Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective?
Cystic fibrosis; Multicenter study; Vitamin D
| Autores: | , , , , , |
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| Tipo de recurso: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2021 |
| País: | España |
| Institución: | Departament de Salut de la Generalitat de Catalunya (DS) |
| Repositorio: | Scientia. Dipòsit d'Informació Digital del Departament de Salut |
| OAI Identifier: | oai:scientiasalut.gencat.cat:11351/7721 |
| Acceso en línea: | https://hdl.handle.net/11351/7721 |
| Access Level: | acceso abierto |
| Palabra clave: | Avitaminosi D Fibrosi quística en infants Posologia DISEASES::Nutritional and Metabolic Diseases::Nutrition Disorders::Malnutrition::Deficiency Diseases::Avitaminosis::Vitamin D Deficiency DISEASES::Digestive System Diseases::Pancreatic Diseases::Cystic Fibrosis PHENOMENA AND PROCESSES::Physiological Phenomena::Diet, Food, and Nutrition::Nutritional Physiological Phenomena::Nutritional Requirements::Recommended Dietary Allowances ENFERMEDADES::enfermedades nutricionales y metabólicas::trastornos nutricionales::desnutrición::enfermedades carenciales::avitaminosis::deficiencia de vitamina D ENFERMEDADES::enfermedades del sistema digestivo::enfermedades pancreáticas::fibrosis quística FENÓMENOS Y PROCESOS::fenómenos fisiológicos::dieta, alimentación y nutrición::fenómenos fisiológicos nutricionales::requerimientos nutricionales::cantidad dietética recomendada |
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Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective?Mangas-Sánchez, CarmenGarriga-García, MaríaSerrano-Nieto, María JulianaGarcía Romero, RuthÁlvarez Beltrán, MarinaCrehuá-Gaudiza, ElenaAvitaminosi DFibrosi quística en infantsPosologiaDISEASES::Nutritional and Metabolic Diseases::Nutrition Disorders::Malnutrition::Deficiency Diseases::Avitaminosis::Vitamin D DeficiencyDISEASES::Digestive System Diseases::Pancreatic Diseases::Cystic FibrosisPHENOMENA AND PROCESSES::Physiological Phenomena::Diet, Food, and Nutrition::Nutritional Physiological Phenomena::Nutritional Requirements::Recommended Dietary AllowancesENFERMEDADES::enfermedades nutricionales y metabólicas::trastornos nutricionales::desnutrición::enfermedades carenciales::avitaminosis::deficiencia de vitamina DENFERMEDADES::enfermedades del sistema digestivo::enfermedades pancreáticas::fibrosis quísticaFENÓMENOS Y PROCESOS::fenómenos fisiológicos::dieta, alimentación y nutrición::fenómenos fisiológicos nutricionales::requerimientos nutricionales::cantidad dietética recomendadaCystic fibrosis; Multicenter study; Vitamin DFibrosis quística; Estudio multicéntrico; Vitamina DFibrosi quística; Estudi multicèntric; Vitamina DIntroduction: In recent years, guidelines for vitamin D supplementation have been updated and prophylactic recommended doses have been increased in patients with cystic fibrosis (CF). Objective: To evaluate safety and efficacy of these new recommendations. Results: Two cohorts of pancreatic insufficient CF patients were compared before (cohort 1: 179 patients) and after (cohort 2: 71 patients) American CF Foundation and European CF Society recommendations were published. Cohort 2 patients received higher Vitamin D doses: 1509 (1306-1711 95% CI) vs 1084 (983-1184 95% CI) IU/Day (p < 0.001), had higher 25 OH vitamin D levels: 30.6 (27.9-33.26 95% CI) vs. 27.4 (25.9-28.8 95% CI) ng/mL (p = 0.028), and had a lower prevalence of insufficient vitamin D levels (<30 ng/mL): 48% vs 65% (p = 0.011). Adjusted by confounding factors, patients in cohort 1 had a higher risk of vitamin D insufficiency: OR 2.23 (1.09-4.57 95% CI) (p = 0.028). Conclusion: After the implementation of new guidelines, CF patients received higher doses of vitamin D and a risk of vitamin D insufficiency decreased. Despite this, almost a third of CF patients still do not reach sufficient serum