A Further Case Supporting CCNK as a Neurodevelopmental Disease Gene.

De novo CCNK missense variant associated with mild intellectual disability, subtle dysmorphism (hypertelorism, depressed/broad nasal bridge), and ventriculomegaly. This case broadens the clinical spectrum of CCNK-related neurodevelopmental disease and supports cyclin K as a disease gene; imaging and...

ver descrição completa

Detalhes bibliográficos
Autores: Xiol C, Olival J, Martorell L, Ortigoza-Escobar JD
Tipo de documento: artigo
Estado:Versão publicada
Data de publicação:2026
País:España
Recursos:Fundació Sant Joan de Déu
Repositório:r-FSJD. Repositorio Institucional de Producción Científica de la Fundació Sant Joan de Déu
OAI Identifier:oai:fsjd.fundanetsuite.com:p29258
Acesso em linha:https://fsjd.fundanetsuite.com/Publicaciones/ProdCientif/PublicacionFrw.aspx?id=29258
Access Level:Acceso aberto
Palavra-chave:CCNK
genotype–phenotype variability
intellectual disability
ventriculomegaly
whole-exome sequencing
Descrição
Resumo:De novo CCNK missense variant associated with mild intellectual disability, subtle dysmorphism (hypertelorism, depressed/broad nasal bridge), and ventriculomegaly. This case broadens the clinical spectrum of CCNK-related neurodevelopmental disease and supports cyclin K as a disease gene; imaging and phenotype suggest a milder presentation compared with deletions.