Portal hypertension as an uncommon presentation of hepatic epithelioid hemangioendothelioma: a case report

Hepatic epithelioid hemangioendothelioma (HEHE) is a vascular tumor with a low incidence rate. We report a case of a 26-year-old man who was referred to our hospital with a misdiagnosis of liver cirrhosis. On physical examination, ascites was noted. Chest and abdominal computer tomography scans show...

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Detalles Bibliográficos
Autores: Zambrano-Huailla, Rommel, Guzmán-Poma, Roxana, Cahua-Segura, Giancarlo, Flores-Ezcurra, Lourdes, Sumire Umeres, Julia, Cebreros Ibarra, Oscar, Martel Mory, Silvia
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2021
País:Perú
Institución:Sociedad de Gastroenterología del Perú
Repositorio:Revista de Gastroenterología del Perú
Idioma:español
OAI Identifier:oai:ojs.revistagastroperu.com:article/1276
Acceso en línea:https://revistagastroperu.com/index.php/rgp/article/view/1276
Access Level:acceso abierto
Palabra clave:Hemangioendothelioma
epithelioid
Hypertension
portal
Liver neoplasms
Liver transplantation
Case reports
Descripción
Sumario:Hepatic epithelioid hemangioendothelioma (HEHE) is a vascular tumor with a low incidence rate. We report a case of a 26-year-old man who was referred to our hospital with a misdiagnosis of liver cirrhosis. On physical examination, ascites was noted. Chest and abdominal computer tomography scans showed coalescent lesions involving the peripheral liver with heterogeneous contrast enhancement and portal vein dilation due to portal hypertension. Extrahepatic metastasis was not observed. The biopsy with immunohistochemical stains suggested HE d CD34). This report describes an uncommon case of HEHE with non-cirrhotic portal hypertension.