Synovial chondromatosis of the knee. A rare cause of knee pain in pediatric age

Synovial osteochondromatosis consists of a synovial metaplasia which affects 1 per 100000 people. It is a very rare disease among children. It typically affects large joints of the body, especially the knee. Due to the lack of specificity of the signs and symptoms and X-Ray images, imaging tests suc...

Descripción completa

Detalles Bibliográficos
Autores: Botaya, EG, Almero, LP, Menchon, MOM, Munoz, AS, Moscardo-Navarro, A, Rey, MFM
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2020
País:España
Institución:INCLIVA
Repositorio:r-INCLIVA. Repositorio Institucional de Producción Científica de INCLIVA
OAI Identifier:oai:incliva.fundanetsuite.com:p4314
Acceso en línea:https://incliva.portalinvestigacion.com/publicaciones/4314
Access Level:acceso abierto
Palabra clave:synovial chondromatosis
metaplasia
knee
chondrosarcoma
Descripción
Sumario:Synovial osteochondromatosis consists of a synovial metaplasia which affects 1 per 100000 people. It is a very rare disease among children. It typically affects large joints of the body, especially the knee. Due to the lack of specificity of the signs and symptoms and X-Ray images, imaging tests such as nuclear magnetic resonance or computerized tomography are frequently needed for diagnosis. We report a case of a ten-year-old female patient with a six months history of pain and deformity of left patella which was diagnosed with synovial osteochondromatosis. This case highlights the importance of clinical suspicion, not only because it is an extremely rare disease in children, but also because it needs a surgical treatment as soon as possible in order to avoid consequences it might have in pediatric age, asjoint destruction or malignization to chondrosarcoma.