Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report

Acute pulmonary artery dissection; Congenital heart disease; Pulmonary hypertension

Detalles Bibliográficos
Autores: tomasino, marco, Sambola Ayala, Antonia, Gordon Ramirez, Blanca, Soriano Colomé, Toni
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2023
País:España
Institución:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
Repositorio:Recercat. Dipósit de la Recerca de Catalunya
OAI Identifier:oai:recercat.cat:11351/10604
Acceso en línea:https://hdl.handle.net/11351/10604
http://hdl.handle.net/11351/10604
Access Level:acceso abierto
Palabra clave:Hipertensió pulmonar
Cardiopatia congènita
Artèria pulmonar
Aneurismes
DISEASES::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, Dissecting
ANATOMY::Cardiovascular System::Blood Vessels::Arteries::Pulmonary Artery
DISEASES::Respiratory Tract Diseases::Lung Diseases::Hypertension, Pulmonary
DISEASES::Cardiovascular Diseases::Cardiovascular Abnormalities::Heart Defects, Congenital
ENFERMEDADES::enfermedades cardiovasculares::enfermedades vasculares::aneurisma::aneurisma disecante
ANATOMÍA::sistema cardiovascular::vasos sanguíneos::arterias::arteria pulmonar
ENFERMEDADES::enfermedades respiratorias::enfermedades pulmonares::hipertensión pulmonar
ENFERMEDADES::enfermedades cardiovasculares::anomalías cardiovasculares::cardiopatías congénitas
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spelling Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case reporttomasino, marcoSambola Ayala, AntoniaGordon Ramirez, BlancaSoriano Colomé, ToniHipertensió pulmonarCardiopatia congènitaArtèria pulmonarAneurismesDISEASES::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, DissectingANATOMY::Cardiovascular System::Blood Vessels::Arteries::Pulmonary ArteryDISEASES::Respiratory Tract Diseases::Lung Diseases::Hypertension, PulmonaryDISEASES::Cardiovascular Diseases::Cardiovascular Abnormalities::Heart Defects, CongenitalENFERMEDADES::enfermedades cardiovasculares::enfermedades vasculares::aneurisma::aneurisma disecanteANATOMÍA::sistema cardiovascular::vasos sanguíneos::arterias::arteria pulmonarENFERMEDADES::enfermedades respiratorias::enfermedades pulmonares::hipertensión pulmonarENFERMEDADES::enfermedades cardiovasculares::anomalías cardiovasculares::cardiopatías congénitasAcute pulmonary artery dissection; Congenital heart disease; Pulmonary hypertensionDisección aguda de la arteria pulmonar; Cardiopatía congénita; Hipertensión pulmonarDissecció aguda de l'artèria pulmonar; Cardiopatia congènita; Hipertensió pulmonarBackground D-Transposition of the great arteries (d-TGA) is characterized by the aorta positioned above the right ventricle and the pulmonary artery above the left ventricle. Acute pulmonary artery dissection (PAD) is a rare and often lethal condition. We present a case report of acute PAD in an adult with d-TGA and pulmonary hypertension. Case summary A 49-year-old male with history of d-TGA palliated with an atrial switch (Mustard) operation, pulmonary venous baffle stenosis treated percutaneously, chronic pulmonary hypertension (mixed group 1 and 2), and severe dilatation of pulmonary arteries (pulmonary trunk of 75 mm) presented to the emergency department with chest pain and acute respiratory failure. Blood pressure was 106/78 mmHg, heart rate 93 b.p.m., and oxygen saturation 88% on room air. A computed tomography (CT) scan showed acute right PAD. He was not considered suitable for surgery nor percutaneous procedure. Epoprostenol was initiated to reduce parietal stress, but after initial stabilization, pulmonary venous stent baffle gradient increased and acute pulmonary oedema occurred. Epoprostenol was withdrawn, and furosemide was initiated, with good clinical response. A follow-up CT scan showed dissection morphological stabilization and false lumen thrombosis, and the patient was discharged. Discussion Pulmonary hypertension and previous pulmonary artery dilatation are reported as the main underlying conditions leading to PAD. No previous cases of PAD are described in patients with history of d-TGA and atrial switch procedure. Evidence regarding the best treatment of PAD is lacking, but it seems reasonable to reduce parietal stress using pulmonary vasodilators. Nevertheless, in patients with post-capillary pulmonary hypertension, pulmonary vasodilatation may cause important pulmonary congestion.Oxford University PressInstitut Català de la SalutServei de Cardiologia, Vall d'Hebron Hospital Universitari, Barcelona, SpainVall d'Hebron Barcelona Hospital Campus202320232023info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://hdl.handle.net/11351/10604http://hdl.handle.net/11351/10604Scientiareponame:Recercat. Dipósit de la Recerca de Catalunyainstname:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)InglésEuropean Heart Journal: Case Reports;7(10)https://doi.org/10.1093/ehjcr/ytad508Attribution-NonCommercial 4.0 Internationalhttp://creativecommons.org/licenses/by-nc/4.0/info:eu-repo/semantics/openAccessoai:recercat.cat:11351/106042026-05-29T05:05:01Z
