Comprehensive analysis and insights gained from long-term experience of the Spanish DILI Registry

Background & Aims: Prospective drug-induced liver injury (DILI) registries are important sources of information on idiosyncratic DILI. We aimed to present a comprehensive analysis of 843 patients with DILI enrolled into the Spanish DILI Registry over a 20-year time period. Methods: Cases were id...

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Detalhes bibliográficos
Autores: Stephens, Camilla|||0000-0002-0796-9610, Robles Díaz, Mercedes|||0000-0002-2365-2787, Medina-Cáliz, Inmaculada|||0000-0003-0471-6658, Garcia-Cortes, Miren|||0000-0003-0410-8273, Ortega-Alonso, Aida|||0000-0002-8999-4093, Sanabria-Cabrera, Judith|||0000-0002-7769-7008, Gonzalez-Jimenez, Andrés, Alvarez-Alvarez, Ismael, Slim, Mahmoud|||0000-0003-2455-1432, Jimenez-Perez, Miguel, Gonzalez-Grande, Rocio, Fernández, M.Carmen, Casado, Marta, Soriano, German|||0000-0002-9267-6811, Roman, Eva|||0000-0001-9084-8555, Hallal, Hacibe, Romero-Gómez, Manuel|||0000-0001-8494-8947, Castiella, Agustin, Conde, Isabel|||0000-0001-7863-2233, Prieto, Martin, Moreno-Planas, Jose Maria, Giraldez, Alvaro, Moreno-Sanfiel, J.Miguel, Kaplowitz, Neil, Lucena, M. Isabel|||0000-0001-9586-4896, Andrade, Raúl J., Cortés, M.G., Pinazo, Jose, García Muñoz, B., Alcántara, Ramiro, Hernández, Andrés, Escaño, M.D.García, del Campo, E., González-Jiménez, A., Sanjuán Jiménez, Rocío, Cueto, Alejandro, Bonilla, Elvira, Di Zeo, D., Niu, H., Villanueva-Paz, Marina|||0000-0003-4728-201X, Papineau, A., Pérez Hernández, Manuel José, González-Grande, Rocío|||0000-0002-7691-5755, López Ortega, S., Santaella, I., Ocaña, A., Palomino, P., Fernández, Maria Carmen, Peláez, Gloria, Porcel, A., Casado, M., González Sánchez, Mara, Millán-Domínguez, R., Fombuena, Blanca, Gallego, Rocío, Ampuero, Javier|||0000-0002-8332-2122, Del Campo, José Antonio, Calle-Sanz, R., Rojas, Lourdes, Rojas, Ángela|||0000-0003-0853-4800, Gil Gómez, Alexandra, Vilar, Eduardo, Guarner, Carlos|||0000-0001-5957-9481, Quijada-Manuitt, María Ángeles|||0000-0002-9624-0177, Antonijoan Arbós, Rosa Ma (Rosa María)|||0000-0002-7099-5125, Sánchez Delgado, Jordi|||0000-0002-5217-6492, Vergara Gómez, Mariano, Hallal, H., García Oltra, Ester, Titos Arcos, J.C., Pérez Martínez, Alfonso, Sánchez Cobarro, C., Egea Caparrós, J.M., Zapata, Eva María, Arenas, Juan Ignacio, Gómez García, Alexandra, Esandi, F.J., Blanco, Sonia, Martínez Odriozola, Pedro, Crespo García, Javier|||0000-0001-8248-0172, Iruzubieta, Paula|||0000-0001-9476-1801, Cabezas González, Joaquín|||0000-0003-0012-484X, Giráldez Gallego, Álvaro, Rodríguez Seguel, Elisa, Cuaresma, María, González-Gallego, Javier|||0000-0002-4386-9342, Jorquera, Francisco|||0000-0002-1799-2881, Sánchez Campos, S., Otazua, Pedro, de Juan Gómez, A., Salmerón, Javier, Gila, Ana, Quiles, Rosa, González, José Manuel, Lorenzo, Sara, Prieto, Martín, Conde Amiel, I., Berenguer, Marina|||0000-0001-9246-4264, García-Eliz, María, Primo, Joaquín, Molés, José Ramón, Garayoa, Ana, Carrascosa, Miguel, Gómez Domínguez, Elena, Cuevas, L., Farré Albaladejo, Magí|||0000-0001-8338-7543, Montané Esteva, Eva|||0000-0002-1691-7652, Barriocanal, Ana María|||0000-0002-4159-519X, Arellano, Ana Lucía|||0000-0001-8601-3504, Sanz, Yolanda, Morillas Cunill, Rosa Ma|||0000-0001-9117-5049, Sala, Margarita, Masnou Ridaura, H., Bruguera, Miquel, Ginès, Pere|||0000-0003-4657-4504, Lens, Sabela|||0000-0003-4900-411X, Mariño, Zoe|||0000-0001-6321-9534, Hernández