Epigenetic inactivation of the ERK inhibitor Spry2 in B-cell diffuse lymphomas

Spry2 has been characterized as a negative regulator of the extracellular-regulated kinase (ERK) pathway. In this study we analysed whether epigenetic alterations of hSpry2 promoter occur in human lymphoid/hematopoietic malignancies. Our results revealed that hSpry2 promoter was hypermethylated in t...

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Detalles Bibliográficos
Autores: Sanchez, Agustin, Setién, F, Martinez, Natalia, Oliva-Martinez, Jose Luis, Herranz, M, Fraga, M-F, Alaminos, M, Esteller, M, Rojas-Cabañeros, Jose Maria
Tipo de recurso: artículo
Fecha de publicación:2008
País:España
Institución:Instituto de Salud Carlos III (ISCIII)
Repositorio:Repisalud
Idioma:inglés
OAI Identifier:oai:repisalud.isciii.es:20.500.12105/26130
Acceso en línea:https://hdl.handle.net/20.500.12105/26130
Access Level:acceso abierto
Palabra clave:hSpry2
Epigenetic
Lymphomas
B cells
Suppressor gene
Animals
Epigenesis, Genetic
Extracellular Signal-Regulated MAP Kinases
Humans
Intracellular Signaling Peptides and Proteins
Lymphoma, B-Cell
Membrane Proteins
Mice
Mice, Nude
Protein Kinase Inhibitors
Tetradecanoylphorbol Acetate
Descripción
Sumario:Spry2 has been characterized as a negative regulator of the extracellular-regulated kinase (ERK) pathway. In this study we analysed whether epigenetic alterations of hSpry2 promoter occur in human lymphoid/hematopoietic malignancies. Our results revealed that hSpry2 promoter was hypermethylated in the HT cell line derived from a B-cell diffuse lymphoma, which correlated with decreased hSpry2 expression. We detected deregulation of the ERK pathway in these cells, but not in other blood cell lines expressing hSpry2. In addition, the ectopic overexpression of hSpry2 in HT cells drastically reduced the activation of ERK upon phorbol 12-myristate-13-acetate stimulation. Nude mice inoculated with HT mock cells developed tumors seven times larger than those from HT-hSpry2-transfected cells. We found hypermethylation of hSpry2 promoter in 37% (26 cases out of 71) of primary tumors from patients with B-cell diffuse lymphoma but none in normal B lymphocytes from 37 healthy individuals. Finally, we detected that hSpry2 promoter hypermethylation was associated with a significant decrease in the 5-year survival rate. These data suggest that hSpry2 could be important in lymphoid malignancies.