A rare form of hereditary angioedema could be confused with ovarian cáncer

Hereditary angioedema (HAE) is a rare genetic disorder characterized by recurrent and circumscribed episodes of subcutaneous and submucosal edema involving different organs. Gastrointestinal involvement usually presents as abdominal pain. The presence of ascites is rare with only few cases reported...

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Detalles Bibliográficos
Autores: Melero-Cortés, Lidia María, Rosso-González, María del Rosario, Frutos-Arenas, Javier, Silvan Alfaro, José Manuel, Martínez Maestre, María Ángeles
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2021
País:España
Institución:Universidad de Sevilla (US)
Repositorio:idUS. Depósito de Investigación de la Universidad de Sevilla
OAI Identifier:oai:idus.us.es:11441/138102
Acceso en línea:https://hdl.handle.net/11441/138102
https://doi.org/10.31083/j.ejgo.2021.02.2164
Access Level:acceso abierto
Palabra clave:Hereditary angioedema
C1-inhibitor
Abdominal pain
Ascites
Ovarian edema
Descripción
Sumario:Hereditary angioedema (HAE) is a rare genetic disorder characterized by recurrent and circumscribed episodes of subcutaneous and submucosal edema involving different organs. Gastrointestinal involvement usually presents as abdominal pain. The presence of ascites is rare with only few cases reported in the literature. We report a case of HAE with ovarian edema, ascites and elevation of CA-125 which led to an initial suspicion of ovarian neoplasia. It is important for gynaecologists to be aware of HAE, as this disease can present a symptomatology similar to that described in gynaecological diseases and therefore lead to unnecessary invasive procedures and delay proper treatment.