Guerra, Manuel, Moreno Sanfiel, J.M., Fernández del Campo, C.Boada, Tejedor, Martián, González Ferrer, Ruth, Fernández, Conrado, Fernández Gil, Marta, Montero, José Luís, de la Mata, Manuel, Fuentes Olmo, J., Fernández Bonilla, E.M., Moreno, Julián M., Martínez-Ródenas, Ponciano, Gómez Garrido, M., Oliva, C., Rendón, Paloma|||0000-0002-6521-3766, García Samaniego, Javier, Madejón, Antonio, Calleja, Jose Luis|||0000-0002-2265-6591, Martínez Porras, J.L., Cabriada, José Luis|||0000-0002-3068-5659, Pérez-Moreno, José Manuel, Lara, Carmen
Formato: artículo
Fecha de publicación:2021
País:España
Recursos:Universitat Autònoma de Barcelona
Repositorio:Dipòsit Digital de Documents de la UAB
Idioma:inglés
OAI Identifier:oai:ddd.uab.cat:271904
Acesso em linha:https://ddd.uab.cat/record/271904
https://dx.doi.org/urn:doi:10.1016/j.jhep.2021.01.029
Access Level:acceso abierto
Palavra-chave:Hepatotoxicity
DILI
Epidemiology
Liver-related death
Causative agents
Outcome
Risk factors
Therapy in DILI
Drug-induced autoimmune hepatitis
id ES_468427dfe1eff32ca9ceec6e90fed8fe
oai_identifier_str oai:ddd.uab.cat:271904
network_acronym_str ES
network_name_str España
repository_id_str
dc.title.none.fl_str_mv Comprehensive analysis and insights gained from long-term experience of the Spanish DILI Registry
title Comprehensive analysis and insights gained from long-term experience of the Spanish DILI Registry
spellingShingle Comprehensive analysis and insights gained from long-term experience of the Spanish DILI Registry
Stephens, Camilla|||0000-0002-0796-9610
Hepatotoxicity
DILI
Epidemiology
Liver-related death
Causative agents
Outcome
Risk factors
Therapy in DILI
Drug-induced autoimmune hepatitis
title_short Comprehensive analysis and insights gained from long-term experience of the Spanish DILI Registry
title_full Comprehensive analysis and insights gained from long-term experience of the Spanish DILI Registry
title_fullStr Comprehensive analysis and insights gained from long-term experience of the Spanish DILI Registry
title_full_unstemmed Comprehensive analysis and insights gained from long-term experience of the Spanish DILI Registry
title_sort Comprehensive analysis and insights gained from long-term experience of the Spanish DILI Registry
dc.creator.none.fl_str_mv Stephens, Camilla|||0000-0002-0796-9610
Robles Díaz, Mercedes|||0000-0002-2365-2787
Medina-Cáliz, Inmaculada|||0000-0003-0471-6658
Garcia-Cortes, Miren|||0000-0003-0410-8273
Ortega-Alonso, Aida|||0000-0002-8999-4093
Sanabria-Cabrera, Judith|||0000-0002-7769-7008
Gonzalez-Jimenez, Andrés
Alvarez-Alvarez, Ismael
Slim, Mahmoud|||0000-0003-2455-1432
Jimenez-Perez, Miguel
Gonzalez-Grande, Rocio
Fernández, M.Carmen
Casado, Marta
Soriano, German|||0000-0002-9267-6811
Roman, Eva|||0000-0001-9084-8555
Hallal, Hacibe
Romero-Gómez, Manuel|||0000-0001-8494-8947
Castiella, Agustin
Conde, Isabel|||0000-0001-7863-2233
Prieto, Martin
Moreno-Planas, Jose Maria
Giraldez, Alvaro
Moreno-Sanfiel, J.Miguel
Kaplowitz, Neil
Lucena, M. Isabel|||0000-0001-9586-4896
Andrade, Raúl J.
Cortés, M.G.
Pinazo, Jose
García Muñoz, B.
Alcántara, Ramiro
Hernández, Andrés
Escaño, M.D.García
del Campo, E.
González-Jiménez, A.
Sanjuán Jiménez, Rocío
Cueto, Alejandro
Bonilla, Elvira
Di Zeo, D.
Niu, H.
Villanueva-Paz, Marina|||0000-0003-4728-201X
Papineau, A.
Pérez Hernández, Manuel José
González-Grande, Rocío|||0000-0002-7691-5755
López Ortega, S.