dc.title.none.fl_str_mv Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report
title Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report
spellingShingle Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report
tomasino, marco
Hipertensió pulmonar
Cardiopatia congènita
Artèria pulmonar
Aneurismes
DISEASES::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, Dissecting
ANATOMY::Cardiovascular System::Blood Vessels::Arteries::Pulmonary Artery
DISEASES::Respiratory Tract Diseases::Lung Diseases::Hypertension, Pulmonary
DISEASES::Cardiovascular Diseases::Cardiovascular Abnormalities::Heart Defects, Congenital
ENFERMEDADES::enfermedades cardiovasculares::enfermedades vasculares::aneurisma::aneurisma disecante
ANATOMÍA::sistema cardiovascular::vasos sanguíneos::arterias::arteria pulmonar
ENFERMEDADES::enfermedades respiratorias::enfermedades pulmonares::hipertensión pulmonar
ENFERMEDADES::enfermedades cardiovasculares::anomalías cardiovasculares::cardiopatías congénitas
title_short Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report
title_full Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report
title_fullStr Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report
title_full_unstemmed Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report
title_sort Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report
dc.creator.none.fl_str_mv tomasino, marco
Sambola Ayala, Antonia
Gordon Ramirez, Blanca
Soriano Colomé, Toni
author tomasino, marco
author_facet tomasino, marco
Sambola Ayala, Antonia
Gordon Ramirez, Blanca
Soriano Colomé, Toni
author_role author
author2 Sambola Ayala, Antonia
Gordon Ramirez, Blanca
Soriano Colomé, Toni
author2_role author
author
author
dc.contributor.none.fl_str_mv Institut Català de la Salut
Servei de Cardiologia, Vall d'Hebron Hospital Universitari, Barcelona, Spain
Vall d'Hebron Barcelona Hospital Campus
dc.subject.none.fl_str_mv Hipertensió pulmonar
Cardiopatia congènita
Artèria pulmonar
Aneurismes
DISEASES::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, Dissecting
ANATOMY::Cardiovascular System::Blood Vessels::Arteries::Pulmonary Artery
DISEASES::Respiratory Tract Diseases::Lung Diseases::Hypertension, Pulmonary
DISEASES::Cardiovascular Diseases::Cardiovascular Abnormalities::Heart Defects, Congenital
ENFERMEDADES::enfermedades cardiovasculares::enfermedades vasculares::aneurisma::aneurisma disecante
ANATOMÍA::sistema cardiovascular::vasos sanguíneos::arterias::arteria pulmonar
ENFERMEDADES::enfermedades respiratorias::enfermedades pulmonares::hipertensión pulmonar
ENFERMEDADES::enfermedades cardiovasculares::anomalías cardiovasculares::cardiopatías congénitas
topic Hipertensió pulmonar
Cardiopatia congènita
Artèria pulmonar
Aneurismes
DISEASES::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, Dissecting
ANATOMY::Cardiovascular System::Blood Vessels::Arteries::Pulmonary Artery
DISEASES::Respiratory Tract Diseases::Lung Diseases::Hypertension, Pulmonary
DISEASES::Cardiovascular Diseases::Cardiovascular Abnormalities::Heart Defects, Congenital
ENFERMEDADES::enfermedades cardiovasculares::enfermedades vasculares::aneurisma::aneurisma disecante
ANATOMÍA::sistema cardiovascular::vasos sanguíneos::arterias::arteria pulmonar
ENFERMEDADES::enfermedades respiratorias::enfermedades pulmonares::hipertensión pulmonar
ENFERMEDADES::enfermedades cardiovasculares::anomalías cardiovasculares::cardiopatías congénitas
description Acute pulmonary artery dissection; Congenital heart disease; Pulmonary hypertension
publishDate 2023
dc.date.none.fl_str_mv 2023
2023
2023
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://hdl.handle.net/11351/10604
http://hdl.handle.net/11351/10604
url https://hdl.handle.net/11351/10604
http://hdl.handle.net/11351/10604
dc.language.none.fl_str_mv Inglés
language_invalid_str_mv Inglés
dc.relation.none.fl_str_mv European Heart Journal: Case Reports;7(10)
https://doi.org/10.1093/ehjcr/ytad508
dc.rights.none.fl_str_mv Attribution-NonCommercial 4.0 International
http://creativecommons.org/licenses/by-nc/4.0/
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Attribution-NonCommercial 4.0 International
http://creativecommons.org/licenses/by-nc/4.0/
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Oxford University Press
publisher.none.fl_str_mv Oxford University Press
dc.source.none.fl_str_mv Scientia
reponame:Recercat. Dipósit de la Recerca de Catalunya
instname:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
instname_str Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
reponame_str Recercat. Dipósit de la Recerca de Catalunya
collection Recercat. Dipósit de la Recerca de Catalunya
repository.name.fl_str_mv
repository.mail.fl_str_mv
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