calcidiol levels.This research was partially funded by Fundación Ernesto Sánchez Villares and Fundación Nutrición y Crecimiento.MDPIInstitut Català de la Salut[Mangas-Sánchez C] Pediatric Gastroenterology and Nutrition Section, Hospital Central de Asturias, Oviedo, Spain. [Garriga-García M] Cystic Fibrosis Section, Hospital Ramón y Cajal, Madrid, Spain. [Serrano-Nieto MJ] Pediatric Gastroenterology and Nutrition Section, Hospital Carlos Haya, Málaga, Spain. [García-Romero R] Pediatric Gastroenterology and Nutrition Section, Hospital Miguel Servet, Zaragoza, Spain. [Álvarez-Beltrán M] Secció de Nutrició i Gastroenterologia Pediàtrica, Vall d’Hebron Hospital Universitari, Barcelona, Spain. [Crehuá-Gaudiza E] Pediatric Gastroenterology and Nutrition Section, Hospital Clínico de Valencia, Valencia, SpainVall d'Hebron Barcelona Hospital Campus202220222021info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://hdl.handle.net/11351/7721Scientiareponame:Scientia. Dipòsit d'Informació Digital del Departament de Salutinstname:Departament de Salut de la Generalitat de Catalunya (DS)InglésNutrients;13(12)https://doi.org/10.3390/nu13124413Attribution 4.0 Internationalhttp://creativecommons.org/licenses/by/4.0/info:eu-repo/semantics/openAccessoai:scientiasalut.gencat.cat:11351/77212026-06-12T09:38:37Z |
| dc.title.none.fl_str_mv |
Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective? |
| title |
Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective? |
| spellingShingle |
Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective? Mangas-Sánchez, Carmen Avitaminosi D Fibrosi quística en infants Posologia DISEASES::Nutritional and Metabolic Diseases::Nutrition Disorders::Malnutrition::Deficiency Diseases::Avitaminosis::Vitamin D Deficiency DISEASES::Digestive System Diseases::Pancreatic Diseases::Cystic Fibrosis PHENOMENA AND PROCESSES::Physiological Phenomena::Diet, Food, and Nutrition::Nutritional Physiological Phenomena::Nutritional Requirements::Recommended Dietary Allowances ENFERMEDADES::enfermedades nutricionales y metabólicas::trastornos nutricionales::desnutrición::enfermedades carenciales::avitaminosis::deficiencia de vitamina D ENFERMEDADES::enfermedades del sistema digestivo::enfermedades pancreáticas::fibrosis quística FENÓMENOS Y PROCESOS::fenómenos fisiológicos::dieta, alimentación y nutrición::fenómenos fisiológicos nutricionales::requerimientos nutricionales::cantidad dietética recomendada |
| title_short |
Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective? |
| title_full |
Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective? |
| title_fullStr |
Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective? |
| title_full_unstemmed |
Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective? |
| title_sort |
Vitamin D Status in Pediatric and Young Adult Cystic Fibrosis Patients. Are the New Recommendations Effective? |
| dc.creator.none.fl_str_mv |
Mangas-Sánchez, Carmen Garriga-García, María Serrano-Nieto, María Juliana García Romero, Ruth Álvarez Beltrán, Marina Crehuá-Gaudiza, Elena |
| author |
Mangas-Sánchez, Carmen |
| author_facet |
Mangas-Sánchez, Carmen Garriga-García, María Serrano-Nieto, María Juliana García Romero, Ruth Álvarez Beltrán, Marina Crehuá-Gaudiza, Elena |
| author_role |
author |
| author2 |
Garriga-García, María Serrano-Nieto, María Juliana García Romero, Ruth Álvarez Beltrán, Marina Crehuá-Gaudiza, Elena |
| author2_role |
author author author author author |
| dc.contributor.none.fl_str_mv |
Institut Català de la Salut [Mangas-Sánchez C] Pediatric Gastroenterology and Nutrition Section, Hospital Central de Asturias, Oviedo, Spain. [Garriga-García M] Cystic Fibrosis Section, Hospital Ramón y Cajal, Madrid, Spain. [Serrano-Nieto MJ] Pediatric Gastroenterology and Nutrition Section, Hospital Carlos Haya, Málaga, Spain. [García-Romero R] Pediatric Gastroenterology and Nutrition Section, Hospital Miguel Servet, Zaragoza, Spain. [Álvarez-Beltrán M] Secció de Nutrició i Gastroenterologia Pediàtrica, Vall d’Hebron Hospital Universitari, Barcelona, Spain. [Crehuá-Gaudiza E] Pediatric Gastroenterology and Nutrition Section, Hospital Clínico de Valencia, Valencia, Spain Vall d'Hebron Barcelona Hospital Campus |
