RB1 gene mutation up-date, a meta-analysis based on 932 reported mutations available in a searchable database

[Background] Retinoblastoma, a prototype of hereditary cancer, is the most common intraocular tumour in children and potential cause of blindness from therapeutic eye ablation, second tumours in germ line carrier's survivors, and even death when left untreated. The molecular scanning of RB1 in...

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Detalhes bibliográficos
Autores: Valverde, José R., Alonso García de la Rosa, Francisco Javier, Palacios, Itziar, Pestaña, Ángel
Formato: artículo
Estado:Versión publicada
Fecha de publicación:2005
País:España
Recursos:Consejo Superior de Investigaciones Científicas (CSIC)
Repositorio:DIGITAL.CSIC. Repositorio Institucional del CSIC
OAI Identifier:oai:digital.csic.es:10261/3204
Acesso em linha:http://hdl.handle.net/10261/3204
Access Level:acceso abierto
Palavra-chave:Retinoblastoma
RB1 gene mutations
Database
Descrição
Resumo:[Background] Retinoblastoma, a prototype of hereditary cancer, is the most common intraocular tumour in children and potential cause of blindness from therapeutic eye ablation, second tumours in germ line carrier's survivors, and even death when left untreated. The molecular scanning of RB1 in search of germ line mutations lead to the publication of more than 900 mutations whose knowledge is important for genetic counselling and the characterization of phenotypic-genotypic relationships.