Similarities and differences between systemic juvenile idiopathic arthritis and adult-onset Still's disease: a multicenter Spanish study
Adult-onset still’s disease; Epidemiology; Juvenile arthritis;
| Autores: | , , , , , , |
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| Tipo de recurso: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2024 |
| País: | España |
| Institución: | Departament de Salut de la Generalitat de Catalunya (DS) |
| Repositorio: | Scientia. Dipòsit d'Informació Digital del Departament de Salut |
| OAI Identifier: | oai:dnet:scientia____::b4f69c287e7cfa50e78952fa40d07f97 |
| Acceso en línea: | http://hdl.handle.net/11351/14440 |
| Access Level: | acceso abierto |
| Palabra clave: | Artritis reumatoide - Epidemiologia Malalties autoimmunitàries - Epidemiologia DISEASES::Musculoskeletal Diseases::Joint Diseases::Arthritis::Arthritis, Rheumatoid::Still's Disease, Adult-Onset DISEASES::Musculoskeletal Diseases::Joint Diseases::Arthritis ANALYTICAL, DIAGNOSTIC AND THERAPEUTIC TECHNIQUES, AND EQUIPMENT::Investigative Techniques::Epidemiologic Methods::Epidemiologic Study Characteristics::Epidemiologic Studies::Case-Control Studies::Retrospective Studies ENFERMEDADES::enfermedades musculoesqueléticas::artropatías::artritis::artritis reumatoide::enfermedad de Still del adulto ENFERMEDADES::enfermedades musculoesqueléticas::artropatías::artritis TÉCNICAS Y EQUIPOS ANALÍTICOS, DIAGNÓSTICOS Y TERAPÉUTICOS::técnicas de investigación::métodos epidemiológicos::características de los estudios epidemiológicos::estudios epidemiológicos::estudios de casos y controles::estudios retrospectivos |
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Similarities and differences between systemic juvenile idiopathic arthritis and adult-onset Still's disease: a multicenter Spanish studyMosquera Angarita, Juan ManuelIglesias , Estíbaliz Zacarias Crovato, AndreaOlivé, AlejandroORTIZ-SANTAMARIA, VERAAnton, JordiCalzada-Hernández, JoanArtritis reumatoide - EpidemiologiaMalalties autoimmunitàries - EpidemiologiaDISEASES::Musculoskeletal Diseases::Joint Diseases::Arthritis::Arthritis, Rheumatoid::Still's Disease, Adult-OnsetDISEASES::Musculoskeletal Diseases::Joint Diseases::ArthritisANALYTICAL, DIAGNOSTIC AND THERAPEUTIC TECHNIQUES, AND EQUIPMENT::Investigative Techniques::Epidemiologic Methods::Epidemiologic Study Characteristics::Epidemiologic Studies::Case-Control Studies::Retrospective StudiesENFERMEDADES::enfermedades musculoesqueléticas::artropatías::artritis::artritis reumatoide::enfermedad de Still del adultoENFERMEDADES::enfermedades musculoesqueléticas::artropatías::artritisTÉCNICAS Y EQUIPOS ANALÍTICOS, DIAGNÓSTICOS Y TERAPÉUTICOS::técnicas de investigación::métodos epidemiológicos::características de los estudios epidemiológicos::estudios epidemiológicos::estudios de casos y controles::estudios retrospectivosAdult-onset still’s disease; Epidemiology; Juvenile arthritis;Enfermedad de Still de inicio en la edad adulta; Epidemiología; Artritis juvenilMalaltia de Still d'aparició en adults; Epidemiologia; Artritis juvenilTo describe the characteristics of systemic juvenile idiopathic arthritis (sJIA) and adult-onset Still's disease (AOSD), compare their presentation and evolution, and analyse possible complication predictors. Multicenter study. Data were retrieved from a hospital-based study of patients with a diagnosis or suspected diagnosis of sJIA or AOSD according to the responsible physician and followed-up for at least one year. Descriptive variables (classification criteria, clinical manifestations, complications, family, and personal history) were collected at disease onset and during follow-up. We present the clinical characteristics of 326 patients, 67% of whom had a diagnosis of sJIA and 33% of AOSD. Clinical manifestation frequencies were similar between the two groups, except for odynophagia, which was significantly more frequent in AOSD than in sJIA (78.4% vs. 25.5%; p < 0.0001). Among the complications, macrophage activation syndrome (MAS) was significantly more common in sJIA than in AOSD (24.4% vs. 9.5%; p = 0.002), to the extent that an sJIA diagnosis significantly increased the risk of MAS, together with serositis presence, and the need for biological therapy. Patients