SEOM Clinical Guideline of management of soft-tissue sarcoma (2020)

Soft-tissue sarcomas constitute an uncommon and heterogeneous group of tumors of mesenchymal origin. Diagnosis, treatment, and management should be performed by an expert multidisciplinary team. MRI/CT of the primary tumor and biopsy is mandatory before any treatment. Wide surgical resection with tu...

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Autores: de Juan Ferre, Ana|||0000-0002-5852-9068, Alvarez, Rosa|||0000-0003-0935-8298, Casado Herráez, Antonio|||0000-0002-8200-3306, Cruz-Jurado, Josefina|||0000-0001-6398-1641, Estival, Anna|||0000-0002-2788-9159, Martín-Broto, Javier|||0000-0001-7350-6916, Martínez Marín, Virginia, Moreno Vega, Alberto Luis|||0000-0002-4063-7773, Sebio, Ana|||0000-0003-3333-2370, Valverde Morales, Claudia Maria
Tipo de recurso: artículo
Fecha de publicación:2021
País:España
Institución:Universitat Autònoma de Barcelona
Repositorio:Dipòsit Digital de Documents de la UAB
Idioma:inglés
OAI Identifier:oai:ddd.uab.cat:271999
Acceso en línea:https://ddd.uab.cat/record/271999
https://dx.doi.org/urn:doi:10.1007/s12094-020-02534-0
Access Level:acceso abierto
Palabra clave:Sarcoma
Guidelines
Soft-tissue tumors
Uncommon tumors
Descripción
Sumario:Soft-tissue sarcomas constitute an uncommon and heterogeneous group of tumors of mesenchymal origin. Diagnosis, treatment, and management should be performed by an expert multidisciplinary team. MRI/CT of the primary tumor and biopsy is mandatory before any treatment. Wide surgical resection with tumor-free tissue margin is the mainstay for localized disease. Radiotherapy is indicated in large, deep, high-grade tumors, or after marginal resection not suitable for re-excision. Perioperative chemotherapy should be discussed for high-risk sarcomas of the extremities and trunk-wall. In the case of oligometastatic disease, patients should be considered for local therapies. First-line treatment with anthracyclines (or in combination with ifosfamide) is the treatment of choice. Other drugs have shown activity in second-line therapy and in specific histological subtypes but options are limited and thus, a clinical trial should always be discussed.