Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report
Acute pulmonary artery dissection; Congenital heart disease; Pulmonary hypertension
| Autores: | , , , |
|---|---|
| Tipo de recurso: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2023 |
| País: | España |
| Institución: | Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya) |
| Repositorio: | Recercat. Dipósit de la Recerca de Catalunya |
| OAI Identifier: | oai:recercat.cat:11351/10604 |
| Acceso en línea: | https://hdl.handle.net/11351/10604 http://hdl.handle.net/11351/10604 |
| Access Level: | acceso abierto |
| Palabra clave: | Hipertensió pulmonar Cardiopatia congènita Artèria pulmonar Aneurismes DISEASES::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, Dissecting ANATOMY::Cardiovascular System::Blood Vessels::Arteries::Pulmonary Artery DISEASES::Respiratory Tract Diseases::Lung Diseases::Hypertension, Pulmonary DISEASES::Cardiovascular Diseases::Cardiovascular Abnormalities::Heart Defects, Congenital ENFERMEDADES::enfermedades cardiovasculares::enfermedades vasculares::aneurisma::aneurisma disecante ANATOMÍA::sistema cardiovascular::vasos sanguíneos::arterias::arteria pulmonar ENFERMEDADES::enfermedades respiratorias::enfermedades pulmonares::hipertensión pulmonar ENFERMEDADES::enfermedades cardiovasculares::anomalías cardiovasculares::cardiopatías congénitas |
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Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case reporttomasino, marcoSambola Ayala, AntoniaGordon Ramirez, BlancaSoriano Colomé, ToniHipertensió pulmonarCardiopatia congènitaArtèria pulmonarAneurismesDISEASES::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, DissectingANATOMY::Cardiovascular System::Blood Vessels::Arteries::Pulmonary ArteryDISEASES::Respiratory Tract Diseases::Lung Diseases::Hypertension, PulmonaryDISEASES::Cardiovascular Diseases::Cardiovascular Abnormalities::Heart Defects, CongenitalENFERMEDADES::enfermedades cardiovasculares::enfermedades vasculares::aneurisma::aneurisma disecanteANATOMÍA::sistema cardiovascular::vasos sanguíneos::arterias::arteria pulmonarENFERMEDADES::enfermedades respiratorias::enfermedades pulmonares::hipertensión pulmonarENFERMEDADES::enfermedades cardiovasculares::anomalías cardiovasculares::cardiopatías congénitasAcute pulmonary artery dissection; Congenital heart disease; Pulmonary hypertensionDisección aguda de la arteria pulmonar; Cardiopatía congénita; Hipertensión pulmonarDissecció aguda de l'artèria pulmonar; Cardiopatia congènita; Hipertensió pulmonarBackground D-Transposition of the great arteries (d-TGA) is characterized by the aorta positioned above the right ventricle and the pulmonary artery above the left ventricle. Acute pulmonary artery dissection (PAD) is a rare and often lethal condition. We present a case report of acute PAD in an adult with d-TGA and pulmonary hypertension. Case summary A 49-year-old male with history of d-TGA palliated with an atrial switch (Mustard) operation, pulmonary venous baffle stenosis treated percutaneously, chronic pulmonary hypertension (mixed group 1 and 2), and severe dilatation of pulmonary arteries (pulmonary trunk of 75 mm) presented to the emergency department with chest pain and acute respiratory failure. Blood pressure was 106/78 mmHg, heart rate 93 b.p.m., and oxygen saturation 88% on room air. A computed tomography (CT) scan showed acute right PAD. He was not considered suitable for surgery nor percutaneous procedure. Epoprostenol was initiated to reduce parietal stress, but after initial stabilization, pulmonary venous stent baffle gradient increased and acute pulmonary oedema occurred. Epoprostenol was withdrawn, and furosemide was initiated, with good clinical response. A follow-up CT scan showed dissection morphological stabilization and false lumen thrombosis, and the patient was discharged. Discussion Pulmonary hypertension and previous pulmonary artery dilatation are reported as the main underlying conditions leading to PAD. No previous cases of PAD are described in patients with history of d-TGA and atrial switch procedure. Evidence regarding the best treatment of PAD is lacking, but it seems reasonable to reduce parietal stress using pulmonary vasodilators. Nevertheless, in patients with post-capillary pulmonary hypertension, pulmonary vasodilatation may cause important pulmonary congestion.Oxford University PressInstitut Català de la SalutServei de Cardiologia, Vall d'Hebron Hospital Universitari, Barcelona, SpainVall d'Hebron Barcelona Hospital Campus202320232023info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://hdl.handle.net/11351/10604http://hdl.handle.net/11351/10604Scientiareponame:Recercat. Dipósit de la Recerca de Catalunyainstname:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)InglésEuropean Heart Journal: Case Reports;7(10)https://doi.org/10.1093/ehjcr/ytad508Attribution-NonCommercial 4.0 Internationalhttp://creativecommons.org/licenses/by-nc/4.0/info:eu-repo/semantics/openAccessoai:recercat.cat:11351/106042026-05-29T05:05:01Z |
| dc.title.none.fl_str_mv |
Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report |
| title |
Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report |
| spellingShingle |
Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report tomasino, marco Hipertensió pulmonar Cardiopatia congènita Artèria pulmonar Aneurismes DISEASES::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, Dissecting ANATOMY::Cardiovascular System::Blood Vessels::Arteries::Pulmonary Artery DISEASES::Respiratory Tract Diseases::Lung Diseases::Hypertension, Pulmonary DISEASES::Cardiovascular Diseases::Cardiovascular Abnormalities::Heart Defects, Congenital ENFERMEDADES::enfermedades cardiovasculares::enfermedades vasculares::aneurisma::aneurisma disecante ANATOMÍA::sistema cardiovascular::vasos sanguíneos::arterias::arteria pulmonar ENFERMEDADES::enfermedades respiratorias::enfermedades pulmonares::hipertensión pulmonar ENFERMEDADES::enfermedades cardiovasculares::anomalías cardiovasculares::cardiopatías congénitas |
| title_short |
Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report |
| title_full |
Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report |
| title_fullStr |
Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report |
| title_full_unstemmed |
Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report |
| title_sort |
Acute pulmonary artery dissection in an adult with chronic pulmonary hypertension secondary to congenital heart disease: a case report |
| dc.creator.none.fl_str_mv |
tomasino, marco Sambola Ayala, Antonia Gordon Ramirez, Blanca Soriano Colomé, Toni |
| author |
tomasino, marco |
| author_facet |
tomasino, marco Sambola Ayala, Antonia Gordon Ramirez, Blanca Soriano Colomé, Toni |
| author_role |
author |
| author2 |
Sambola Ayala, Antonia Gordon Ramirez, Blanca Soriano Colomé, Toni |
| author2_role |
author author author |
| dc.contributor.none.fl_str_mv |
Institut Català de la Salut Servei de Cardiologia, Vall d'Hebron Hospital Universitari, Barcelona, Spain Vall d'Hebron Barcelona Hospital Campus |
| dc.subject.none.fl_str_mv |
Hipertensió pulmonar Cardiopatia congènita Artèria pulmonar Aneurismes DISEASES::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, Dissecting ANATOMY::Cardiovascular System::Blood Vessels::Arteries::Pulmonary Artery DISEASES::Respiratory Tract Diseases::Lung Diseases::Hypertension, Pulmonary DISEASES::Cardiovascular Diseases::Cardiovascular Abnormalities::Heart Defects, Congenital ENFERMEDADES::enfermedades cardiovasculares::enfermedades vasculares::aneurisma::aneurisma disecante ANATOMÍA::sistema cardiovascular::vasos sanguíneos::arterias::arteria pulmonar ENFERMEDADES::enfermedades respiratorias::enfermedades pulmonares::hipertensión pulmonar ENFERMEDADES::enfermedades cardiovasculares::anomalías cardiovasculares::cardiopatías congénitas |
| topic |
Hipertensió pulmonar Cardiopatia congènita Artèria pulmonar Aneurismes DISEASES::Cardiovascular Diseases::Vascular Diseases::Aneurysm::Aneurysm, Dissecting ANATOMY::Cardiovascular System::Blood Vessels::Arteries::Pulmonary Artery DISEASES::Respiratory Tract Diseases::Lung Diseases::Hypertension, Pulmonary DISEASES::Cardiovascular Diseases::Cardiovascular Abnormalities::Heart Defects, Congenital ENFERMEDADES::enfermedades cardiovasculares::enfermedades vasculares::aneurisma::aneurisma disecante ANATOMÍA::sistema cardiovascular::vasos sanguíneos::arterias::arteria pulmonar ENFERMEDADES::enfermedades respiratorias::enfermedades pulmonares::hipertensión pulmonar ENFERMEDADES::enfermedades cardiovasculares::anomalías cardiovasculares::cardiopatías congénitas |
| description |
Acute pulmonary artery dissection; Congenital heart disease; Pulmonary hypertension |
| publishDate |
2023 |
| dc.date.none.fl_str_mv |
2023 2023 2023 |
| dc.type.none.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
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article |
| status_str |
publishedVersion |
| dc.identifier.none.fl_str_mv |
https://hdl.handle.net/11351/10604 http://hdl.handle.net/11351/10604 |
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https://hdl.handle.net/11351/10604 http://hdl.handle.net/11351/10604 |
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Inglés |
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Inglés |
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European Heart Journal: Case Reports;7(10) https://doi.org/10.1093/ehjcr/ytad508 |
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Attribution-NonCommercial 4.0 International http://creativecommons.org/licenses/by-nc/4.0/ info:eu-repo/semantics/openAccess |
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Attribution-NonCommercial 4.0 International http://creativecommons.org/licenses/by-nc/4.0/ |
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openAccess |
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application/pdf |
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Oxford University Press |
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Oxford University Press |
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Scientia reponame:Recercat. Dipósit de la Recerca de Catalunya instname:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya) |
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Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya) |
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Recercat. Dipósit de la Recerca de Catalunya |
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