STAT1 and STAT3 gain of function: clinically heterogenous immune regulatory disorders

The identification of STAT1 gain-of-function (GOF) in 2011 and STAT3 GOF in 2014 has advanced our understanding of the host immunity along the JAK/STAT pathway and allowed targeted treatment approaches. We review the clinical features and pathogenesis of STAT1 and STAT3 GOF and how this has shaped n...

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Detalles Bibliográficos
Autores: Olbrich, Peter, Freeman, Alexandra F.
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2024
País:España
Institución:Consejo Superior de Investigaciones Científicas (CSIC)
Repositorio:DIGITAL.CSIC. Repositorio Institucional del CSIC
OAI Identifier:oai:digital.csic.es:10261/386370
Acceso en línea:http://hdl.handle.net/10261/386370
https://api.elsevier.com/content/abstract/scopus_id/85208160872
Access Level:acceso abierto
Palabra clave:Immune regulatory disorders
Jak inhibitors
sTAT1 gain of function
sTAT3 gain of function
Descripción
Sumario:The identification of STAT1 gain-of-function (GOF) in 2011 and STAT3 GOF in 2014 has advanced our understanding of the host immunity along the JAK/STAT pathway and allowed targeted treatment approaches. We review the clinical features and pathogenesis of STAT1 and STAT3 GOF and how this has shaped new approaches to therapy.