Santaella, I.
Ocaña, A.
Palomino, P.
Fernández, Maria Carmen
Peláez, Gloria
Porcel, A.
Casado, M.
González Sánchez, Mara
Millán-Domínguez, R.
Fombuena, Blanca
Gallego, Rocío
Ampuero, Javier|||0000-0002-8332-2122
Del Campo, José Antonio
Calle-Sanz, R.
Rojas, Lourdes
Rojas, Ángela|||0000-0003-0853-4800
Gil Gómez, Alexandra
Vilar, Eduardo
Guarner, Carlos|||0000-0001-5957-9481
Quijada-Manuitt, María Ángeles|||0000-0002-9624-0177
Antonijoan Arbós, Rosa Ma (Rosa María)|||0000-0002-7099-5125
Sánchez Delgado, Jordi|||0000-0002-5217-6492
Vergara Gómez, Mariano
Hallal, H.
García Oltra, Ester
Titos Arcos, J.C.
Pérez Martínez, Alfonso
Sánchez Cobarro, C.
Egea Caparrós, J.M.
Zapata, Eva María
Arenas, Juan Ignacio
Gómez García, Alexandra
Esandi, F.J.
Blanco, Sonia
Martínez Odriozola, Pedro
Crespo García, Javier|||0000-0001-8248-0172
Iruzubieta, Paula|||0000-0001-9476-1801
Cabezas González, Joaquín|||0000-0003-0012-484X
Giráldez Gallego, Álvaro
Rodríguez Seguel, Elisa
Cuaresma, María
González-Gallego, Javier|||0000-0002-4386-9342
Jorquera, Francisco|||0000-0002-1799-2881
Sánchez Campos, S.
Otazua, Pedro
de Juan Gómez, A.
Salmerón, Javier
Gila, Ana
Quiles, Rosa
González, José Manuel
Lorenzo, Sara
Prieto, Martín
Conde Amiel, I.
Berenguer, Marina|||0000-0001-9246-4264
García-Eliz, María
Primo, Joaquín
Molés, José Ramón
Garayoa, Ana
Carrascosa, Miguel
Gómez Domínguez, Elena
Cuevas, L.
Farré Albaladejo, Magí|||0000-0001-8338-7543
Montané Esteva, Eva|||0000-0002-1691-7652
Barriocanal, Ana María|||0000-0002-4159-519X
Arellano, Ana Lucía|||0000-0001-8601-3504
Sanz, Yolanda
Morillas Cunill, Rosa Ma|||0000-0001-9117-5049
Sala, Margarita
Masnou Ridaura, H.
Bruguera, Miquel
Ginès, Pere|||0000-0003-4657-4504
Lens, Sabela|||0000-0003-4900-411X
Mariño, Zoe|||0000-0001-6321-9534
Hernández Guerra, Manuel
Moreno Sanfiel, J.M.
Fernández del Campo, C.Boada
Tejedor, Martián
González Ferrer, Ruth
Fernández, Conrado
Fernández Gil, Marta
Montero, José Luís
de la Mata, Manuel
Fuentes Olmo, J.
Fernández Bonilla, E.M.
Moreno, Julián M.
Martínez-Ródenas, Ponciano
Gómez Garrido, M.
Oliva, C.
Rendón, Paloma|||0000-0002-6521-3766
García Samaniego, Javier
Madejón, Antonio
Calleja, Jose Luis|||0000-0002-2265-6591
Martínez Porras, J.L.
Cabriada, José Luis|||0000-0002-3068-5659
Pérez-Moreno, José Manuel
Lara, Carmen
author Stephens, Camilla|||0000-0002-0796-9610
author_facet Stephens, Camilla|||0000-0002-0796-9610
Robles Díaz, Mercedes|||0000-0002-2365-2787
Medina-Cáliz, Inmaculada|||0000-0003-0471-6658
Garcia-Cortes, Miren|||0000-0003-0410-8273
Ortega-Alonso, Aida|||0000-0002-8999-4093
Sanabria-Cabrera, Judith|||0000-0002-7769-7008
Gonzalez-Jimenez, Andrés
Alvarez-Alvarez, Ismael
Slim, Mahmoud|||0000-0003-2455-1432
Jimenez-Perez, Miguel
Gonzalez-Grande, Rocio
Fernández, M.Carmen
Casado, Marta
Soriano, German|||0000-0002-9267-6811
Roman, Eva|||0000-0001-9084-8555
Hallal, Hacibe
Romero-Gómez, Manuel|||0000-0001-8494-8947
Castiella, Agustin
Conde, Isabel|||0000-0001-7863-2233
Prieto, Martin
Moreno-Planas, Jose Maria
Giraldez, Alvaro
Moreno-Sanfiel, J.Miguel
Kaplowitz, Neil
Lucena, M. Isabel|||0000-0001-9586-4896
Andrade, Raúl J.
