An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)

Kasper, Bernd; Baumgarten, C.; García, J.; Bonvalot, Sylvie; Haas, R. L.; Haller, F.; Hohenberger, Peter; Penel, Nicolas; Messiou, C.; van der Graaf, W. T.; Gronchi, Alesandro; Bauer, Sebastian; Blay, Jean-Yves; van Coevorden, F.; Dileo, P.; Dürr, H. R.; Fiore, M. R.; Grünwald, V.; Jones, Robin L.; Judson, I.; Kettelhack, C.; Kopeckova, K.; Lazar, A. J.; Lindner, Lars H.; Martín-Broto, Javier; Rutkowski, Piotr; Stacchiotti, Silvia; Stoeckle, E.; Valverde, Claudia M.; Verhoef, K.; Wardelmann, Eva; Wartenberg, M.

An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)

Desmoid-type fibromatosis is a rare and locally aggressive monoclonal, fibroblastic proliferation characterized by a variable and often unpredictable clinical course. Currently, there is no established or evidence-based treatment approach available for this disease. Therefore, in 2015 the European D...

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Autores:	Kasper, Bernd, Baumgarten, C., García, J., Bonvalot, Sylvie, Haas, R. L., Haller, F., Hohenberger, Peter, Penel, Nicolas, Messiou, C., van der Graaf, W. T., Gronchi, Alesandro, Bauer, Sebastian, Blay, Jean-Yves, van Coevorden, F., Dileo, P., Dürr, H. R., Fiore, M. R., Grünwald, V., Jones, Robin L., Judson, I., Kettelhack, C., Kopeckova, K., Lazar, A. J., Lindner, Lars H., Martín-Broto, Javier, Rutkowski, Piotr, Stacchiotti, Silvia, Stoeckle, E., Valverde, Claudia M., Verhoef, K., Wardelmann, Eva, Wartenberg, M.
Tipo de documento:	artigo
Estado:	Versão publicada
Data de publicação:	2017
País:	España
Recursos:	Consejo Superior de Investigaciones Científicas (CSIC)
Repositório:	DIGITAL.CSIC. Repositorio Institucional del CSIC
OAI Identifier:	oai:digital.csic.es:10261/182594
Acesso em linha:	http://hdl.handle.net/10261/182594
Access Level:	Acceso aberto
Palavra-chave:	Desmoid Aggressive fibromatosis EORTC/STBSG Patient advocacy groups SPAEN Treatment algorithm

