is a very rare disease; between 0.2 and 2.7% of pancreatic carcinomas. Ethiology is unknown; is observed in young women. It´s a tumors with low malignant potential, usually of asymptomatic evolution by long time and the symptoms are...

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Detalles Bibliográficos
Autores: Marrero, Gregory, Campos, Maite, Laca, Elisa, González, Daniel, Ruso Martínez, Luis
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2023
País:Uruguay
Institución:Sociedad de Cirugía del Uruguay
Repositorio:Revista Cirugía del Uruguay
Idioma:español
OAI Identifier:oai:ojs2.revista.scu.org.uy:article/5730
Acceso en línea:https://revista.scu.org.uy/index.php/cir_urug/article/view/5730
Access Level:acceso abierto
Palabra clave:Tumor de Frantz
tumores neuroendócrinos
páncreas
pancreatectomía
Frantz tumor
neuroendocrine tumors
pancreas
pancreatectomy
tumor de Frantz
Descripción
Sumario:Pseudo papillary tumor of the pancreas, also called Frantz´s tumor, is a very rare disease; between 0.2 and 2.7% of pancreatic carcinomas. Ethiology is unknown; is observed in young women. It´s a tumors with low malignant potential, usually of asymptomatic evolution by long time and the symptoms are due to regional compression: pain or abdominal mass. The possibility of a malignant form is around 15%. Anatomically, they are most frequently located in the tail of the pancreas, followed by the head and body. The treatment is the surgical resection; with an excellent prognosis and a 5-year survival almost 100%. The diagnosis is with pathological study, considering the microscopic appearance and the immunohistochemical profile. Its perform an analysis of the literature and once case of a 21 years old, woman is reported. A complete resection surgery of the tumor was performed and remains asymptomatic at 24 months of follow-up.