Cortés, M.G.
Pinazo, Jose
García Muñoz, B.
Alcántara, Ramiro
Hernández, Andrés
Escaño, M.D.García
del Campo, E.
González-Jiménez, A.
Sanjuán Jiménez, Rocío
Cueto, Alejandro
Bonilla, Elvira
Di Zeo, D.
Niu, H.
Villanueva-Paz, Marina|||0000-0003-4728-201X
Papineau, A.
Pérez Hernández, Manuel José
González-Grande, Rocío|||0000-0002-7691-5755
López Ortega, S.
Santaella, I.
Ocaña, A.
Palomino, P.
Fernández, Maria Carmen
Peláez, Gloria
Porcel, A.
Casado, M.
González Sánchez, Mara
Millán-Domínguez, R.
Fombuena, Blanca
Gallego, Rocío
Ampuero, Javier|||0000-0002-8332-2122
Del Campo, José Antonio
Calle-Sanz, R.
Rojas, Lourdes
Rojas, Ángela|||0000-0003-0853-4800
Gil Gómez, Alexandra
Vilar, Eduardo
Guarner, Carlos|||0000-0001-5957-9481
Quijada-Manuitt, María Ángeles|||0000-0002-9624-0177
Antonijoan Arbós, Rosa Ma (Rosa María)|||0000-0002-7099-5125
Sánchez Delgado, Jordi|||0000-0002-5217-6492
Vergara Gómez, Mariano
Hallal, H.
García Oltra, Ester
Titos Arcos, J.C.
Pérez Martínez, Alfonso
Sánchez Cobarro, C.
Egea Caparrós, J.M.
Zapata, Eva María
Arenas, Juan Ignacio
Gómez García, Alexandra
Esandi, F.J.
Blanco, Sonia
Martínez Odriozola, Pedro
Crespo García, Javier|||0000-0001-8248-0172
Iruzubieta, Paula|||0000-0001-9476-1801
Cabezas González, Joaquín|||0000-0003-0012-484X
Giráldez Gallego, Álvaro
Rodríguez Seguel, Elisa
Cuaresma, María
González-Gallego, Javier|||0000-0002-4386-9342
Jorquera, Francisco|||0000-0002-1799-2881
Sánchez Campos, S.
Otazua, Pedro
de Juan Gómez, A.
Salmerón, Javier
Gila, Ana
Quiles, Rosa
González, José Manuel
Lorenzo, Sara
Prieto, Martín
Conde Amiel, I.
Berenguer, Marina|||0000-0001-9246-4264
García-Eliz, María
Primo, Joaquín
Molés, José Ramón
Garayoa, Ana
Carrascosa, Miguel
Gómez Domínguez, Elena
Cuevas, L.
Farré Albaladejo, Magí|||0000-0001-8338-7543
Montané Esteva, Eva|||0000-0002-1691-7652
Barriocanal, Ana María|||0000-0002-4159-519X
Arellano, Ana Lucía|||0000-0001-8601-3504
Sanz, Yolanda
Morillas Cunill, Rosa Ma|||0000-0001-9117-5049
Sala, Margarita
Masnou Ridaura, H.
Bruguera, Miquel
Ginès, Pere|||0000-0003-4657-4504
Lens, Sabela|||0000-0003-4900-411X
Mariño, Zoe|||0000-0001-6321-9534
Hernández Guerra, Manuel
Moreno Sanfiel, J.M.
Fernández del Campo, C.Boada
Tejedor, Martián
González Ferrer, Ruth
Fernández, Conrado
Fernández Gil, Marta
Montero, José Luís
de la Mata, Manuel
Fuentes Olmo, J.
Fernández Bonilla, E.M.
Moreno, Julián M.
Martínez-Ródenas, Ponciano
Gómez Garrido, M.
Oliva, C.
Rendón, Paloma|||0000-0002-6521-3766
García Samaniego, Javier
Madejón, Antonio
Calleja, Jose Luis|||0000-0002-2265-6591
Martínez Porras, J.L.