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spelling	An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)Kasper, BerndBaumgarten, C.García, J.Bonvalot, SylvieHaas, R. L.Haller, F.Hohenberger, PeterPenel, NicolasMessiou, C.van der Graaf, W. T.Gronchi, AlesandroBauer, SebastianBlay, Jean-Yvesvan Coevorden, F.Dileo, P.Dürr, H. R.Fiore, M. R.Grünwald, V.Jones, Robin L.Judson, I.Kettelhack, C.Kopeckova, K.Lazar, A. J.Lindner, Lars H.Martín-Broto, JavierRutkowski, PiotrStacchiotti, SilviaStoeckle, E.Valverde, Claudia M.Verhoef, K.Wardelmann, EvaWartenberg, M.DesmoidAggressive fibromatosisEORTC/STBSGPatient advocacy groupsSPAENTreatment algorithmDesmoid-type fibromatosis is a rare and locally aggressive monoclonal, fibroblastic proliferation characterized by a variable and often unpredictable clinical course. Currently, there is no established or evidence-based treatment approach available for this disease. Therefore, in 2015 the European Desmoid Working Group published a position paper giving recommendations on the treatment of this intriguing disease. Here, we present an update of this consensus approach based on professionals’ AND patients’ expertise following a round table meeting bringing together sarcoma experts from the European Organization for Research and Treatment of Cancer/Soft Tissue and Bone Sarcoma Group with patients and patient advocates from Sarcoma PAtients EuroNet. In this paper, we focus on new findings regarding the prognostic value of mutational analysis in desmoid-type fibromatosis patients and new systemic treatment options.Peer reviewedOxford University PressConsejo Superior de Investigaciones Científicas [https://ror.org/02gfc7t72]201920192017info:eu-repo/semantics/articlehttp://purl.org/coar/resource_type/c_6501Publisher's versioninfo:eu-repo/semantics/publishedVersionhttp://hdl.handle.net/10261/182594reponame:DIGITAL.CSIC. Repositorio Institucional del CSICinstname:Consejo Superior de Investigaciones Científicas (CSIC)Ingléshttps://doi.org/10.1093/annonc/mdx323Síinfo:eu-repo/semantics/openAccessoai:digital.csic.es:10261/1825942026-05-22T06:33:51Z
dc.title.none.fl_str_mv	An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)
title	An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)
spellingShingle	An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG) Kasper, Bernd Desmoid Aggressive fibromatosis EORTC/STBSG Patient advocacy groups SPAEN Treatment algorithm
title_short	An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)
title_full	An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)
title_fullStr	An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)
title_full_unstemmed	An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)
title_sort	An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)
dc.creator.none.fl_str_mv	Kasper, Bernd Baumgarten, C. García, J. Bonvalot, Sylvie Haas, R. L. Haller, F. Hohenberger, Peter Penel, Nicolas Messiou, C. van der Graaf, W. T. Gronchi, Alesandro Bauer, Sebastian Blay, Jean-Yves van Coevorden, F. Dileo, P. Dürr, H. R. Fiore, M. R. Grünwald, V. Jones, Robin L. Judson, I. Kettelhack, C. Kopeckova, K. Lazar, A. J. Lindner, Lars H. Martín-Broto, Javier Rutkowski, Piotr Stacchiotti, Silvia Stoeckle, E. Valverde, Claudia M. Verhoef, K. Wardelmann, Eva Wartenberg, M.
author	Kasper, Bernd
author_facet	Kasper, Bernd Baumgarten, C. García, J. Bonvalot, Sylvie Haas, R. L. Haller, F. Hohenberger, Peter Penel, Nicolas Messiou, C. van der Graaf, W. T. Gronchi, Alesandro Bauer, Sebastian Blay, Jean-Yves van Coevorden, F. Dileo, P. Dürr, H. R. Fiore, M. R. Grünwald, V. Jones, Robin L. Judson, I. Kettelhack, C. Kopeckova, K. Lazar, A. J. Lindner, Lars H. Martín-Broto, Javier Rutkowski, Piotr Stacchiotti, Silvia Stoeckle, E. Valverde, Claudia M. Verhoef, K. Wardelmann, Eva Wartenberg, M.
author_role	author
author2	Baumgarten, C. García, J. Bonvalot, Sylvie Haas, R. L. Haller, F. Hohenberger, Peter Penel, Nicolas Messiou, C. van der Graaf, W. T. Gronchi, Alesandro Bauer, Sebastian Blay, Jean-Yves van Coevorden, F. Dileo, P. Dürr, H. R. Fiore, M. R. Grünwald, V. Jones, Robin L. Judson, I. Kettelhack, C. Kopeckova, K. Lazar, A. J. Lindner, Lars H. Martín-Broto, Javier Rutkowski, Piotr Stacchiotti, Silvia Stoeckle, E. Valverde, Claudia M. Verhoef, K. Wardelmann, Eva Wartenberg, M.
author2_role	author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author
dc.contributor.none.fl_str_mv	Consejo Superior de Investigaciones Científicas [https://ror.org/02gfc7t72]
dc.subject.none.fl_str_mv	Desmoid Aggressive fibromatosis EORTC/STBSG Patient advocacy groups SPAEN Treatment algorithm
topic	Desmoid Aggressive fibromatosis EORTC/STBSG Patient advocacy groups SPAEN Treatment algorithm
description	Desmoid-type fibromatosis is a rare and locally aggressive monoclonal, fibroblastic proliferation characterized by a variable and often unpredictable clinical course. Currently, there is no established or evidence-based treatment approach available for this disease. Therefore, in 2015 the European Desmoid Working Group published a position paper giving recommendations on the treatment of this intriguing disease. Here, we present an update of this consensus approach based on professionals’ AND patients’ expertise following a round table meeting bringing together sarcoma experts from the European Organization for Research and Treatment of Cancer/Soft Tissue and Bone Sarcoma Group with patients and patient advocates from Sarcoma PAtients EuroNet. In this paper, we focus on new findings regarding the prognostic value of mutational analysis in desmoid-type fibromatosis patients and new systemic treatment options.
publishDate	2017
dc.date.none.fl_str_mv	2017 2019 2019
dc.type.none.fl_str_mv	info:eu-repo/semantics/article http://purl.org/coar/resource_type/c_6501 Publisher's version info:eu-repo/semantics/publishedVersion
format	article
status_str	publishedVersion
dc.identifier.none.fl_str_mv	http://hdl.handle.net/10261/182594
url	http://hdl.handle.net/10261/182594
dc.language.none.fl_str_mv	Inglés
language_invalid_str_mv	Inglés
dc.relation.none.fl_str_mv	https://doi.org/10.1093/annonc/mdx323 Sí
dc.rights.none.fl_str_mv	info:eu-repo/semantics/openAccess
eu_rights_str_mv	openAccess
dc.publisher.none.fl_str_mv	Oxford University Press
publisher.none.fl_str_mv	Oxford University Press
dc.source.none.fl_str_mv	reponame:DIGITAL.CSIC. Repositorio Institucional del CSIC instname:Consejo Superior de Investigaciones Científicas (CSIC)
instname_str	Consejo Superior de Investigaciones Científicas (CSIC)
reponame_str	DIGITAL.CSIC. Repositorio Institucional del CSIC
collection	DIGITAL.CSIC. Repositorio Institucional del CSIC
repository.name.fl_str_mv
repository.mail.fl_str_mv
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An update on the management of sporadic desmoid-type fibromatosis: a European Consensus Initiative between Sarcoma PAtients EuroNet (SPAEN) and European Organization for Research and Treatment of Cancer (EORTC)/Soft Tissue and Bone Sarcoma Group (STBSG)

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