Exon junction complex shapes the transcriptome by repressing recursive splicing

Recursive splicing (RS) starts by defining an "RS-exon," which is then spliced to the preceding exon, thus creating a recursive 5' splice site (RS-5ss). Previous studies focused on cryptic RS-exons, and now we find that the exon junction complex (EJC) represses RS of hundr...

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Detalles Bibliográficos
Autores: Blazquez, Lorea, Emmett, Warren, Faraway, Rupert, Pineda, Jose Mario Bello, Bajew, Simon, 1994-, Gohr, André, Haberman, Nejc, Sibley, Christopher R., Bradley, Robert K., Irimia Martínez, Manuel, Ule, Jernej
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2018
País:España
Institución:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
Repositorio:Recercat. Dipósit de la Recerca de Catalunya
OAI Identifier:oai:recercat.cat:10230/42934
Acceso en línea:http://hdl.handle.net/10230/42934
http://dx.doi.org/10.1016/j.molcel.2018.09.033
Access Level:acceso abierto
Palabra clave:RS exon
Alternative splicing mechanisms
Evolution
Exon junction complex
Gene expression
Microcephaly
Microexon
Neurodevelopmental disorders
Recursive splicing
Descripción
Sumario:Recursive splicing (RS) starts by defining an "RS-exon," which is then spliced to the preceding exon, thus creating a recursive 5' splice site (RS-5ss). Previous studies focused on cryptic RS-exons, and now we find that the exon junction complex (EJC) represses RS of hundreds of annotated, mainly constitutive RS-exons. The core EJC factors, and the peripheral factors PNN and RNPS1, maintain RS-exon inclusion by repressing spliceosomal assembly on RS-5ss. The EJC also blocks 5ss located near exon-exon junctions, thus repressing inclusion of cryptic microexons. The prevalence of annotated RS-exons is high in deuterostomes, while the cryptic RS-exons are more prevalent in Drosophila, where EJC appears less capable of repressing RS. Notably, incomplete repression of RS also contributes to physiological alternative splicing of several human RS-exons. Finally, haploinsufficiency of the EJC factor Magoh in mice is associated with skipping of RS-exons in the brain, with relevance to the microcephaly phenotype and human diseases.