Rehabilitación neuropsicológica en personas con síndrome de Prader-Willi

Prader-Willi Syndrome (PWS) is a complex neurodevelopmental disorder caused by genetic anomalies that presents itself with a characteristic neurobehavioral phenotype. The aim of this project was to analyze interventions of neuropsychological rehabilitation that exist in PWS and to achieve it, a syst...

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Detalles Bibliográficos
Autor: Tapia de Moya, Karol
Tipo de recurso: artículo
Fecha de publicación:2017
País:España
Institución:Universidad de Salamanca (USAL)
Repositorio:GREDOS. Repositorio Institucional de la Universidad de Salamanca
OAI Identifier:oai:gredos.usal.es:10366/137863
Acceso en línea:http://hdl.handle.net/10366/137863
Access Level:acceso abierto
Palabra clave:Familia y Salud
Hacer frente a la discapacidad
Health and Family
Coping with disability
Descripción
Sumario:Prader-Willi Syndrome (PWS) is a complex neurodevelopmental disorder caused by genetic anomalies that presents itself with a characteristic neurobehavioral phenotype. The aim of this project was to analyze interventions of neuropsychological rehabilitation that exist in PWS and to achieve it, a systematic search was done, resulting in a total of 14 articles with interventions for behavioral, cognitive and familial phenotypical characteristics. The studies were analyzed according to the focus of the intervention, models, specific procedures and results. Most studies used a compensation model and almost all applied behavioral modification techniques. The results suggest that techniques that use differential reinforcement and a more active involvement of the person with PWS and their family during intervention, are more successful.