Calmodulin-dependent KCNE4 dimerization controls membrane targeting.

The voltage-dependent potassium channel Kv1.3 participates in the immune response. Kv1.3 is essential in diferent cellular functions, such as proliferation, activation and apoptosis. Because aberrant expression of Kv1.3 is linked to autoimmune diseases, fne-tuning its function is crucial for leukocy...

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Autores: Roig, Sara R., Solé, Laura, Cassinelli, Silvia, Colomer-Molera, Magalí, Sastre Martinez, Daniel, Serrano-Novillo, Clara, Serrano-Albarrás, Antonio, Lillo, M. Pilar, Tamkun, Michael M., Felipe Campo, Antonio
Formato: artículo
Estado:Versión publicada
Fecha de publicación:2021
País:España
Recursos:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
Repositorio:Recercat. Dipósit de la Recerca de Catalunya
OAI Identifier:oai:recercat.cat:2445/186238
Acesso em linha:https://hdl.handle.net/2445/186238
Access Level:acceso abierto
Palavra-chave:Malalties autoimmunitàries
Canals de potassi
Reticle endoplasmàtic
Autoimmune diseases
Potassium channels
Endoplasmic reticulum
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spelling Calmodulin-dependent KCNE4 dimerization controls membrane targeting.Roig, Sara R.Solé, LauraCassinelli, SilviaColomer-Molera, MagalíSastre Martinez, DanielSerrano-Novillo, ClaraSerrano-Albarrás, AntonioLillo, M. PilarTamkun, Michael M.Felipe Campo, AntonioMalalties autoimmunitàriesCanals de potassiReticle endoplasmàticAutoimmune diseasesPotassium channelsEndoplasmic reticulumThe voltage-dependent potassium channel Kv1.3 participates in the immune response. Kv1.3 is essential in diferent cellular functions, such as proliferation, activation and apoptosis. Because aberrant expression of Kv1.3 is linked to autoimmune diseases, fne-tuning its function is crucial for leukocyte physiology. Regulatory KCNE subunits are expressed in the immune system, and KCNE4 specifcally tightly regulates Kv1.3. KCNE4 modulates Kv1.3 currents slowing activation, accelerating inactivation and retaining the channel at the endoplasmic reticulum (ER), thereby altering its membrane localization. In addition, KCNE4 genomic variants are associated with immune pathologies. Therefore, an in-depth knowledge of KCNE4 function is extremely relevant for understanding immune system physiology. We demonstrate that KCNE4 dimerizes, which is unique among KCNE regulatory peptide family members. Furthermore, the juxtamembrane tetraleucine carboxyl-terminal domain of KCNE4 is a structural platform in which Kv1.3, Ca2+/calmodulin (CaM) and dimerizing KCNE4 compete for multiple interaction partners. CaM-dependent KCNE4 dimerization controls KCNE4 membrane targeting and modulates its interaction with Kv1.3. KCNE4, which is highly retained at the ER, contains an important ER retention motif near the tetraleucine motif. Upon escaping the ER in a CaM-dependent pattern, KCNE4 follows a COP-II-dependent forward trafcking mechanism. Therefore, CaM, an essential signaling molecule that controls the dimerization and membrane targeting of KCNE4, modulates the KCNE4-dependent regulation of Kv1.3, which in turn fne-tunes leukocyte physiology.Nature Publishing Group2022202220212022info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersion16 p.application/pdfhttps://hdl.handle.net/2445/186238Articles publicats en revistes (Bioquímica i Biomedicina Molecular)reponame:Recercat. Dipósit de la Recerca de Catalunyainstname:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)InglésReproducció del document publicat a: https://doi.org/10.1038/s41598-021-93562-5Scientific Reports, 2021, vol. 11, num. 1, p. 14046https://doi.org/10.1038/s41598-021-93562-5cc-by (c) Roig, Sara R. et al., 2021https://creativecommons.org/licenses/by/4.0/info:eu-repo/semantics/openAccessoai:recercat.cat:2445/1862382026-05-29T05:05:01Z
dc.title.none.fl_str_mv Calmodulin-dependent KCNE4 dimerization controls membrane targeting.
title Calmodulin-dependent KCNE4 dimerization controls membrane targeting.
spellingShingle Calmodulin-dependent KCNE4 dimerization controls membrane targeting.
Roig, Sara R.
Malalties autoimmunitàries
Canals de potassi
Reticle endoplasmàtic
Autoimmune diseases
Potassium channels
Endoplasmic reticulum
title_short Calmodulin-dependent KCNE4 dimerization controls membrane targeting.
title_full Calmodulin-dependent KCNE4 dimerization controls membrane targeting.
title_fullStr Calmodulin-dependent KCNE4 dimerization controls membrane targeting.
title_full_unstemmed Calmodulin-dependent KCNE4 dimerization controls membrane targeting.
title_sort Calmodulin-dependent KCNE4 dimerization controls membrane targeting.
dc.creator.none.fl_str_mv Roig, Sara R.
