Sarcomatose transformation in von Recklinghausen's disease

The authors describe 2 clinical observations of neurofibrosarcomas in patients suffering from von Recklinghausen'sdisease ( or multiple .neurofibromato'sis) : 1 mediastinal fibrosarcoma and 1 neurofibrosarcoma of right femoral nerve.Therc is a bibliographic review of sarcomatose transforma...

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Bibliographic Details
Authors: de Pena, Mario, Carriquiry, Luis A, Davidenko, Nicolás, Peyroulou, Alfredo, Gómez Fossati, Carlos, Priario, Julio César
Format: article
Status:Published version
Publication Date:1979
Country:Uruguay
Institution:Sociedad de Cirugía del Uruguay
Repository:Revista Cirugía del Uruguay
Language:Spanish
OAI Identifier:oai:ojs2.revista.scu.org.uy:article/3029
Online Access:https://revista.scu.org.uy/index.php/cir_urug/article/view/3029
Access Level:Open access
Keyword:neurofibromatosis
Description
Summary:The authors describe 2 clinical observations of neurofibrosarcomas in patients suffering from von Recklinghausen'sdisease ( or multiple .neurofibromato'sis) : 1 mediastinal fibrosarcoma and 1 neurofibrosarcoma of right femoral nerve.Therc is a bibliographic review of sarcomatose transformation in von Recklinghausen's disease.