Therapeutic outcomes and survival analysis of Extramammary Paget's disease: A multicentre retrospective study of 249 patients

Background: Evidence regarding long-term therapeutic outcomes and disease-specific survival (DSS) in Extramammary Paget's disease (EMPD) is limited. Objectives: To assess the DSS and outcomes of surgical and nonsurgical therapeutic modalities in a large cohort of EMPD patients. Methods: Ret...

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Autores: Escolà, Helena, Leal, Lorena, Pujol Vallverdú, Ramón M., Deza Vargas, Luis Gustavo
Tipo de recurso: artículo
Estado:Versión aceptada para publicación
Fecha de publicación:2024
País:España
Institución:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
Repositorio:Recercat. Dipósit de la Recerca de Catalunya
OAI Identifier:oai:recercat.cat:10230/60242
Acceso en línea:http://hdl.handle.net/10230/60242
http://dx.doi.org/10.1016/j.jaad.2023.08.088
Access Level:acceso abierto
Palabra clave:Extramammary Paget&apos
s disease
Mohs micrographic surgery
Imiquimod
Local recurrence
Margin status
Radiotherapy
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spelling Therapeutic outcomes and survival analysis of Extramammary Paget's disease: A multicentre retrospective study of 249 patientsEscolà, HelenaLeal, LorenaPujol Vallverdú, Ramón M.Deza Vargas, Luis GustavoExtramammary Paget&aposs diseaseMohs micrographic surgeryImiquimodLocal recurrenceMargin statusRadiotherapyBackground: Evidence regarding long-term therapeutic outcomes and disease-specific survival (DSS) in Extramammary Paget's disease (EMPD) is limited. Objectives: To assess the DSS and outcomes of surgical and nonsurgical therapeutic modalities in a large cohort of EMPD patients. Methods: Retrospective chart review of EMPD patients from 20 Spanish tertiary care hospitals. Results: Data on 249 patients with a median follow-up of 60 months were analyzed. The estimated 5-, 10-, and 15-year DSS was 95.9%, 92.9%, and 88.5%, respectively. A significantly lower DSS was observed in patients showing deep dermal invasion (≥1 mm) or metastatic disease (P < .05). A ≥50% reduction in EMPD lesion size was achieved in 100% and 75.3% of patients treated with surgery and topical therapies, respectively. Tumor-free resection margins were obtained in 42.4% of the patients after wide local excision (WLE). The 5-year recurrence-free survival after Mohs micrographic surgery (MMS), WLE with tumor-free margins, WLE with positive margins, radiotherapy, and topical treatments was 63.0%, 51.4%, 20.4%, 30.1%, and 20.8%, respectively. Limitations: Retrospective design. Conclusions: EMPD is usually a chronic condition with favorable prognosis. MMS represents the therapeutic alternative with the greatest efficacy for the disease. Recurrence rates in patients with positive margins after WLE are similar to the ones observed in patients treated with topical agents.Elsevier20242024info:eu-repo/semantics/articleinfo:eu-repo/semantics/acceptedVersionapplication/pdfapplication/pdfhttp://hdl.handle.net/10230/60242http://dx.doi.org/10.1016/j.jaad.2023.08.088reponame:Recercat. Dipósit de la Recerca de Catalunyainstname:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)InglésJ Am Acad Dermatol. 2024 Jan;90(1):66-73© Elsevier http://dx.doi.org/10.1016/j.jaad.2023.08.088info:eu-repo/semantics/openAccessoai:recercat.cat:10230/602422026-05-29T05:05:01Z
dc.title.none.fl_str_mv Therapeutic outcomes and survival analysis of Extramammary Paget's disease: A multicentre retrospective study of 249 patients
title Therapeutic outcomes and survival analysis of Extramammary Paget's disease: A multicentre retrospective study of 249 patients
spellingShingle Therapeutic outcomes and survival analysis of Extramammary Paget's disease: A multicentre retrospective study of 249 patients
Escolà, Helena
Extramammary Paget&apos
s disease
Mohs micrographic surgery
Imiquimod
Local recurrence
Margin status
Radiotherapy
title_short Therapeutic outcomes and survival analysis of Extramammary Paget's disease: A multicentre retrospective study of 249 patients
title_full Therapeutic outcomes and survival analysis of Extramammary Paget's disease: A multicentre retrospective study of 249 patients
title_fullStr Therapeutic outcomes and survival analysis of Extramammary Paget's disease: A multicentre retrospective study of 249 patients
title_full_unstemmed Therapeutic outcomes and survival analysis of Extramammary Paget's disease: A multicentre retrospective study of 249 patients
title_sort Therapeutic outcomes and survival analysis of Extramammary Paget's disease: A multicentre retrospective study of 249 patients
dc.creator.none.fl_str_mv Escolà, Helena
Leal, Lorena
Pujol Vallverdú, Ramón M.