with sJIA and AOSD showed similar characteristics, supporting the idea that they are both part of Still's disease, but are expressed at different ages. Differences in manifestations and complications might be due to different management between diseases and immune response maturity.Springer[Antón J] Hospital Sant Joan de Déu, Barcelona, Spain. Departament de Cirurgia i Especialitats Mèdico-Quirúrgiques, Obstetrícia, Ginecologia i Pediatria, Facultat de Medicina i Ciències de la Salut, Universitat de Barcelona, Barcelona, Spain. [Mosquera JM, Calzada J, Iglesias E, Zacarías A] Hospital Sant Joan de Déu, Barcelona, Spain. [Olivé A] Hospital Universitari Germans Trias i Pujol, Badalona, Spain. [Ortiz-Santamaria V] Hospital General de Granollers, Granollers, Spain.Hospital General de Granollers202620262024info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttp://hdl.handle.net/11351/14440Scientiareponame:Scientia. Dipòsit d'Informació Digital del Departament de Salutinstname:Departament de Salut de la Generalitat de Catalunya (DS)InglésRheumatology international;44(12)https://doi.org/10.1007/s00296-024-05658-6Attribution 4.0 Internationalhttp://creativecommons.org/licenses/by/4.0/info:eu-repo/semantics/openAccessoai:dnet:scientia____::b4f69c287e7cfa50e78952fa40d07f972026-06-12T09:38:37Z |
| dc.title.none.fl_str_mv |
Similarities and differences between systemic juvenile idiopathic arthritis and adult-onset Still's disease: a multicenter Spanish study |
| title |
Similarities and differences between systemic juvenile idiopathic arthritis and adult-onset Still's disease: a multicenter Spanish study |
| spellingShingle |
Similarities and differences between systemic juvenile idiopathic arthritis and adult-onset Still's disease: a multicenter Spanish study Mosquera Angarita, Juan Manuel Artritis reumatoide - Epidemiologia Malalties autoimmunitàries - Epidemiologia DISEASES::Musculoskeletal Diseases::Joint Diseases::Arthritis::Arthritis, Rheumatoid::Still's Disease, Adult-Onset DISEASES::Musculoskeletal Diseases::Joint Diseases::Arthritis ANALYTICAL, DIAGNOSTIC AND THERAPEUTIC TECHNIQUES, AND EQUIPMENT::Investigative Techniques::Epidemiologic Methods::Epidemiologic Study Characteristics::Epidemiologic Studies::Case-Control Studies::Retrospective Studies ENFERMEDADES::enfermedades musculoesqueléticas::artropatías::artritis::artritis reumatoide::enfermedad de Still del adulto ENFERMEDADES::enfermedades musculoesqueléticas::artropatías::artritis TÉCNICAS Y EQUIPOS ANALÍTICOS, DIAGNÓSTICOS Y TERAPÉUTICOS::técnicas de investigación::métodos epidemiológicos::características de los estudios epidemiológicos::estudios epidemiológicos::estudios de casos y controles::estudios retrospectivos |
| title_short |
Similarities and differences between systemic juvenile idiopathic arthritis and adult-onset Still's disease: a multicenter Spanish study |
| title_full |
Similarities and differences between systemic juvenile idiopathic arthritis and adult-onset Still's disease: a multicenter Spanish study |
| title_fullStr |
Similarities and differences between systemic juvenile idiopathic arthritis and adult-onset Still's disease: a multicenter Spanish study |
| title_full_unstemmed |
Similarities and differences between systemic juvenile idiopathic arthritis and adult-onset Still's disease: a multicenter Spanish study |
| title_sort |
Similarities and differences between systemic juvenile idiopathic arthritis and adult-onset Still's disease: a multicenter Spanish study |
| dc.creator.none.fl_str_mv |
Mosquera Angarita, Juan Manuel Iglesias , Estíbaliz Zacarias Crovato, Andrea Olivé, Alejandro ORTIZ-SANTAMARIA, VERA Anton, Jordi Calzada-Hernández, Joan |
| author |
Mosquera Angarita, Juan Manuel |
| author_facet |
Mosquera Angarita, Juan Manuel Iglesias , Estíbaliz Zacarias Crovato, Andrea Olivé, Alejandro ORTIZ-SANTAMARIA, VERA Anton, Jordi Calzada-Hernández, Joan |
| author_role |
author |
| author2 |
Iglesias , Estíbaliz Zacarias Crovato, Andrea Olivé, Alejandro ORTIZ-SANTAMARIA, VERA Anton, Jordi Calzada-Hernández, Joan |
| author2_role |
author author author author author author |
| dc.contributor.none.fl_str_mv |
