Challenges in diagnosis and treatment of late-onset Rasmussen encephalitis: Report of three cases.

Rasmussen’s encephalitis is an unusual clinical entity characterized by drug-resistant focal epilepsy, neurological deficit and progressive cerebral hemiatrophy. The diagnostic and therapeutic approach is complex, even more so in patients with Rasmussen’s encephalitis of late onset (in adolescence a...

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Detalles Bibliográficos
Autores: Rodríguez-Vega, Oswaldo, Barreto-Acevedo, Elliot, Becerra-Zegarra, Alicia, Cortez-Salazar, Luis
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2022
País:Perú
Institución:Universidad Peruana Cayetano Heredia
Repositorio:Revistas - Universidad Peruana Cayetano Heredia
Idioma:español
OAI Identifier:oai:revistas.upch.edu.pe:article/4370
Acceso en línea:https://revistas.upch.edu.pe/index.php/RNP/article/view/4370
Access Level:acceso abierto
Palabra clave:Rasmussen’s encephalitis
drug resistant epilepsy
histopathology
epilepsy surgery
Encefalitis de Rasmussen
epilepsia farmacorresistente
histopatología
cirugía de epilepsia
Descripción
Sumario:Rasmussen’s encephalitis is an unusual clinical entity characterized by drug-resistant focal epilepsy, neurological deficit and progressive cerebral hemiatrophy. The diagnostic and therapeutic approach is complex, even more so in patients with Rasmussen’s encephalitis of late onset (in adolescence and adulthood) whose clinical picture could be atypical when compared with its occurrence in children. We report a series of three clinical cases of late-onset Rasmussen’s encephalitis confirmed by histopathology and immunohistochemistry evaluations and in which clinical improvement was achieved after surgical interventions. Literature reviews on the clinical evolution and therapeutic alternatives for this type of presentation are included.