Cabriada, José Luis|||0000-0002-3068-5659
Pérez-Moreno, José Manuel
Lara, Carmen
author_role author
author2 Robles Díaz, Mercedes|||0000-0002-2365-2787
Medina-Cáliz, Inmaculada|||0000-0003-0471-6658
Garcia-Cortes, Miren|||0000-0003-0410-8273
Ortega-Alonso, Aida|||0000-0002-8999-4093
Sanabria-Cabrera, Judith|||0000-0002-7769-7008
Gonzalez-Jimenez, Andrés
Alvarez-Alvarez, Ismael
Slim, Mahmoud|||0000-0003-2455-1432
Jimenez-Perez, Miguel
Gonzalez-Grande, Rocio
Fernández, M.Carmen
Casado, Marta
Soriano, German|||0000-0002-9267-6811
Roman, Eva|||0000-0001-9084-8555
Hallal, Hacibe
Romero-Gómez, Manuel|||0000-0001-8494-8947
Castiella, Agustin
Conde, Isabel|||0000-0001-7863-2233
Prieto, Martin
Moreno-Planas, Jose Maria
Giraldez, Alvaro
Moreno-Sanfiel, J.Miguel
Kaplowitz, Neil
Lucena, M. Isabel|||0000-0001-9586-4896
Andrade, Raúl J.
Cortés, M.G.
Pinazo, Jose
García Muñoz, B.
Alcántara, Ramiro
Hernández, Andrés
Escaño, M.D.García
del Campo, E.
González-Jiménez, A.
Sanjuán Jiménez, Rocío
Cueto, Alejandro
Bonilla, Elvira
Di Zeo, D.
Niu, H.
Villanueva-Paz, Marina|||0000-0003-4728-201X
Papineau, A.
Pérez Hernández, Manuel José
González-Grande, Rocío|||0000-0002-7691-5755
López Ortega, S.
Santaella, I.
Ocaña, A.
Palomino, P.
Fernández, Maria Carmen
Peláez, Gloria
Porcel, A.
Casado, M.
González Sánchez, Mara
Millán-Domínguez, R.
Fombuena, Blanca
Gallego, Rocío
Ampuero, Javier|||0000-0002-8332-2122
Del Campo, José Antonio
Calle-Sanz, R.
Rojas, Lourdes
Rojas, Ángela|||0000-0003-0853-4800
Gil Gómez, Alexandra
Vilar, Eduardo
Guarner, Carlos|||0000-0001-5957-9481
Quijada-Manuitt, María Ángeles|||0000-0002-9624-0177
Antonijoan Arbós, Rosa Ma (Rosa María)|||0000-0002-7099-5125
Sánchez Delgado, Jordi|||0000-0002-5217-6492
Vergara Gómez, Mariano
Hallal, H.
García Oltra, Ester
Titos Arcos, J.C.
Pérez Martínez, Alfonso
Sánchez Cobarro, C.
Egea Caparrós, J.M.
Zapata, Eva María
Arenas, Juan Ignacio
Gómez García, Alexandra
Esandi, F.J.
Blanco, Sonia
Martínez Odriozola, Pedro
Crespo García, Javier|||0000-0001-8248-0172
Iruzubieta, Paula|||0000-0001-9476-1801
Cabezas González, Joaquín|||0000-0003-0012-484X
Giráldez Gallego, Álvaro
Rodríguez Seguel, Elisa
Cuaresma, María
González-Gallego, Javier|||0000-0002-4386-9342
Jorquera, Francisco|||0000-0002-1799-2881
Sánchez Campos, S.
Otazua, Pedro
de Juan Gómez, A.
Salmerón, Javier
Gila, Ana
Quiles, Rosa
González, José Manuel
Lorenzo, Sara
Prieto, Martín
Conde Amiel, I.
Berenguer, Marina|||0000-0001-9246-4264
García-Eliz, María
Primo, Joaquín
Molés, José Ramón
Garayoa, Ana
Carrascosa, Miguel
Gómez Domínguez, Elena
Cuevas, L.
Farré Albaladejo, Magí|||0000-0001-8338-7543
Montané Esteva, Eva|||0000-0002-1691-7652
Barriocanal, Ana María|||0000-0002-4159-519X
Arellano, Ana Lucía|||0000-0001-8601-3504
Sanz, Yolanda
Morillas Cunill, Rosa Ma|||0000-0001-9117-5049
Sala, Margarita
Masnou Ridaura, H.
Bruguera, Miquel
Ginès, Pere|||0000-0003-4657-4504
Lens, Sabela|||0000-0003-4900-411X
Mariño, Zoe|||0000-0001-6321-9534
Hernández Guerra, Manuel
Moreno Sanfiel, J.M.
Fernández del Campo, C.Boada
Tejedor, Martián
González Ferrer, Ruth
Fernández, Conrado
Fernández Gil, Marta
Montero, José Luís
de la Mata, Manuel
Fuentes Olmo, J.
Fernández Bonilla, E.M.
Moreno, Julián M.
Martínez-Ródenas, Ponciano
Gómez Garrido, M.