| dc.subject.none.fl_str_mv |
Avitaminosi D Fibrosi quística en infants Posologia DISEASES::Nutritional and Metabolic Diseases::Nutrition Disorders::Malnutrition::Deficiency Diseases::Avitaminosis::Vitamin D Deficiency DISEASES::Digestive System Diseases::Pancreatic Diseases::Cystic Fibrosis PHENOMENA AND PROCESSES::Physiological Phenomena::Diet, Food, and Nutrition::Nutritional Physiological Phenomena::Nutritional Requirements::Recommended Dietary Allowances ENFERMEDADES::enfermedades nutricionales y metabólicas::trastornos nutricionales::desnutrición::enfermedades carenciales::avitaminosis::deficiencia de vitamina D ENFERMEDADES::enfermedades del sistema digestivo::enfermedades pancreáticas::fibrosis quística FENÓMENOS Y PROCESOS::fenómenos fisiológicos::dieta, alimentación y nutrición::fenómenos fisiológicos nutricionales::requerimientos nutricionales::cantidad dietética recomendada |
| topic |
Avitaminosi D Fibrosi quística en infants Posologia DISEASES::Nutritional and Metabolic Diseases::Nutrition Disorders::Malnutrition::Deficiency Diseases::Avitaminosis::Vitamin D Deficiency DISEASES::Digestive System Diseases::Pancreatic Diseases::Cystic Fibrosis PHENOMENA AND PROCESSES::Physiological Phenomena::Diet, Food, and Nutrition::Nutritional Physiological Phenomena::Nutritional Requirements::Recommended Dietary Allowances ENFERMEDADES::enfermedades nutricionales y metabólicas::trastornos nutricionales::desnutrición::enfermedades carenciales::avitaminosis::deficiencia de vitamina D ENFERMEDADES::enfermedades del sistema digestivo::enfermedades pancreáticas::fibrosis quística FENÓMENOS Y PROCESOS::fenómenos fisiológicos::dieta, alimentación y nutrición::fenómenos fisiológicos nutricionales::requerimientos nutricionales::cantidad dietética recomendada |
| description |
Cystic fibrosis; Multicenter study; Vitamin D |
| publishDate |
2021 |
| dc.date.none.fl_str_mv |
2021 2022 2022 |
| dc.type.none.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
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article |
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publishedVersion |
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https://hdl.handle.net/11351/7721 |
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https://hdl.handle.net/11351/7721 |
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Inglés |
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Inglés |
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Nutrients;13(12) https://doi.org/10.3390/nu13124413 |
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Attribution 4.0 International http://creativecommons.org/licenses/by/4.0/ info:eu-repo/semantics/openAccess |
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Attribution 4.0 International http://creativecommons.org/licenses/by/4.0/ |
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openAccess |
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application/pdf |
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MDPI |
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MDPI |
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Scientia reponame:Scientia. Dipòsit d'Informació Digital del Departament de Salut instname:Departament de Salut de la Generalitat de Catalunya (DS) |
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Departament de Salut de la Generalitat de Catalunya (DS) |
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Scientia. Dipòsit d'Informació Digital del Departament de Salut |
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15,81155 |