GEIS-21: a multicentric phase II study of intensive chemotherapy including gemcitabine and docetaxel for the treatment of Ewing sarcoma of children and adults: a report from the Spanish sarcoma group (GEIS)

Background: First Spanish trial of Ewing sarcoma (ES) including adults and children with the aim to test the efficacy of Gemcitabine and Docetaxel (G/D) in newly diagnosed high-risk (HR) patients. Methods: This was a prospective, multicentric, non-randomised, open study for patients p40 years with n...

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Detalles Bibliográficos
Autores: Mora, J., Castaneda, A., Perez-Jaume, S., Lopez-Pousa, A., Maradiegue, E., Valverde, Claudia, Martin-Broto, J., Garcia del Muro, Xavier, Cruz, Ofelia, Cruz, Josefina, Martinez-Trufero, J., Maurel, J., Vaz Salgado, Maria Angeles, de Alava, Enrique, de Torres, C.
Tipo de recurso: artículo
Fecha de publicación:2017
País:España
Institución:Conselleria de Salut i Consum del Govern de les Illes Balears
Repositorio:Docusalut
Idioma:inglés
OAI Identifier:oai:docusalut.com:20.500.13003/16597
Acceso en línea:https://hdl.handle.net/20.500.13003/16597
Access Level:acceso abierto
Palabra clave:Antineoplastic Combined Chemotherapy Protocols
Survival Rate
Odds Ratio
Sarcoma, Ewing
Prospective Studies
Prognosis
Age Factors
Taxoids
Adolescent
Deoxycytidine
Child, Preschool
Humans
Adult
Spain
Bone Neoplasms
Kaplan-Meier Estimate
Child
Disease-Free Survival
Niño
Adulto
Supervivencia sin Enfermedad
España
Neoplasias Óseas
Oportunidad Relativa
Taxoides
Adolescente
Tasa de Supervivencia
Humanos
Preescolar
Pronóstico
Sarcoma de Ewing
Factores de Edad
Protocolos de Quimioterapia Combinada Antineoplásica
Desoxicitidina
Estimación de Kaplan-Meier
Estudios Prospectivos
gemcitabine
docetaxel
Ewing sarcoma
adolescent and young adult sarcomas
minimal residual disease management
Descripción
Sumario:Background: First Spanish trial of Ewing sarcoma (ES) including adults and children with the aim to test the efficacy of Gemcitabine and Docetaxel (G/D) in newly diagnosed high-risk (HR) patients. Methods: This was a prospective, multicentric, non-randomised, open study for patients p40 years with newly diagnosed ES. HR patients (metastatic, axial-pelvic primaries or bone marrow micrometastasis) received 2 window cycles of G/D. Patients with an objective response (OR) to G/D received 12 monthly cycles of G/D after completion of mP6. The primary end point was the OR rate to the G/D window phase and the event-free survival (EFS) and overall survival (OS) for all patients. The study is registered at ClinicalTrials.gov (identifier: NCT00006734). Results: Forty-three patients were enroled, median age 17 years (range, 3-40). After a median follow-up of 43.4 months, the 5-year OS rate is 55.0% (95% CI, 41-74%) with an EFS of 50.0% (95% CI, 36-68%). The 5-year OS and EFS rates for standard risk (SR) patients was 76.0% (95% CI, 57-100%) and 71.0% (CI, 54-94%); for HR 36.0% (CI, 20-65%) and 29.0% (CI, 15-56%). Twelve of 17 (70.6%) high-risk (HR) patients showed an OR (7 PR and 5 SD) to G/D window therapy. The 5-year OS rate for patients p18 years of age was 74.0% (CI, 56-97%) and 31.0% for 418 years (95% CI, 15-66%), Po0.001. Grade 4 adverse events during mP6 occurred in 28/39 of patients (72%) and did not correlate with age. Multivariate survival analyses with o18 vs X18 and risk groups significant differences, Po0.00001. Using a Cox model for OS, both age and risk group were statistically significant (P = 0.0011 and P = 0.0065, respectively). Conclusions: Age at diagnosis is an independent prognostic factor superior to the presence of metastases with 18 years as the strongest cut-off. The mP6 regimen provided survival curves that plateau at 3 years and G/D produced significant responses in HR-ES that is worth further exploring.