Oliva, C.
Rendón, Paloma|||0000-0002-6521-3766
García Samaniego, Javier
Madejón, Antonio
Calleja, Jose Luis|||0000-0002-2265-6591
Martínez Porras, J.L.
Cabriada, José Luis|||0000-0002-3068-5659
Pérez-Moreno, José Manuel
Lara, Carmen
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dc.contributor.none.fl_str_mv Universitat Autònoma de Barcelona
dc.subject.none.fl_str_mv Hepatotoxicity
DILI
Epidemiology
Liver-related death
Causative agents
Outcome
Risk factors
Therapy in DILI
Drug-induced autoimmune hepatitis
topic Hepatotoxicity
DILI
Epidemiology
Liver-related death
Causative agents
Outcome
Risk factors
Therapy in DILI
Drug-induced autoimmune hepatitis
description Background & Aims: Prospective drug-induced liver injury (DILI) registries are important sources of information on idiosyncratic DILI. We aimed to present a comprehensive analysis of 843 patients with DILI enrolled into the Spanish DILI Registry over a 20-year time period. Methods: Cases were identified, diagnosed and followed prospectively. Clinical features, drug information and outcome data were collected. Results: A total of 843 patients, with a mean age of 54 years (48% females), were enrolled up to 2018. Hepatocellular injury was associated with younger age (adjusted odds ratio [aOR] per year 0.983; 95% CI 0.974-0.991) and lower platelet count (aOR per unit 0.996; 95% CI 0.994-0.998). Anti-infectives were the most common causative drug class (40%). Liver-related mortality was more frequent in patients with hepatocellular damage aged ≥65 years (p = 0.0083) and in patients with underlying liver disease (p = 0.0221). Independent predictors of liver-related death/transplantation included nR-based hepatocellular injury, female sex, higher onset aspartate aminotransferase (AST) and bilirubin values. nR-based hepatocellular injury was not associated with 6-month overall mortality, for which comorbidity burden played a more important role. The prognostic capacity of Hy's law varied between causative agents. Empirical therapy (corticosteroids, ursodeoxycholic acid and MARS) was prescribed to 20% of patients. Drug-induced autoimmune hepatitis patients (26 cases) were mainly females (62%) with hepatocellular damage (92%), who more frequently received immunosuppressive therapy (58%). Conclusions: AST elevation at onset is a strong predictor of poor outcome and should be routinely assessed in DILI evaluation. Mortality is higher in older patients with hepatocellular damage and patients with underlying hepatic conditions. The Spanish DILI Registry is a valuable tool in the identification of causative drugs, clinical signatures and prognostic risk factors in DILI and can aid physicians in DILI characterisation and management. Lay summary: Clinical information on drug-induced liver injury (DILI) collected from enrolled patients in the Spanish DILI Registry can guide physicians in the decision-making process. We have found that older patients with hepatocellular type liver injury and patients with additional liver conditions are at a higher risk of mortality. The type of liver injury, patient sex and analytical values of aspartate aminotransferase and total bilirubin can also help predict clinical outcomes.
publishDate 2021
dc.date.none.fl_str_mv 2
2021-01-01
2021
2021-01-01
dc.type.none.fl_str_mv Article
http://purl.org/coar/resource_type/c_6501
VoR
http://purl.org/coar/version/c_970fb48d4fbd8a85
dc.type.openaire.fl_str_mv info:eu-repo/semantics/article
format article
dc.identifier.none.fl_str_mv https://ddd.uab.cat/record/271904
https://dx.doi.org/urn:doi:10.1016/j.jhep.2021.01.029
url https://ddd.uab.cat/record/271904
https://dx.doi.org/urn:doi:10.1016/j.jhep.2021.01.029
dc.language.none.fl_str_mv Inglés
eng
language_invalid_str_mv Inglés
language eng
dc.relation.none.fl_str_mv Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI19/00883
Ministerio de Economía y Competitividad https://doi.org/10.13039/501100003329 PI16/01748
Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI18/00901
Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI18/01804
Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI-0285-2016
Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI-0274-2016
Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI-0310-2018
Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PT17/0017/0020
