Glandular odontogenic cyst: insights into a rare and challenging lesion.

The glandular odontogenic cyst (GOC) is a rare developmental odontogenic cyst characterized by an epithelial lining resembling salivary or glandular tissue. Its aggressive behavior and potential for recurrence pose challenges in both diagnosis and management. This review consolidates current knowled...

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Detalles Bibliográficos
Autores: Schuch, Lauren Frenzel, Silveira, Felipe Martins, González Umpiérrez, María Natalia, Beovide Cortegoso, Verónica, Sicco, Estefanía, Bologna-Molina, Ronell, Pereira-Prado, Vanesa
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2025
País:Uruguay
Institución:Universidad de la República
Repositorio:COLIBRI
Idioma:inglés
OAI Identifier:oai:colibri.udelar.edu.uy:20.500.12008/51892
Acceso en línea:https://hdl.handle.net/20.500.12008/51892
Access Level:acceso abierto
Palabra clave:Odontogenic lesion
Glandular odontogenic cyst
Diagnostic challenge
QUISTES ODONTOGÉNICOS
ODONTOGENIC CYSTS
Descripción
Sumario:The glandular odontogenic cyst (GOC) is a rare developmental odontogenic cyst characterized by an epithelial lining resembling salivary or glandular tissue. Its aggressive behavior and potential for recurrence pose challenges in both diagnosis and management. This review consolidates current knowledge on etiopathogenesis, clinical presentation, histopathological features, and treatment approaches. GOC primarily affects male adults, often presenting asymptomatically, and is most commonly found in the mandible. Radiographically, it appears as a unilocular or multilocular radiolucency, frequently associated with unerupted teeth. Histologically, GOC is istinguished by a multilocular cystic structure lined with epithelial cells, which may include “hobnail,” clear, and mucous cells. While traditionally thought to lack MAML2 gene rearrangements, recent studies have identified MAML2 fusion transcripts in recurrent GOCs, suggesting a link to aggressive behavior. The differential diagnosis includes both benign and malignant conditions. Treatment options range from conservative management to radical resection, with recurrence being a notable concern. This review highlights the need for accurate diagnosis and long-term follow-up, as no histopathological features reliably predict recurrence. Further research is needed to optimize treatment strategies and deepen understanding of its biological behavior.