Pregnanetriolone in paper-borne urine for neonatal screening for 21-hydroxylase deficiency: The place of urine in neonatal screening

The standard method of primary neonatal screening for congenital adrenal hyperlasia (CAH), determination of 17-hydroxyprogesterone (17OHP) in heelprick blood, is the object of recurrent controversy because of its poor diagnostic and economic efficiency. The superior ability of urinary pregnanetriolo...

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Detalles Bibliográficos
Autor: Alonso Fernández, José R
Tipo de recurso: artículo
Fecha de publicación:2016
País:España
Institución:Servizo Galego de Saúde (SERGAS)
Repositorio:RUNA. Repositorio da Consellería de Sanidade e Sergas
OAI Identifier:oai:runa.sergas.gal:20.500.11940/9950
Acceso en línea:https://www.ncbi.nlm.nih.gov/pubmed/27570738
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4992010/
http://hdl.handle.net/20.500.11940/9950
Access Level:acceso abierto
Palabra clave:Steroids
Failure to Thrive
Neonatal Screening
Genotype
cribado neonatal
genotipo
esteroides
insuficiencia de crecimiento
Cribado neonatal
Hiperplasia adrenal congénita
Hiperplasia adrenal conxénita
Descripción
Sumario:The standard method of primary neonatal screening for congenital adrenal hyperlasia (CAH), determination of 17-hydroxyprogesterone (17OHP) in heelprick blood, is the object of recurrent controversy because of its poor diagnostic and economic efficiency. The superior ability of urinary pregnanetriolone levels to discriminate between infants with and without classical CAH has been known for some time, but has not hitherto been exploited for primary screening. Here we propose an economical neonatal CAH-screening system based on fluorimetric determination of the product of reaction between urinary pregnanetriolone and phosphoric acid.