Sporadic Creutzfeldt-Jakob disease with glial PrPRes nuclear and perinuclear immunoreactivity

Proteinase K-resistant prion protein (PrPRes ) nuclear and perinuclear immunoreactivity in oligodendrocytes of the frontal cortex is found in one case of otherwise typical sporadic Creutzfeldt-Jakob disease (sCJD) type VV2a. The PrP nature of the inclusions is validated with several anti-PrP antibod...

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Detalles Bibliográficos
Autores: Fernández-Vega, Iván, Diaz-Lucena, Daniela, Azkune Calle, Itxaso, Geijo, Maria, Juste, Ramón A., Llorens Torres, Franc, Vicente Etxenausia, Ikerne, Santos-Juanes, Jorge, Zarranz, Juan J., Ferrer, Isidro (Ferrer Abizanda)
Tipo de recurso: artículo
Estado:Versión aceptada para publicación
Fecha de publicación:2018
País:España
Institución:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
Repositorio:Recercat. Dipósit de la Recerca de Catalunya
OAI Identifier:oai:recercat.cat:2445/155518
Acceso en línea:https://hdl.handle.net/2445/155518
Access Level:acceso abierto
Palabra clave:Malaltia de Creutzfeldt-Jakob
Neuròglia
Prions
Proteïnes
Metabolisme
Patologia
Creutzfeldt-Jakob disease
Neuroglia
Proteins
Metabolism
Pathology
Descripción
Sumario:Proteinase K-resistant prion protein (PrPRes ) nuclear and perinuclear immunoreactivity in oligodendrocytes of the frontal cortex is found in one case of otherwise typical sporadic Creutzfeldt-Jakob disease (sCJD) type VV2a. The PrP nature of the inclusions is validated with several anti-PrP antibodies directed to amino acids 130-160 (12F10), 109-112 (3F4), 97-102 (8G8) and the octarepeat region (amino acids 59-89: SAF32). Cellular identification and subcellular localization were evaluated with double- and triple-labeling immunofluorescence and confocal microscopy using antibodies against PrP, glial markers, and histone H3. Based on review of the literature and our own experience, this is a very odd situation that deserves further validation in other cases. Keywords: Creutzfeldt-Jakob disease; astrocytes; oligodendrocytes; prion.