Ministerio de Economía y Competitividad https://doi.org/10.13039/501100003329 JR16/00015
Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 B-0002-2019
Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 CM17/00243
dc.rights.none.fl_str_mv open access
http://purl.org/coar/access_right/c_abf2
https://creativecommons.org/licenses/by-nc-nd/4.0/
dc.rights.openaire.fl_str_mv info:eu-repo/semantics/openAccess
rights_invalid_str_mv open access
http://purl.org/coar/access_right/c_abf2
https://creativecommons.org/licenses/by-nc-nd/4.0/
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.source.none.fl_str_mv reponame:Dipòsit Digital de Documents de la UAB
instname:Universitat Autònoma de Barcelona
instname_str Universitat Autònoma de Barcelona
reponame_str Dipòsit Digital de Documents de la UAB
collection Dipòsit Digital de Documents de la UAB
repository.name.fl_str_mv
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spelling Comprehensive analysis and insights gained from long-term experience of the Spanish DILI RegistryStephens, Camilla|||0000-0002-0796-9610Robles Díaz, Mercedes|||0000-0002-2365-2787Medina-Cáliz, Inmaculada|||0000-0003-0471-6658Garcia-Cortes, Miren|||0000-0003-0410-8273Ortega-Alonso, Aida|||0000-0002-8999-4093Sanabria-Cabrera, Judith|||0000-0002-7769-7008Gonzalez-Jimenez, AndrésAlvarez-Alvarez, IsmaelSlim, Mahmoud|||0000-0003-2455-1432Jimenez-Perez, MiguelGonzalez-Grande, RocioFernández, M.CarmenCasado, MartaSoriano, German|||0000-0002-9267-6811Roman, Eva|||0000-0001-9084-8555Hallal, HacibeRomero-Gómez, Manuel|||0000-0001-8494-8947Castiella, AgustinConde, Isabel|||0000-0001-7863-2233Prieto, MartinMoreno-Planas, Jose MariaGiraldez, AlvaroMoreno-Sanfiel, J.MiguelKaplowitz, NeilLucena, M. Isabel|||0000-0001-9586-4896Andrade, Raúl J.Cortés, M.G.Pinazo, JoseGarcía Muñoz, B.Alcántara, RamiroHernández, AndrésEscaño, M.D.Garcíadel Campo, E.González-Jiménez, A.Sanjuán Jiménez, RocíoCueto, AlejandroBonilla, ElviraDi Zeo, D.Niu, H.Villanueva-Paz, Marina|||0000-0003-4728-201XPapineau, A.Pérez Hernández, Manuel JoséGonzález-Grande, Rocío|||0000-0002-7691-5755López Ortega, S.Santaella, I.Ocaña, A.Palomino, P.Fernández, Maria CarmenPeláez, GloriaPorcel, A.Casado, M.González Sánchez, MaraMillán-Domínguez, R.Fombuena, BlancaGallego, RocíoAmpuero, Javier|||0000-0002-8332-2122Del Campo, José AntonioCalle-Sanz, R.Rojas, LourdesRojas, Ángela|||0000-0003-0853-4800Gil Gómez, AlexandraVilar, EduardoGuarner, Carlos|||0000-0001-5957-9481Quijada-Manuitt, María Ángeles|||0000-0002-9624-0177Antonijoan Arbós, Rosa Ma (Rosa María)|||0000-0002-7099-5125Sánchez Delgado, Jordi|||0000-0002-5217-6492Vergara Gómez, MarianoHallal, H.García Oltra, EsterTitos Arcos, J.C.Pérez Martínez, AlfonsoSánchez Cobarro, C.Egea Caparrós, J.M.Zapata, Eva MaríaArenas, Juan IgnacioGómez García, AlexandraEsandi, F.J.Blanco, SoniaMartínez Odriozola, PedroCrespo García, Javier|||0000-0001-8248-0172Iruzubieta, Paula|||0000-0001-9476-1801Cabezas González, Joaquín|||0000-0003-0012-484XGiráldez Gallego, ÁlvaroRodríguez Seguel, ElisaCuaresma, MaríaGonzález-Gallego, Javier|||0000-0002-4386-9342Jorquera, Francisco|||0000-0002-1799-2881Sánchez Campos, S.Otazua, Pedrode Juan Gómez, A.Salmerón, JavierGila, AnaQuiles, RosaGonzález, José ManuelLorenzo, SaraPrieto, MartínConde Amiel, I.Berenguer, Marina|||0000-0001-9246-4264García-Eliz, MaríaPrimo, JoaquínMolés, José RamónGarayoa, AnaCarrascosa, MiguelGómez Domínguez, ElenaCuevas, L.Farré Albaladejo, Magí|||0000-0001-8338-7543Montané Esteva, Eva|||0000-0002-1691-7652Barriocanal, Ana María|||0000-0002-4159-519XArellano, Ana Lucía|||0000-0001-8601-3504Sanz, YolandaMorillas Cunill, Rosa Ma|||0000-0001-9117-5049Sala, MargaritaMasnou Ridaura, H.Bruguera, MiquelGinès, Pere|||0000-0003-4657-4504Lens, Sabela|||0000-0003-4900-411XMariño, Zoe|||0000-0001-6321-9534Hernández Guerra, ManuelMoreno Sanfiel, J.M.Fernández del Campo, C.BoadaTejedor, MartiánGonzález Ferrer, RuthFernández, ConradoFernández Gil, MartaMontero, José Luísde la Mata, ManuelFuentes Olmo, J.Fernández Bonilla, E.M.Moreno, Julián M.Martínez-Ródenas, PoncianoGómez Garrido, M.Oliva, C.Rendón, Paloma|||0000-0002-6521-3766García Samaniego, JavierMadejón, AntonioCalleja, Jose Luis|||0000-0002-2265-6591Martínez Porras, J.L.Cabriada, José Luis|||0000-0002-3068-5659Pérez-Moreno, José ManuelLara, CarmenHepatotoxicityDILIEpidemiologyLiver-related