Association of location of BRCA1 and BRCA2 mutations with benefit from olaparib and bevacizumab maintenance in high-grade ovarian cancer: phase III PAOLA-1/ENGOT-ov25 trial subgroup exploratory analysis

Background: In the phase III PAOLA-1 study, the addition of maintenance olaparib to bevacizumab in patients with newly diagnosed high-grade ovarian cancer (HGOC) resulted in prolonged progression-free survival (PFS), particularly for homologous recombination deficiency-positive tumors, including tho...

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Authors: Labidi-Galy S.I., Rodrigues M., Sandoval J.L., Kurtz J.E., Heitz F., Mosconi A.M., Romero I., Denison U., Nagao S., Vergote I., Parma G., Nøttrup T.J., Rouleau E., Garnier G., El-Balat A., Zamagni C., Martín-Lorente C., Pujade-Lauraine E., Fiévet A., Ray-Coquard I.L.
Format: article
Status:Published version
Publication Date:2023
Country:España
Institution:Institut d’Investigació Biomèdica Sant Pau (IIB Sant Pau)
Repository:r-IIB SANT PAU. Repositorio Institucional de Producción Científica del Instituto de Investigación Biomédica Sant Pau
OAI Identifier:oai:iibsantpau.fundanetsuite.com:p15662
Online Access:https://iibsantpau.fundanetsuite.com/Publicaciones/ProdCientif/PublicacionFrw.aspx?id=15662
https://www.scopus.com/inward/record.uri?eid=2-s2.0-85144784154&doi=10.1016%2fj.annonc.2022.11.003&partnerID=40&md5=053359e51411958e1f3922d15aeb6f05
Access Level:Open access
Keyword:bevacizumab
BRCA1 protein
DNA binding protein
olaparib
placebo
Rad51 protein
antineoplastic agent
BRCA1 protein, human
BRCA2 protein
BRCA2 protein, human
phthalazine derivative
adult
advanced cancer
aged
Article
cancer chemotherapy
cancer grading
cancer patient
cancer staging
carboxy terminal sequence
clinical outcome
cohort analysis
controlled study
drug response
exon
exploratory research
female
follow up
gene mutation
genetic association
genotype
hazard ratio
human
human tissue
maintenance therapy
major clinical study
middle aged
oncogene
ovary cancer
post hoc analysis
predictive value
progression free survival
protein domain
retrospective study
tumor suppressor gene
genetics
maintenance chemotherapy
mutation
ovary tumor
pathology
Antineoplastic Agents
Bevacizumab
BRCA1 Protein
BRCA2 Protein
Female
Humans
Maintenance Chemotherapy
Mutation
Ovarian Neoplasms
Phthalazines
Description
Summary:Background: In the phase III PAOLA-1 study, the addition of maintenance olaparib to bevacizumab in patients with newly diagnosed high-grade ovarian cancer (HGOC) resulted in prolonged progression-free survival (PFS), particularly for homologous recombination deficiency-positive tumors, including those with a BRCA mutation (BRCAm). The magnitude of benefit from olaparib and bevacizumab according to the location of mutation in BRCA1/BRCA2 remains to be explored. Patients and methods: Patients with advanced-stage HGOC responding after platinum-based chemotherapy + bevacizumab received maintenance therapy bevacizumab (15 mg/kg q3w for 15 months) + either olaparib (300 mg b.i.d. for 24 months) or placebo. PFS was analyzed in the subgroup of patients with BRCA1m/BRCA2m according to mutation location in the functional domains of BRCA1 [Really Interesting Gene (RING), DNA-binding domain (DBD), or C-terminal domain of BRCA1 (BRCT)] and BRCA2 [RAD51-binding domain (RAD51-BD); DBD]. Results: From 806 randomized patients, 159 harbored BRCA1m (19.7%) and 74 BRCA2m (9.2%). BRCA1m in RING, DBD, and BRCT domains was detected in 18, 40, and 33 patients, and BRCA2m in RAD51-BD and DBD in 36 and 13 patients, respectively. After a median follow-up of 25.5 months, benefit from maintenance olaparib + bevacizumab was observed irrespective of location of BRCAm. The benefit was particularly high for those with BRCA1m located in the DBD, with 24-month PFS estimated to be 89% and 15% [olaparib + bevacizumab versus placebo + bevacizumab hazard ratio = 0.08 (95% confidence interval 0.02-0.28); interaction P = 0.03]. In BRCA2m patients, 24-month PFS rates for those with mutations located in the DBD were 90% and 100% (olaparib + bevacizumab versus placebo + bevacizumab), respectively. Conclusions: Advanced-stage BRCA-mutated HGOC patients reported PFS benefit from maintenance olaparib and bevacizumab regardless of mutation location. The benefit is particularly high for patients with mutations located in the DBD of BRCA1. Mutations located in the DBD of BRCA2 are also associated with excellent outcome. © 2022 The Author(s)