Autophagy and Neurodegeneration: Pathogenic Mechanisms and Therapeutic Opportunities

Autophagy is a conserved pathway that delivers cytoplasmic contents to the lysosome for degradation. Here we consider its roles in neuronal health and disease. We review evidence from mouse knockout studies demonstrating the normal functions of autophagy as a protective factor against neurodegenerat...

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Detalhes bibliográficos
Autores: Menzies, Fiona M., Fleming, Angeleen, Caricasole, Andrea, Bento, Carla F., Andrews, Stephen P., Ashkenazi, Avraham, Füllgrabe, Jens, Jackson, Anne, Jimenez-Sanchez, Maria, Karabiyik, Cansu, Licitra, Floriana, Lopez Ramirez, Ana, Pavel, Mariana, Puri, Claudia, Renna, Maurizio, Ricketts, Thomas, Schlotawa, Lars, Vicinanza, Mariella, Won, Hyeran, Zhu, Ye, Skidmore, John, Rubinsztein, David C.
Formato: artículo
Estado:Versión publicada
Fecha de publicación:2017
País:España
Recursos:Consejo Superior de Investigaciones Científicas (CSIC)
Repositorio:DIGITAL.CSIC. Repositorio Institucional del CSIC
OAI Identifier:oai:digital.csic.es:10261/413783
Acesso em linha:http://hdl.handle.net/10261/413783
https://api.elsevier.com/content/abstract/scopus_id/85014799386
Access Level:acceso abierto
Palavra-chave:Alzheimer’s disease
Huntington’s disease
Parkinson’s disease
Autophagy
Dementia
lysosome
Motor neuron disease
Neurodegeneration
Tau
Descrição
Resumo:Autophagy is a conserved pathway that delivers cytoplasmic contents to the lysosome for degradation. Here we consider its roles in neuronal health and disease. We review evidence from mouse knockout studies demonstrating the normal functions of autophagy as a protective factor against neurodegeneration associated with intracytoplasmic aggregate-prone protein accumulation as well as other roles, including in neuronal stem cell differentiation. We then describe how autophagy may be affected in a range of neurodegenerative diseases. Finally, we describe how autophagy upregulation may be a therapeutic strategy in a wide range of neurodegenerative conditions and consider possible pathways and druggable targets that may be suitable for this objective.