Solé, Laura
Cassinelli, Silvia
Colomer-Molera, Magalí
Sastre Martinez, Daniel
Serrano-Novillo, Clara
Serrano-Albarrás, Antonio
Lillo, M. Pilar
Tamkun, Michael M.
Felipe Campo, Antonio
author Roig, Sara R.
author_facet Roig, Sara R.
Solé, Laura
Cassinelli, Silvia
Colomer-Molera, Magalí
Sastre Martinez, Daniel
Serrano-Novillo, Clara
Serrano-Albarrás, Antonio
Lillo, M. Pilar
Tamkun, Michael M.
Felipe Campo, Antonio
author_role author
author2 Solé, Laura
Cassinelli, Silvia
Colomer-Molera, Magalí
Sastre Martinez, Daniel
Serrano-Novillo, Clara
Serrano-Albarrás, Antonio
Lillo, M. Pilar
Tamkun, Michael M.
Felipe Campo, Antonio
author2_role author
author
author
author
author
author
author
author
author
dc.subject.none.fl_str_mv Malalties autoimmunitàries
Canals de potassi
Reticle endoplasmàtic
Autoimmune diseases
Potassium channels
Endoplasmic reticulum
topic Malalties autoimmunitàries
Canals de potassi
Reticle endoplasmàtic
Autoimmune diseases
Potassium channels
Endoplasmic reticulum
description The voltage-dependent potassium channel Kv1.3 participates in the immune response. Kv1.3 is essential in diferent cellular functions, such as proliferation, activation and apoptosis. Because aberrant expression of Kv1.3 is linked to autoimmune diseases, fne-tuning its function is crucial for leukocyte physiology. Regulatory KCNE subunits are expressed in the immune system, and KCNE4 specifcally tightly regulates Kv1.3. KCNE4 modulates Kv1.3 currents slowing activation, accelerating inactivation and retaining the channel at the endoplasmic reticulum (ER), thereby altering its membrane localization. In addition, KCNE4 genomic variants are associated with immune pathologies. Therefore, an in-depth knowledge of KCNE4 function is extremely relevant for understanding immune system physiology. We demonstrate that KCNE4 dimerizes, which is unique among KCNE regulatory peptide family members. Furthermore, the juxtamembrane tetraleucine carboxyl-terminal domain of KCNE4 is a structural platform in which Kv1.3, Ca2+/calmodulin (CaM) and dimerizing KCNE4 compete for multiple interaction partners. CaM-dependent KCNE4 dimerization controls KCNE4 membrane targeting and modulates its interaction with Kv1.3. KCNE4, which is highly retained at the ER, contains an important ER retention motif near the tetraleucine motif. Upon escaping the ER in a CaM-dependent pattern, KCNE4 follows a COP-II-dependent forward trafcking mechanism. Therefore, CaM, an essential signaling molecule that controls the dimerization and membrane targeting of KCNE4, modulates the KCNE4-dependent regulation of Kv1.3, which in turn fne-tunes leukocyte physiology.
publishDate 2021
dc.date.none.fl_str_mv 2021
2022
2022
2022
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://hdl.handle.net/2445/186238
url https://hdl.handle.net/2445/186238
dc.language.none.fl_str_mv Inglés
language_invalid_str_mv Inglés
dc.relation.none.fl_str_mv Reproducció del document publicat a: https://doi.org/10.1038/s41598-021-93562-5
Scientific Reports, 2021, vol. 11, num. 1, p. 14046
https://doi.org/10.1038/s41598-021-93562-5
dc.rights.none.fl_str_mv cc-by (c) Roig, Sara R. et al., 2021
https://creativecommons.org/licenses/by/4.0/
info:eu-repo/semantics/openAccess
rights_invalid_str_mv cc-by (c) Roig, Sara R. et al., 2021
https://creativecommons.org/licenses/by/4.0/
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv 16 p.
application/pdf
dc.publisher.none.fl_str_mv Nature Publishing Group
publisher.none.fl_str_mv Nature Publishing Group
dc.source.none.fl_str_mv Articles publicats en revistes (Bioquímica i Biomedicina Molecular)
reponame:Recercat. Dipósit de la Recerca de Catalunya
instname:Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
instname_str Varias* (Consorci de Biblioteques Universitáries de Catalunya, Centre de Serveis Científics i Acadèmics de Catalunya)
reponame_str Recercat. Dipósit de la Recerca de Catalunya
collection Recercat. Dipósit de la Recerca de Catalunya
repository.name.fl_str_mv
repository.mail.fl_str_mv
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