[Antón J] Hospital Sant Joan de Déu, Barcelona, Spain. Departament de Cirurgia i Especialitats Mèdico-Quirúrgiques, Obstetrícia, Ginecologia i Pediatria, Facultat de Medicina i Ciències de la Salut, Universitat de Barcelona, Barcelona, Spain. [Mosquera JM, Calzada J, Iglesias E, Zacarías A] Hospital Sant Joan de Déu, Barcelona, Spain. [Olivé A] Hospital Universitari Germans Trias i Pujol, Badalona, Spain. [Ortiz-Santamaria V] Hospital General de Granollers, Granollers, Spain. Hospital General de Granollers |
| dc.subject.none.fl_str_mv |
Artritis reumatoide - Epidemiologia Malalties autoimmunitàries - Epidemiologia DISEASES::Musculoskeletal Diseases::Joint Diseases::Arthritis::Arthritis, Rheumatoid::Still's Disease, Adult-Onset DISEASES::Musculoskeletal Diseases::Joint Diseases::Arthritis ANALYTICAL, DIAGNOSTIC AND THERAPEUTIC TECHNIQUES, AND EQUIPMENT::Investigative Techniques::Epidemiologic Methods::Epidemiologic Study Characteristics::Epidemiologic Studies::Case-Control Studies::Retrospective Studies ENFERMEDADES::enfermedades musculoesqueléticas::artropatías::artritis::artritis reumatoide::enfermedad de Still del adulto ENFERMEDADES::enfermedades musculoesqueléticas::artropatías::artritis TÉCNICAS Y EQUIPOS ANALÍTICOS, DIAGNÓSTICOS Y TERAPÉUTICOS::técnicas de investigación::métodos epidemiológicos::características de los estudios epidemiológicos::estudios epidemiológicos::estudios de casos y controles::estudios retrospectivos |
| topic |
Artritis reumatoide - Epidemiologia Malalties autoimmunitàries - Epidemiologia DISEASES::Musculoskeletal Diseases::Joint Diseases::Arthritis::Arthritis, Rheumatoid::Still's Disease, Adult-Onset DISEASES::Musculoskeletal Diseases::Joint Diseases::Arthritis ANALYTICAL, DIAGNOSTIC AND THERAPEUTIC TECHNIQUES, AND EQUIPMENT::Investigative Techniques::Epidemiologic Methods::Epidemiologic Study Characteristics::Epidemiologic Studies::Case-Control Studies::Retrospective Studies ENFERMEDADES::enfermedades musculoesqueléticas::artropatías::artritis::artritis reumatoide::enfermedad de Still del adulto ENFERMEDADES::enfermedades musculoesqueléticas::artropatías::artritis TÉCNICAS Y EQUIPOS ANALÍTICOS, DIAGNÓSTICOS Y TERAPÉUTICOS::técnicas de investigación::métodos epidemiológicos::características de los estudios epidemiológicos::estudios epidemiológicos::estudios de casos y controles::estudios retrospectivos |
| description |
Adult-onset still’s disease; Epidemiology; Juvenile arthritis; |
| publishDate |
2024 |
| dc.date.none.fl_str_mv |
2024 2026 2026 |
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info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
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article |
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publishedVersion |
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http://hdl.handle.net/11351/14440 |
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http://hdl.handle.net/11351/14440 |
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Inglés |
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Inglés |
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Rheumatology international;44(12) https://doi.org/10.1007/s00296-024-05658-6 |
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Attribution 4.0 International http://creativecommons.org/licenses/by/4.0/ info:eu-repo/semantics/openAccess |
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Attribution 4.0 International http://creativecommons.org/licenses/by/4.0/ |
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openAccess |
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application/pdf |
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Springer |
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Springer |
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Scientia reponame:Scientia. Dipòsit d'Informació Digital del Departament de Salut instname:Departament de Salut de la Generalitat de Catalunya (DS) |
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Departament de Salut de la Generalitat de Catalunya (DS) |
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Scientia. Dipòsit d'Informació Digital del Departament de Salut |
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Scientia. Dipòsit d'Informació Digital del Departament de Salut |
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15.812429 |