Regulation of respiratory complex I assembly by FMN cofactor targeting.

Respiratory complex I plays a crucial role in the mitochondrial electron transport chain and shows promise as a therapeutic target for various human diseases. While most studies focus on inhibiting complex I at the Q-site, little is known about inhibitors targeting other sites within the complex. In...

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Detalles Bibliográficos
Autores: Curtabbi, Andrea, Guaras, Adela, Cabrera-Alarcón, José Luis, Rivero, Maribel, Calvo, Enrique, Rosa-Moreno, Marina, Vazquez, Jesus, Medina, Milagros, Enriquez, Jose Antonio
Tipo de recurso: artículo
Fecha de publicación:2024
País:España
Institución:Instituto de Salud Carlos III (ISCIII)
Repositorio:Repisalud
Idioma:inglés
OAI Identifier:oai:repisalud.isciii.es:20.500.12105/19037
Acceso en línea:http://hdl.handle.net/20.500.12105/19037
Access Level:acceso abierto
Palabra clave:Electron Transport Complex I
Riboflavin
Humans
Mitochondria
Descripción
Sumario:Respiratory complex I plays a crucial role in the mitochondrial electron transport chain and shows promise as a therapeutic target for various human diseases. While most studies focus on inhibiting complex I at the Q-site, little is known about inhibitors targeting other sites within the complex. In this study, we demonstrate that diphenyleneiodonium (DPI), a N-site inhibitor, uniquely affects the stability of complex I by reacting with its flavin cofactor FMN. Treatment with DPI blocks the final stage of complex I assembly, leading to the complete and reversible degradation of complex I in different cellular models. Growing cells in medium lacking the FMN precursor riboflavin or knocking out the mitochondrial flavin carrier gene SLC25A32 results in a similar complex I degradation. Overall, our findings establish a direct connection between mitochondrial flavin homeostasis and complex I stability and assembly, paving the way for novel pharmacological strategies to regulate respiratory complex I.