Right hemitruncus in adulthood: an unusual finding

Hemitruncus arteriosus is a rare congenital heart disease characterized by the abnormal origin of one of the branches of the pulmonary artery from the ascending aorta. In most cases, its diagnosis is made during childhood; in addition, due to its high morbidity and mortality, its asymptomatic evolut...

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Detalles Bibliográficos
Autores: Huerta Robles, Rocío, Chávez Solsol, Jorge Francisco, Rodríguez Urteaga, Zoila, Nario Lazo, Viviana, Palacios-León, José, Robles-Velarde, Victor
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2020
País:Perú
Institución:Instituto Nacional Cardiovascular
Repositorio:Archivos peruanos de cardiología y cirugía cardiovascular
Idioma:español
OAI Identifier:oai:apcyccv.org.pe:article/46
Acceso en línea:https://apcyccv.org.pe/index.php/apccc/article/view/46
Access Level:acceso abierto
Palabra clave:Cardiopatía congénita
adulto
neumonectomía
Congenital heart disease
adult
pneumonectomy
Descripción
Sumario:Hemitruncus arteriosus is a rare congenital heart disease characterized by the abnormal origin of one of the branches of the pulmonary artery from the ascending aorta. In most cases, its diagnosis is made during childhood; in addition, due to its high morbidity and mortality, its asymptomatic evolution and survival to adulthood is extremely unusual. We present the case of a 30-year-old male patient, with a history of surgical closure of patent ductus arteriosus during childhood, who was asymptomatic until a year ago, in whom hemitruncus arteriosus was diagnosed after recurrent episodes of hemoptysis.