Genomic instability in mice lacking histone H2AX.

Higher order chromatin structure presents a barrier to the recognition and repair of DNA damage. Double-strand breaks (DSBs) induce histone H2AX phosphorylation, which is associated with the recruitment of repair factors to damaged DNA. To help clarify the physiological role of H2AX, we targeted H2A...

Descripción completa

Detalles Bibliográficos
Autores: Celeste, Arkady, Petersen, Simone, Romanienko, Peter J, Fernandez-Capetillo, Oscar, Chen, Hua Tang, Sedelnikova, Olga A, Reina-San-Martin, Bernardo, Coppola, Vincenzo, Meffre, Eric, Difilippantonio, Michael J, Redon, Christophe, Pilch, Duane R, Olaru, Alexandru, Eckhaus, Michael, Camerini-Otero, R Daniel, Tessarollo, Lino, Livak, Ferenc, Manova, Katia, Bonner, William M, Nussenzweig, Michel C, Nussenzweig, André
Tipo de recurso: artículo
Fecha de publicación:2002
País:España
Institución:Instituto de Salud Carlos III (ISCIII)
Repositorio:Repisalud
Idioma:inglés
OAI Identifier:oai:repisalud.isciii.es:20.500.12105/17702
Acceso en línea:http://hdl.handle.net/20.500.12105/17702
Access Level:acceso abierto
Palabra clave:Chromosome Aberrations
DNA Repair
Recombination, Genetic
Amino Acid Sequence
Animals
B-Lymphocytes
Base Sequence
Cell Cycle
Cells, Cultured
Cellular Senescence
DNA Damage
Female
Gene Targeting
Histones
Immunoglobulin Class Switching
Infertility, Male
Lymphocyte Count
Male
Meiosis
Mice
Mice, Knockout
Molecular Sequence Data
Mutation
Phosphorylation
Spermatocytes
T-Lymphocytes
Descripción
Sumario:Higher order chromatin structure presents a barrier to the recognition and repair of DNA damage. Double-strand breaks (DSBs) induce histone H2AX phosphorylation, which is associated with the recruitment of repair factors to damaged DNA. To help clarify the physiological role of H2AX, we targeted H2AX in mice. Although H2AX is not essential for irradiation-induced cell-cycle checkpoints, H2AX-/- mice were radiation sensitive, growth retarded, and immune deficient, and mutant males were infertile. These pleiotropic phenotypes were associated with chromosomal instability, repair defects, and impaired recruitment of Nbs1, 53bp1, and Brca1, but not Rad51, to irradiation-induced foci. Thus, H2AX is critical for facilitating the assembly of specific DNA-repair complexes on damaged DNA.