Paraneoplastic neurologic syndromes associated with nasopharyngeal carcinoma: a systematic review

Introduction and objectives: Paraneoplastic syndromes (PS) are a heterogeneous group of cancer-associated disorders caused by mechanisms other than metastases, metabolic, nutritional deficits, infections, or side effects of cancer treatment PS appear in 1-7.4 % of all cancer patients. Paraneoplastic...

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Detalles Bibliográficos
Autores: Riancho Zarrabeitia, Javier, Rodríguez Rodríguez, Eloy Manuel, Martínez-Camerano, Andrea, Fernández-Enseñat, Julia, Morales Angulo, Carmelo|||0000-0002-4268-2762
Tipo de recurso: artículo
Fecha de publicación:2025
País:España
Institución:Universidad de Cantabria (UC)
Repositorio:UCrea Repositorio Abierto de la Universidad de Cantabria
Idioma:inglés
OAI Identifier:oai:repositorio.unican.es:10902/38709
Acceso en línea:https://hdl.handle.net/10902/38709
Access Level:acceso abierto
Palabra clave:Paraneoplastic
Myelitis
Nasopharyngeal carcinoma
Antineural antibodies
Head and neck carcinoma
Paraneoplásico
Carcinoma nasofaríngeo
Anticuerpos antineuronales
Carcinoma de cabeza y cuello
Mielitis
Descripción
Sumario:Introduction and objectives: Paraneoplastic syndromes (PS) are a heterogeneous group of cancer-associated disorders caused by mechanisms other than metastases, metabolic, nutritional deficits, infections, or side effects of cancer treatment PS appear in 1-7.4 % of all cancer patients. Paraneoplastic neurological syndromes (PNS) associated with nasopharyngeal carcinoma (NC) are very rare. The objective of this review is to characterize the PNS associated with NC. Methods: A systematic review of cases of PNS associated to NC was carried out. The following databases were used for the search: Pubmed, Web of Science and Cochrane library. As search terms we used the keywords: ?paraneoplastic syndrome? and ?nasopharyngeal carcinoma?. Results: We included a total of 11 patients in the review. The PNS most frequently identified were cerebellar degeneration, limbic encephalitis, and opsoclonus-myoclonus syndrome. Auto antibodies against neural structures were identified in 5 cases (anti-Yo, anti-Hu and anti-RI). Regarding neurological prognosis, neurological symptoms did not improve or improved only partially after both primary tumor and steroids and immunoglobulins. Conclusions: Clinicians should consider the possibility of a paraneo-plastic etiology when caring for patients with NC who present with subacute neurological symptoms. The prognosis of PNS after treatment is poor.