deathCausative agentsOutcomeRisk factorsTherapy in DILIDrug-induced autoimmune hepatitisBackground & Aims: Prospective drug-induced liver injury (DILI) registries are important sources of information on idiosyncratic DILI. We aimed to present a comprehensive analysis of 843 patients with DILI enrolled into the Spanish DILI Registry over a 20-year time period. Methods: Cases were identified, diagnosed and followed prospectively. Clinical features, drug information and outcome data were collected. Results: A total of 843 patients, with a mean age of 54 years (48% females), were enrolled up to 2018. Hepatocellular injury was associated with younger age (adjusted odds ratio [aOR] per year 0.983; 95% CI 0.974-0.991) and lower platelet count (aOR per unit 0.996; 95% CI 0.994-0.998). Anti-infectives were the most common causative drug class (40%). Liver-related mortality was more frequent in patients with hepatocellular damage aged ≥65 years (p = 0.0083) and in patients with underlying liver disease (p = 0.0221). Independent predictors of liver-related death/transplantation included nR-based hepatocellular injury, female sex, higher onset aspartate aminotransferase (AST) and bilirubin values. nR-based hepatocellular injury was not associated with 6-month overall mortality, for which comorbidity burden played a more important role. The prognostic capacity of Hy's law varied between causative agents. Empirical therapy (corticosteroids, ursodeoxycholic acid and MARS) was prescribed to 20% of patients. Drug-induced autoimmune hepatitis patients (26 cases) were mainly females (62%) with hepatocellular damage (92%), who more frequently received immunosuppressive therapy (58%). Conclusions: AST elevation at onset is a strong predictor of poor outcome and should be routinely assessed in DILI evaluation. Mortality is higher in older patients with hepatocellular damage and patients with underlying hepatic conditions. The Spanish DILI Registry is a valuable tool in the identification of causative drugs, clinical signatures and prognostic risk factors in DILI and can aid physicians in DILI characterisation and management. Lay summary: Clinical information on drug-induced liver injury (DILI) collected from enrolled patients in the Spanish DILI Registry can guide physicians in the decision-making process. We have found that older patients with hepatocellular type liver injury and patients with additional liver conditions are at a higher risk of mortality. The type of liver injury, patient sex and analytical values of aspartate aminotransferase and total bilirubin can also help predict clinical outcomes.Universitat Autònoma de Barcelona 22021-01-0120212021-01-01Articlehttp://purl.org/coar/resource_type/c_6501VoRhttp://purl.org/coar/version/c_970fb48d4fbd8a85info:eu-repo/semantics/articleapplication/pdfhttps://ddd.uab.cat/record/271904https://dx.doi.org/urn:doi:10.1016/j.jhep.2021.01.029reponame:Dipòsit Digital de Documents de la UABinstname:Universitat Autònoma de BarcelonaInglésengInstituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI19/00883Ministerio de Economía y Competitividad https://doi.org/10.13039/501100003329 PI16/01748Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI18/00901Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI18/01804Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI-0285-2016Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI-0274-2016Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PI-0310-2018Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 PT17/0017/0020Ministerio de Economía y Competitividad https://doi.org/10.13039/501100003329 JR16/00015Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 B-0002-2019Instituto de Salud Carlos III https://doi.org/10.13039/501100004587 CM17/00243open accesshttp://purl.org/coar/access_right/c_abf2Aquest document està subjecte a una llicència d'ús Creative Commons. Es permet la reproducció total o parcial, la distribució, i la comunicació pública de l'obra, sempre que no sigui amb finalitats comercials, i sempre que es reconegui l'autoria de l'obra original. No es permet la creació d'obres derivades.https://creativecommons.org/licenses/by-nc-nd/4.0/info:eu-repo/semantics/openAccessoai:ddd.uab.cat:2719042026-06-06T12:50:31Z
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