Deza Vargas, Luis Gustavo
author Escolà, Helena
author_facet Escolà, Helena
Leal, Lorena
Pujol Vallverdú, Ramón M.
Deza Vargas, Luis Gustavo
author_role author
author2 Leal, Lorena
Pujol Vallverdú, Ramón M.
Deza Vargas, Luis Gustavo
author2_role author
author
author
dc.subject.none.fl_str_mv Extramammary Paget&apos
s disease
Mohs micrographic surgery
Imiquimod
Local recurrence
Margin status
Radiotherapy
topic Extramammary Paget&apos
s disease
Mohs micrographic surgery
Imiquimod
Local recurrence
Margin status
Radiotherapy
description Background: Evidence regarding long-term therapeutic outcomes and disease-specific survival (DSS) in Extramammary Paget's disease (EMPD) is limited. Objectives: To assess the DSS and outcomes of surgical and nonsurgical therapeutic modalities in a large cohort of EMPD patients. Methods: Retrospective chart review of EMPD patients from 20 Spanish tertiary care hospitals. Results: Data on 249 patients with a median follow-up of 60 months were analyzed. The estimated 5-, 10-, and 15-year DSS was 95.9%, 92.9%, and 88.5%, respectively. A significantly lower DSS was observed in patients showing deep dermal invasion (≥1 mm) or metastatic disease (P < .05). A ≥50% reduction in EMPD lesion size was achieved in 100% and 75.3% of patients treated with surgery and topical therapies, respectively. Tumor-free resection margins were obtained in 42.4% of the patients after wide local excision (WLE). The 5-year recurrence-free survival after Mohs micrographic surgery (MMS), WLE with tumor-free margins, WLE with positive margins, radiotherapy, and topical treatments was 63.0%, 51.4%, 20.4%, 30.1%, and 20.8%, respectively. Limitations: Retrospective design. Conclusions: EMPD is usually a chronic condition with favorable prognosis. MMS represents the therapeutic alternative with the greatest efficacy for the disease. Recurrence rates in patients with positive margins after WLE are similar to the ones observed in patients treated with topical agents.
publishDate 2024
dc.date.none.fl_str_mv 2024
2024
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/acceptedVersion
format article
status_str acceptedVersion
dc.identifier.none.fl_str_mv http://hdl.handle.net/10230/60242
http://dx.doi.org/10.1016/j.jaad.2023.08.088
url http://hdl.handle.net/10230/60242
http://dx.doi.org/10.1016/j.jaad.2023.08.088
dc.language.none.fl_str_mv Inglés
language_invalid_str_mv Inglés
dc.relation.none.fl_str_mv J Am Acad Dermatol. 2024 Jan;90(1):66-73
dc.rights.none.fl_str_mv © Elsevier http://dx.doi.org/10.1016/j.jaad.2023.08.088
info:eu-repo/semantics/openAccess
rights_invalid_str_mv © Elsevier http://dx.doi.org/10.1016/j.jaad.2023.08.088
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
application/pdf
dc.publisher.none.fl_str_mv Elsevier
publisher.none.fl_str_mv Elsevier
dc.source.none.fl_str_mv reponame:Recercat. Dipósit de la Recerca de Catalunya
instname:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
instname_str Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
reponame_str Recercat. Dipósit de la Recerca de Catalunya
collection Recercat. Dipósit de la Recerca de Catalunya
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